Carriers of


Journal

Viruses
ISSN: 1999-4915
Titre abrégé: Viruses
Pays: Switzerland
ID NLM: 101509722

Informations de publication

Date de publication:
29 05 2022
Historique:
received: 21 03 2022
revised: 25 05 2022
accepted: 25 05 2022
entrez: 24 6 2022
pubmed: 25 6 2022
medline: 28 6 2022
Statut: epublish

Résumé

Thrombosis of small and large vessels is reported as a key player in COVID-19 severity. However, host genetic determinants of this susceptibility are still unclear. Congenital Thrombotic Thrombocytopenic Purpura is a severe autosomal recessive disorder characterized by uncleaved ultra-large vWF and thrombotic microangiopathy, frequently triggered by infections. Carriers are reported to be asymptomatic. Exome analysis of about 3000 SARS-CoV-2 infected subjects of different severities, belonging to the GEN-COVID cohort, revealed the specific role of vWF cleaving enzyme

Identifiants

pubmed: 35746657
pii: v14061185
doi: 10.3390/v14061185
pmc: PMC9227269
pii:
doi:

Substances chimiques

von Willebrand Factor 0
ADAM Proteins EC 3.4.24.-
ADAMTS13 Protein EC 3.4.24.87
ADAMTS13 protein, human EC 3.4.24.87

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

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Auteurs

Kristina Zguro (K)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.

Margherita Baldassarri (M)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.

Francesca Fava (F)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.
Genetica Medica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Giada Beligni (G)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.

Sergio Daga (S)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.

Roberto Leoncini (R)

Laboratorio Patologia Clinica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Lucrezia Galasso (L)

Laboratorio Patologia Clinica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Michele Cirianni (M)

Laboratorio Patologia Clinica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Stefano Rusconi (S)

Infectious Diseases Unit, ASST Ovest Milanese, 20025 Legnano, Italy.
Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, 20157 Milan, Italy.

Matteo Siano (M)

Department of Biomedical and Clinical Sciences Luigi Sacco, University of Milan, 20157 Milan, Italy.

Daniela Francisci (D)

Infectious Diseases Clinic, "Santa Maria della Misericordia" Hospital, University of Perugia, 06124 Perugia, Italy.

Elisabetta Schiaroli (E)

Infectious Diseases Clinic, "Santa Maria della Misericordia" Hospital, University of Perugia, 06124 Perugia, Italy.

Sauro Luchi (S)

Infectious Disease Unit, Hospital of Lucca, 55100 Lucca, Italy.

Giovanna Morelli (G)

Infectious Disease Unit, Hospital of Lucca, 55100 Lucca, Italy.

Enrico Martinelli (E)

Department of Respiratory Diseases, Azienda Ospedaliera di Cremona, 26100 Cremona, Italy.

Massimo Girardis (M)

Department of Anesthesia and Intensive Care, University of Modena and Reggio Emilia, 41124 Modena, Italy.

Stefano Busani (S)

Department of Anesthesia and Intensive Care, University of Modena and Reggio Emilia, 41124 Modena, Italy.

Saverio Giuseppe Parisi (SG)

Department of Molecular Medicine, University of Padova, 35121 Padova, Italy.

Sandro Panese (S)

Clinical Infectious Diseases, Mestre Hospital, 30171 Venezia, Italy.

Carmelo Piscopo (C)

Medical Genetics and Laboratory Genetics Unit, "Antonio Cardarelli" hospital, 80131 Naples, Italy.

Mario Capasso (M)

Department of Molecular Medicine and Medical Biotechnology, University of Naples Federico II, 80138 Naples, Italy.
CEINGE Biotecnologie Avanzate, 80145 Naples, Italy.

Danilo Tacconi (D)

Department of Specialized and Internal Medicine, Infectious Diseases Unit, San Donato Hospital Arezzo, 52100 Arezzo, Italy.

Chiara Spertilli Raffaelli (C)

Department of Specialized and Internal Medicine, Infectious Diseases Unit, San Donato Hospital Arezzo, 52100 Arezzo, Italy.

Annarita Giliberti (A)

Medical Genetics Unit, Meyer Children's University Hospital, 50134 Florence, Italy.

Giulia Gori (G)

Medical Genetics Unit, Meyer Children's University Hospital, 50134 Florence, Italy.

Peter D Katsikis (PD)

Department of Immunology, Erasmus Medical Center, 3015 GD Rotterdam, The Netherlands.

Maria Lorubbio (M)

UOC Laboratorio Analisi Chimico Cliniche, 52100 Arezzo, Italy.

Paola Calzoni (P)

Laboratorio Patologia Clinica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Agostino Ognibene (A)

UOC Laboratorio Analisi Chimico Cliniche, 52100 Arezzo, Italy.

Monica Bocchia (M)

Hematology Unit, Department of Medical Science, Surgery and Neuroscience, University of Siena, 53100 Siena, Italy.

Monica Tozzi (M)

Stem Cell Transplant and Cellular Therapy Unit, University Hospital of Siena, 53100 Siena, Italy.

Alessandro Bucalossi (A)

Stem Cell Transplant and Cellular Therapy Unit, University Hospital of Siena, 53100 Siena, Italy.

Giuseppe Marotta (G)

Stem Cell Transplant and Cellular Therapy Unit, University Hospital of Siena, 53100 Siena, Italy.

Simone Furini (S)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.

Alessandra Renieri (A)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.
Genetica Medica, Azienda Ospedaliero-Universitaria Senese, 53100 Siena, Italy.

Chiara Fallerini (C)

Med Biotech Hub and Competence Center, Department of Medical Biotechnologies, University of Siena, 53100 Siena, Italy.
Medical Genetics, University of Siena, 53100 Siena, Italy.

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Classifications MeSH