USP6 rearrangement in pediatric nodular fasciitis.


Journal

Journal of cutaneous pathology
ISSN: 1600-0560
Titre abrégé: J Cutan Pathol
Pays: United States
ID NLM: 0425124

Informations de publication

Date de publication:
Aug 2022
Historique:
revised: 24 02 2022
received: 06 09 2021
accepted: 27 03 2022
pubmed: 2 4 2022
medline: 22 7 2022
entrez: 1 4 2022
Statut: ppublish

Résumé

Nodular fasciitis (NF) is a myofibroblastic proliferation that is uncommonly present in pediatric patients. These benign neoplasms can masquerade as more insidious sarcomatous proliferations on both clinical exam and initial histopathologic review, often prompting undue concern in patients, parents, and providers. While immunohistochemical analysis of NF can be variable, adding to the diagnostic uncertainty, molecular analysis documenting ubiquitin-specific protease 6 (USP6) gene rearrangement can help confirm the diagnosis as an association between NF and USP6 overexpression was first identified 10 years ago in an analysis that found rearrangements of the involved locus in over 90% of studied samples. In this report, we review one case of NF located on the chin of a nine-year-old girl in which molecular testing was essential to secure the correct diagnosis, and provide a summary of documented cases of USP6 overexpression in transient pediatric neoplasms.

Identifiants

pubmed: 35362105
doi: 10.1111/cup.14237
doi:

Substances chimiques

Proto-Oncogene Proteins 0
USP6 protein, human EC 3.4.19.12
Ubiquitin Thiolesterase EC 3.4.19.12

Types de publication

Case Reports Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

743-746

Informations de copyright

© 2022 John Wiley & Sons A/S. Published by John Wiley & Sons Ltd.

Références

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Auteurs

Rachel Sennett (R)

Department of Dermatology, University of California San Diego, La Jolla, California, USA.

Sheila Friedlander (S)

Department of Dermatology, University of California San Diego, La Jolla, California, USA.
Pediatric and Adolescent Dermatology, Rady Children's Hospital, San Diego, California, USA.

Suzanne Tucker (S)

Pathology, Rady Children's Hospital, San Diego, California, USA.

Brian Hinds (B)

Department of Dermatology, University of California San Diego, La Jolla, California, USA.

George Hightower (G)

Department of Dermatology, University of California San Diego, La Jolla, California, USA.
Pediatric and Adolescent Dermatology, Rady Children's Hospital, San Diego, California, USA.

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