Tromethamine improves mucociliary clearance in cystic fibrosis pigs.
CT imaging
cystic fibrosis
mucociliary transport
therapeutics
Journal
Physiological reports
ISSN: 2051-817X
Titre abrégé: Physiol Rep
Pays: United States
ID NLM: 101607800
Informations de publication
Date de publication:
09 2022
09 2022
Historique:
revised:
12
05
2022
received:
14
04
2022
accepted:
16
05
2022
entrez:
8
9
2022
pubmed:
9
9
2022
medline:
11
9
2022
Statut:
ppublish
Résumé
In cystic fibrosis (CF), the loss of cystic fibrosis transmembrane conductance regulator (CFTR) mediated Cl
Identifiants
pubmed: 36073059
doi: 10.14814/phy2.15340
pmc: PMC9453173
doi:
Substances chimiques
Bicarbonates
0
Tromethamine
023C2WHX2V
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
e15340Subventions
Organisme : NHLBI NIH HHS
ID : K08 HL135433
Pays : United States
Organisme : NHLBI NIH HHS
ID : NIH PPG HL091842
Pays : United States
Organisme : NHLBI NIH HHS
ID : NIH PPG HL051670
Pays : United States
Organisme : NHLBI NIH HHS
ID : NIH R01 HL136813
Pays : United States
Organisme : NHLBI NIH HHS
ID : R56 HL147073
Pays : United States
Informations de copyright
© 2022 The Authors. Physiological Reports published by Wiley Periodicals LLC on behalf of The Physiological Society and the American Physiological Society.
Références
Proc Natl Acad Sci U S A. 2014 Feb 11;111(6):2355-60
pubmed: 24474805
Am J Respir Crit Care Med. 2014 Aug 15;190(4):421-32
pubmed: 25029666
Cold Spring Harb Perspect Med. 2013 Aug 01;3(8):
pubmed: 23751214
JCI Insight. 2019 Jan 10;4(1):
pubmed: 30626743
Biochem J. 1996 Aug 15;318 ( Pt 1):319-24
pubmed: 8761488
Am J Respir Crit Care Med. 2014 May 1;189(9):1082-92
pubmed: 24678594
JCI Insight. 2016 Jun 2;1(8):
pubmed: 27390778
N Engl J Med. 2006 Jan 19;354(3):241-50
pubmed: 16421365
N Engl J Med. 2006 Jan 19;354(3):229-40
pubmed: 16421364
Laryngoscope. 1999 Mar;109(3):396-9
pubmed: 10089964
Cochrane Database Syst Rev. 2009 Jan 21;(1):CD007168
pubmed: 19160327
Eur J Clin Pharmacol. 1982;22(3):257-64
pubmed: 7106159
Annu Rev Physiol. 2008;70:459-86
pubmed: 17850213
Thorax. 2010 May;65(5):379-83
pubmed: 20435858
Cochrane Database Syst Rev. 2013 Jul 12;(7):CD007168
pubmed: 23852992
Science. 2014 Aug 15;345(6198):818-22
pubmed: 25124441
Otolaryngol Head Neck Surg. 2001 Mar;124(3):313-6
pubmed: 11240998
JAMA. 2012 Jun 6;307(21):2269-77
pubmed: 22610452
J Clin Invest. 2016 Mar 1;126(3):879-91
pubmed: 26808501
Anat Rec (Hoboken). 2013 Nov;296(11):1768-74
pubmed: 24106034
Compr Physiol. 2016 Mar 15;6(2):827-95
pubmed: 27065169
Proc Natl Acad Sci U S A. 1994 Jun 7;91(12):5340-4
pubmed: 7515498
N Engl J Med. 1994 Sep 8;331(10):637-42
pubmed: 7503821
Curr Opin Pulm Med. 2006 Nov;12(6):445-52
pubmed: 17053496
J Clin Invest. 2010 Sep;120(9):3161-6
pubmed: 20739758
Lancet. 2016 Nov 19;388(10059):2519-2531
pubmed: 27140670
Intensive Care Med Exp. 2021 Mar 17;9(1):8
pubmed: 33728866
Proc Am Thorac Soc. 2004;1(4):315-20
pubmed: 16113452
PLoS One. 2013;8(1):e54473
pubmed: 23372732
Am J Respir Crit Care Med. 1997 Jul;156(1):173-7
pubmed: 9230743
Biochem J. 1998 Sep 15;334 ( Pt 3):685-93
pubmed: 9729478
Proc Natl Acad Sci U S A. 2022 Mar 29;119(13):e2121731119
pubmed: 35324331
Am Rev Respir Dis. 1983 Mar;127(3):390-1
pubmed: 6830063
J Cyst Fibros. 2015 Sep;14(5):621-6
pubmed: 26074007
Dev Cell. 2020 Aug 24;54(4):488-500.e5
pubmed: 32730755
BMC Pulm Med. 2011 Sep 06;11:45
pubmed: 21896198
Am J Respir Crit Care Med. 1996 Dec;154(6 Pt 1):1868-902
pubmed: 8970383
Am J Respir Crit Care Med. 2018 May 15;197(10):1308-1318
pubmed: 29327941
J Thorac Cardiovasc Surg. 1987 Feb;93(2):309-11
pubmed: 3100872
Front Pharmacol. 2020 Feb 21;10:1662
pubmed: 32153386
Drugs. 1998 Feb;55(2):191-224
pubmed: 9506241
Am J Physiol Lung Cell Mol Physiol. 2013 Feb 1;304(3):L184-90
pubmed: 23204069
Eur Respir J. 1997 Nov;10(11):2449-54
pubmed: 9426077
J Exp Med. 2012 Jul 2;209(7):1263-72
pubmed: 22711878
Am J Respir Crit Care Med. 2012 Mar 15;185(6):645-52
pubmed: 22198974
Proc Natl Acad Sci U S A. 1990 Dec;87(23):9188-92
pubmed: 2251263
Am J Respir Crit Care Med. 1996 May;153(5):1503-9
pubmed: 8630593
J Anat. 2000 Oct;197 Pt 3:361-72
pubmed: 11117623
Am J Respir Crit Care Med. 2020 Jan 15;201(2):188-197
pubmed: 31601120
Respir Care. 2013 Jul;58(7):1226-32
pubmed: 23258576
Sci Rep. 2019 Jan 24;9(1):540
pubmed: 30679487
Eur Respir J. 2018 May 17;51(5):
pubmed: 29599187
Drug Deliv. 2000 Oct-Dec;7(4):223-9
pubmed: 11195429
J Anat. 2002 Oct;201(4):313-8
pubmed: 12430955
Am J Respir Crit Care Med. 2021 Sep 15;204(6):692-702
pubmed: 34170795
N Engl J Med. 2015 Apr 16;372(16):1574-5
pubmed: 25875271
Nat Rev Dis Primers. 2015 May 14;1:15010
pubmed: 27189798
Clin Drug Investig. 2020 Feb;40(2):105-117
pubmed: 31721070
Eur Respir J. 1999 Sep;14(3):678-85
pubmed: 10543292
Nat Med. 2004 May;10(5):487-93
pubmed: 15077107
Cell Calcium. 2014 Jun;55(6):325-36
pubmed: 24703093
Nature. 2012 Jul 04;487(7405):109-13
pubmed: 22763554
Chest. 1998 Jul;114(1):171-7
pubmed: 9674466
J Clin Invest. 2012 Oct;122(10):3629-34
pubmed: 22945630
J Cyst Fibros. 2011 Jun;10 Suppl 2:S172-82
pubmed: 21658636
Am J Dis Child. 1962 Jan;103:1-3
pubmed: 14453784
Proc Natl Acad Sci U S A. 2014 Dec 30;111(52):18703-8
pubmed: 25512526
Am J Respir Crit Care Med. 2019 Mar 15;199(6):715-727
pubmed: 30352166
Eur Respir J. 1999 May;13(5):1177-88
pubmed: 10414423
Ann Otol Rhinol Laryngol. 2022 Sep;131(9):1013-1020
pubmed: 34674574
Proc Natl Acad Sci U S A. 2017 Jun 27;114(26):6842-6847
pubmed: 28607090
Am J Physiol. 1991 Dec;261(6 Pt 1):L361-9
pubmed: 1767856