Case Report: A New Gain-of-Function Mutation of


Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2021
Historique:
received: 17 08 2021
accepted: 15 11 2021
entrez: 6 1 2022
pubmed: 7 1 2022
medline: 17 2 2022
Statut: epublish

Résumé

Heterozygous missense Genetic analysis NGS identified a novel variant of We describe a new

Identifiants

pubmed: 34987506
doi: 10.3389/fimmu.2021.760019
pmc: PMC8721043
doi:

Substances chimiques

STAT1 Transcription Factor 0
STAT1 protein, human 0

Types de publication

Case Reports Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

760019

Subventions

Organisme : NIAID NIH HHS
ID : R01 AI127564
Pays : United States

Informations de copyright

Copyright © 2021 Martinot, Korganow, Wald, Second, Birckel, Mahé, Souply, Mohseni-Zadeh, Droy, Tarabeux, Okada, Migaud, Puel and Guffroy.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

Références

J Eur Acad Dermatol Venereol. 2018 Jun;32(6):1011-1016
pubmed: 29478301
J Am Acad Dermatol. 2011 Oct;65(4):e131-e132
pubmed: 21920237
J Korean Med Sci. 2011 Sep;26(9):1231-7
pubmed: 21935281
J Exp Med. 2011 Aug 1;208(8):1635-48
pubmed: 21727188
J Eur Acad Dermatol Venereol. 2020 Jun;34(6):e265-e267
pubmed: 31991004
Ann Dermatol Venereol. 2020 Jan;147(1):41-45
pubmed: 31677808
N Engl J Med. 2011 Jul 7;365(1):54-61
pubmed: 21714643
Int J STD AIDS. 2008 Jul;19(7):493-5
pubmed: 18574128
New Microbes New Infect. 2019 Jun 09;31:100525
pubmed: 31388432
Ital J Pediatr. 2015 Mar 28;41:23
pubmed: 25881033
Acta Derm Venereol. 2018 Dec 27;99(1):47-52
pubmed: 30226528
Dermatology. 2002;205(4):394-7
pubmed: 12444338
J Clin Immunol. 2020 Jan;40(1):24-64
pubmed: 31953710
J Am Acad Dermatol. 1992 Dec;27(6 Pt 1):1010-1
pubmed: 1479080
J Clin Immunol. 2021 Apr;41(3):698-700
pubmed: 33404972
J Clin Immunol. 2016 Jan;36(1):73-84
pubmed: 26604104
J Clin Immunol. 2020 Nov;40(8):1065-1081
pubmed: 32852681
J Eur Acad Dermatol Venereol. 2018 Mar;32(3):e88-e89
pubmed: 28846817
Blood. 2016 Jun 23;127(25):3154-64
pubmed: 27114460
PeerJ. 2015 Mar 03;3:e796
pubmed: 25780760
Br J Dermatol. 2001 Jan;144(1):139-42
pubmed: 11167695
Z Hautkr. 1989 Jun 15;64(6):452-4
pubmed: 2527449
Pediatr Dermatol. 2020 Jan;37(1):153-155
pubmed: 31637766
J Eur Acad Dermatol Venereol. 2017 Dec;31(12):e542-e544
pubmed: 28622416
Expert Rev Clin Immunol. 2018 Dec;14(12):1029-1041
pubmed: 30280610
Acta Derm Venereol. 1993 Dec;73(6):437
pubmed: 7906456
Dermatol Clin. 2018 Apr;36(2):115-122
pubmed: 29499794
Hum Genet. 2020 Jun;139(6-7):1011-1022
pubmed: 32124012
J Am Acad Dermatol. 2005 Jan;52(1):74-87
pubmed: 15627084
Arch Dermatol. 2010 Aug;146(8):896-902
pubmed: 20713824
Clin Exp Immunol. 2021 Oct;206(1):56-67
pubmed: 34114647

Auteurs

Martin Martinot (M)

Infectious Diseases Department, Hôpitaux Civils de Colmar, Colmar, France.

Anne Sophie Korganow (AS)

Department of Clinical Immunology and Internal Medicine, National Reference Center for Systemic Autoimmune Diseases (CNR RESO), Tertiary Center for Primary Immunodeficiency, Strasbourg University Hospital, Strasbourg, France.

Mathieu Wald (M)

Infectious Diseases Department, Hôpitaux Civils de Colmar, Colmar, France.

Julie Second (J)

Dermatology Department, Hôpitaux Civils de Colmar, Colmar, France.

Elodie Birckel (E)

Dermatology Department, Hôpitaux Civils de Colmar, Colmar, France.

Antoine Mahé (A)

Dermatology Department, Hôpitaux Civils de Colmar, Colmar, France.

Laurent Souply (L)

Microbiology Department, Hôpitaux Civils de Colmar, Colmar, France.

Mahsa Mohseni-Zadeh (M)

Infectious Diseases Department, Hôpitaux Civils de Colmar, Colmar, France.

Laure Droy (L)

Pathology Department, Hôpitaux Civils de Colmar, Colmar, France.

Julien Tarabeux (J)

Genetic Diagnostic Laboratory, Hôpitaux Universitaires de Strasbourg, Strasbourg, France.

Satoshi Okada (S)

Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, UMR 1163, University of Paris, Paris, France.

Mélanie Migaud (M)

Department of Pediatrics, Graduate School of Biomedical and Health Sciences, Hiroshima University, Hiroshima, Japan.

Anne Puel (A)

Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM, UMR 1163, University of Paris, Paris, France.
University of Paris, Imagine Institute, Paris, France.
St. Giles Laboratory of Human Genetics of Infectious Diseases, The Rockefeller University, New York, NY, United States.

Aurelien Guffroy (A)

Department of Clinical Immunology and Internal Medicine, National Reference Center for Systemic Autoimmune Diseases (CNR RESO), Tertiary Center for Primary Immunodeficiency, Strasbourg University Hospital, Strasbourg, France.

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Classifications MeSH