Cathepsin B p.Gly284Val Variant in Parkinson's Disease Pathogenesis.


Journal

International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791

Informations de publication

Date de publication:
25 Jun 2022
Historique:
received: 23 04 2022
revised: 17 06 2022
accepted: 22 06 2022
entrez: 9 7 2022
pubmed: 10 7 2022
medline: 14 7 2022
Statut: epublish

Résumé

Parkinson's disease (PD) is generally considered a sporadic disorder, but a strong genetic background is often found. The aim of this study was to identify the underlying genetic cause of PD in two affected siblings and to subsequently assess the role of mutations in Cathepsin B

Identifiants

pubmed: 35806091
pii: ijms23137086
doi: 10.3390/ijms23137086
pmc: PMC9266886
pii:
doi:

Substances chimiques

CTSB protein, human EC 3.4.22.1
Cathepsin B EC 3.4.22.1

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : NINDS NIH HHS
ID : RF1 NS085070
Pays : United States
Organisme : NINDS NIH HHS
ID : U54 NS110435
Pays : United States
Organisme : NIH HHS
ID : 1U19AG063911
Pays : United States

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Auteurs

Lukasz M Milanowski (LM)

Department of Neurology, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Xu Hou (X)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Jenny M Bredenberg (JM)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Fabienne C Fiesel (FC)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Neuroscience PhD Program, Mayo Graduate School, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Liam T Cocker (LT)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Alexandra I Soto-Beasley (AI)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Ronald L Walton (RL)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Audrey J Strongosky (AJ)

Department of Neurology, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Ayman H Faroqi (AH)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Neuroscience PhD Program, Mayo Graduate School, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Maria Barcikowska (M)

Clinical Department of Neurology, Extrapyramidal Disorders and Alzheimer's Outpatient Clinic, Central Clinical Hospital of the Ministry of the Interior and Administration in Warsaw, 02-507 Warsaw, Poland.

Magdalena Boczarska-Jedynak (M)

Department of Neurology and Restorative Medicine, Health Institute dr Boczarska-Jedynak, 32-600 Oswiecim, Poland.

Jaroslaw Dulski (J)

Department of Neurology, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Department of Neurology, St. Adalbert Hospital, Copernicus PL Ltd., 80-462 Gdansk, Poland.
Division of Neurological and Psychiatric Nursing, Faculty of Health Sciences, Medical University of Gdansk, 80-210 Gdansk, Poland.

Lyuda Fedoryshyn (L)

Lviv Regional Clinical Hospital, 79010 Lviv, Ukraine.

Piotr Janik (P)

Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Anna Potulska-Chromik (A)

Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Katherine Karpinsky (K)

Uzhhorod Regional Clinical Centre of Neurosurgery and Neurology, 88018 Uzhhorod, Ukraine.

Anna Krygowska-Wajs (A)

Department of Neurology, Jagiellonian University Medical College, 31-008 Krakow, Poland.

Tim Lynch (T)

The Dublin Neurological Institute, Mater Misericordiae University Hospital, D07 W7XF Dublin, Ireland.
School of Medicine and Medical Science, University College Dublin, D04 V1W8 Dublin, Ireland.

Diana A Olszewska (DA)

The Dublin Neurological Institute, Mater Misericordiae University Hospital, D07 W7XF Dublin, Ireland.
School of Medicine and Medical Science, University College Dublin, D04 V1W8 Dublin, Ireland.
Edmond J. Safra Program in Parkinson's Disease and the Morton and Gloria Shulman Movement Disorders Clinic, Toronto Western Hospital, Toronto, ON M5T 2S8, Canada.

Grzegorz Opala (G)

Department of Neurology, Faculty of Medical Sciences in Katowice, Medical University of Silesia, 40-055 Katowice, Poland.

Aleksander Pulyk (A)

Uzhhorod National University, 88-000 Uzhhorod, Ukraine.

Irena Rektorova (I)

Applied Neuroscience Research Group, Central European Institute of Technology, CEITEC MU, Masaryk University, 601-77 Brno, Czech Republic.
St. Anne's University Hospital and Faculty of Medicine, Masaryk University, 601-77 Brno, Czech Republic.

Yanosh Sanotsky (Y)

Lviv Regional Clinical Hospital, 79010 Lviv, Ukraine.

Joanna Siuda (J)

Department of Neurology, Faculty of Medical Sciences in Katowice, Medical University of Silesia, 40-055 Katowice, Poland.

Mariusz Widlak (M)

Bielanski Hospital, 01-809 Warsaw, Poland.

Jaroslaw Slawek (J)

Department of Neurology, St. Adalbert Hospital, Copernicus PL Ltd., 80-462 Gdansk, Poland.
Division of Neurological and Psychiatric Nursing, Faculty of Health Sciences, Medical University of Gdansk, 80-210 Gdansk, Poland.

Monika Rudzinska-Bar (M)

Faculty of Medicine and Health Sciences, Andrzej Frycz Modrzewski Krakow University, 30-705 Cracow, Poland.

Ryan Uitti (R)

Department of Neurology, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Monika Figura (M)

Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Stanislaw Szlufik (S)

Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Sylwia Rzonca-Niewczas (S)

Department of Medical Genetics, Institute of Mother and Child, 01-211 Warsaw, Poland.

Elzbieta Podgorska (E)

Institute of Genetics and Biotechnology, Faculty of Biology, University of Warsaw, 00-927 Warsaw, Poland.

Pamela J McLean (PJ)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Neuroscience PhD Program, Mayo Graduate School, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Dariusz Koziorowski (D)

Department of Neurology, Faculty of Health Science, Medical University of Warsaw, 02-091 Warsaw, Poland.

Owen A Ross (OA)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Neuroscience PhD Program, Mayo Graduate School, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
School of Medicine and Medical Science, University College Dublin, D04 V1W8 Dublin, Ireland.
Department of Clinical Genomics, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Dorota Hoffman-Zacharska (D)

Department of Medical Genetics, Institute of Mother and Child, 01-211 Warsaw, Poland.
Institute of Genetics and Biotechnology, Faculty of Biology, University of Warsaw, 00-927 Warsaw, Poland.

Wolfdieter Springer (W)

Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Neuroscience PhD Program, Mayo Graduate School, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

Zbigniew K Wszolek (ZK)

Department of Neurology, Mayo Clinic Florida, Jacksonville, FL 32224, USA.
Department of Neuroscience, Mayo Clinic Florida, Jacksonville, FL 32224, USA.

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