Postinflammatory rupture of right coronary artery ostium complicating Behçet disease.


Journal

Journal of cardiac surgery
ISSN: 1540-8191
Titre abrégé: J Card Surg
Pays: United States
ID NLM: 8908809

Informations de publication

Date de publication:
Oct 2022
Historique:
revised: 14 06 2022
received: 11 04 2022
accepted: 05 07 2022
pubmed: 23 7 2022
medline: 8 9 2022
entrez: 22 7 2022
Statut: ppublish

Résumé

Behçet disease (BD) is a chronic relapsing inflammatory disease of unknown etiology, characterized by variable clinical manifestations. A 28-year-old woman with BD Cardiovascular and Bipolar Disorder underwent emergency surgical treatment of ascending aortic pseudoaneurysm for ruptured right coronary ostium.A modified Bentall procedure with tricuspid annuloplasty, surgical thrombectomy, and a single coronary artery bypass using a saphenous vein graft was performed. A biological prosthesis was used initially but subsequently deteriorated. We then successfully performed a valve-in-valve (ViV) transcatheter aortic valve implantation (TAVI). The postoperative recovery was uneventful and at follow-up, two years post valve procedure, the patient was completely symptom-free. She remains under long-term medical surveillance. The management of BD with cardiac involvement must be led by a multidisciplinary team.

Identifiants

pubmed: 35866180
doi: 10.1111/jocs.16771
doi:

Types de publication

Case Reports

Langues

eng

Sous-ensembles de citation

IM

Pagination

3432-3435

Informations de copyright

© 2022 Wiley Periodicals LLC.

Références

Lee I, Park S, Hwang I, et al. Cardiac behçet disease presenting as aortic valvulitis/aortitis or right heart inflammatory mass: a clinicopathologic study of 12 cases. Am J Surg Pathol. 2008;32:390-398.
Marzban M, Mandegar MH, Karimi A, et al. Cardiac and great vessel involvement in “Behcet's disease”. J Card Surg. 2008;23:765-768.
Zhang Shi-Huai, Zhang Fu-Xian. Behçet's disease with recurrent thoracic aortic aneurysm combined with femoral artery aneurysm: a case report and literature review. J Cardiothorac Surg. 2017;12:79.
Azuma Takashi, Yamazaki Kenji, Saito Satoshi, Kurosawa Hiromi. Aortic valve replacement in Behcet's disease: surgical modification to prevent valve detachment. Eur J Cardiothorac Surg. 2009;36(4):771-772.
Mustafa ALI, Soumitra DAS. “Neuro-psycho- BS”: a case report of rare association with bipolar disorder. Shanghai Arch Psychiatry. 2018;30(1):376-379.

Auteurs

Antonio Fiore (A)

Department of Cardiac Surgery, Hôpitaux Universitaires Henri Mondor, Assistance Publique-Hôpitaux de Paris, Creteil, France.
Department of Cardiac Surgery, Hopitaux Universitaires Henri Mondor, Creteil, France.

Mariantonietta Piscitelli (M)

Department of Cardiac Surgery, Hôpitaux Universitaires Henri Mondor, Assistance Publique-Hôpitaux de Paris, Creteil, France.

Amel Rabia (A)

Department of Cardiac Surgery, Hôpitaux Universitaires Henri Mondor, Assistance Publique-Hôpitaux de Paris, Creteil, France.

Haytham Derbel (H)

Department of Radiology, Hôpitaux Universitaires Henri Mondor, Assistance Publique-Hôpitaux de Paris, Creteil, France.

Eric Bergoend (E)

Department of Cardiac Surgery, Hôpitaux Universitaires Henri Mondor, Assistance Publique-Hôpitaux de Paris, Creteil, France.

Sanjeet S Avtaar Singh (SS)

Department of Cardiothoracic Surgery, Aberdeen Royal Infirmary, Aberdeen, United Kingdom.

Francesco Nappi (F)

Department of Cardiac Surgery, Centre Cardiologique du Nord, Saint-Denis, France.

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