Alkalosis-induced hypoventilation in cystic fibrosis: The importance of efficient renal adaptation.
Acid-Base Equilibrium
/ physiology
Alkalosis
/ metabolism
Animals
Bicarbonates
/ metabolism
Chloride-Bicarbonate Antiporters
Cystic Fibrosis
/ complications
Cystic Fibrosis Transmembrane Conductance Regulator
/ genetics
Disease Models, Animal
Female
Hypoventilation
/ etiology
Ion Transport
Kidney
/ metabolism
Lung
/ metabolism
Male
Mice
Mice, Inbred C57BL
Mice, Knockout
Renal Elimination
Renal Reabsorption
/ physiology
CFTR
acid–base
cystic fibrosis
hypoventilation
kidney
Journal
Proceedings of the National Academy of Sciences of the United States of America
ISSN: 1091-6490
Titre abrégé: Proc Natl Acad Sci U S A
Pays: United States
ID NLM: 7505876
Informations de publication
Date de publication:
22 02 2022
22 02 2022
Historique:
accepted:
13
01
2022
entrez:
17
2
2022
pubmed:
18
2
2022
medline:
15
3
2022
Statut:
ppublish
Résumé
The lungs and kidneys are pivotal organs in the regulation of body acid-base homeostasis. In cystic fibrosis (CF), the impaired renal ability to excrete an excess amount of HCO
Identifiants
pubmed: 35173044
pii: 2116836119
doi: 10.1073/pnas.2116836119
pmc: PMC8872776
pii:
doi:
Substances chimiques
Bicarbonates
0
Chloride-Bicarbonate Antiporters
0
Cystic Fibrosis Transmembrane Conductance Regulator
126880-72-6
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Déclaration de conflit d'intérêts
The authors declare no competing interest.
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