Neuroparalytic keratopathy in Stüve-Wiedemann syndrome treated with tarsoconjunctival flap.
Paralytic lagophthalmos
Stüve–Wiedemann syndrome
tarsoconjunctival flap
Journal
Indian journal of ophthalmology
ISSN: 1998-3689
Titre abrégé: Indian J Ophthalmol
Pays: India
ID NLM: 0405376
Informations de publication
Date de publication:
04 2023
04 2023
Historique:
medline:
10
4
2023
entrez:
7
4
2023
pubmed:
8
4
2023
Statut:
ppublish
Résumé
Stüve-Wiedemann syndrome is a rare bone dysplasia with dysautonomic manifestations. Most patients die in the neonatal period or during infancy because of the multiple complications they present. The main ophthalmological complications reported are reduced corneal reflex, corneal anesthesia, hypolacrimation, and severely reduced blinking. We are going to present the first tarsoconjunctival flap in a Stüve-Wiedemann patient, the surgery, and the results in a 13-year-old patient that came to our hospital because of severe corneal ulceration.
Identifiants
pubmed: 37026318
pii: IndianJOphthalmol_2023_71_4_1651_373522
doi: 10.4103/IJO.IJO_3260_22
pmc: PMC10276720
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
1651-1653Déclaration de conflit d'intérêts
None
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