Health-Related Quality of Life and Its Association With Outcomes in Adults With Congenital Heart Disease and Heart Failure: Insight From FRESH-ACHD Registry.


Journal

Journal of the American Heart Association
ISSN: 2047-9980
Titre abrégé: J Am Heart Assoc
Pays: England
ID NLM: 101580524

Informations de publication

Date de publication:
18 04 2023
Historique:
medline: 19 4 2023
pubmed: 8 4 2023
entrez: 7 4 2023
Statut: ppublish

Résumé

Background Quality of Life (QoL) is a prognostic factor in heart failure (HF) of patients with acquired cardiac disease. The aim of this study was to determine the predictive value of QoL on outcomes in adults with congenital heart disease (ACHD) and HF. Methods and Results Quality of life of 196 adults with congenital heart disease with clinical heart failure (HF) (mean age: 44.3±13.8 years; 51% male; 56% with complex congenital heart disease; 47% New York Heart Association class III/IV) included in the prospective multicentric registry FRESH-ACHD (French Survey on Heart Failure-Adult with Congenital Heart Disease) was assessed using the 36-Item Short Form Survey (SF-36), a patient-reported survey. The primary end point was defined by all-cause death, HF-related hospitalization, heart transplantation, and mechanical circulatory support. At 12 months, 28 (14%) patients reached the combined end point. Patients with low quality of life experienced major adverse events more frequently (logrank

Identifiants

pubmed: 37026543
doi: 10.1161/JAHA.122.027819
pmc: PMC10227248
doi:

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

e027819

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Auteurs

Reaksmei Ly (R)

Adult Congenital Heart Disease Unit Hôpital Européen Georges Pompidou Centre de Référence des Malformations Cardiaques Congénitales Complexes Assistance Publique-Hôpitaux de Paris Paris University Paris France.

Clément Karsenty (C)

Congenital Cardiology Unit Children Hospital CHU Toulouse Institut Des Maladies Métaboliques et Cardiovasculaires Université de Toulouse INSERM U1048, I2MC Toulouse France.

Pascal Amedro (P)

Department of Paediatric and Adult Congenital Cardiology Bordeaux University Hospital Bordeaux France.
Inserm, U1045, IHU Liryc Bordeaux Cardio-Thoracic Research Centre Electrophysiology and Heart Modelling Institute University of Bordeaux Fondation Bordeaux Université Pessac France.

Sarah Cohen (S)

Division of Congenital Heart Disease, Expert Center for Complex Congenital Heart Disease (M3C Network) Marie Lannelongue Hospital Groupe Hospitalier Paris Saint Joseph Inserm UMRs-999 Paris-Saclay University Le Plessis Robinson France.

Olivia Domanski (O)

CHRU de Lille University Lille Nord-de-France Faculté de médecine, hôpital cardiologique, service des maladies cardiovasculaires infantiles et congénitales Lille France.

Francois Godart (F)

Cardiologie Congenitale Strasbourg France.

Jelena Radojevic (J)

Division of Congenital Heart Disease, Expert Center for Complex Congenital Heart Disease (M3C Network) Marie Lannelongue Hospital Groupe Hospitalier Paris Saint Joseph Inserm UMRs-999 Paris-Saclay University Le Plessis Robinson France.
Cardiologie Congenitale Strasbourg France.

Guy Vaksmann (G)

Department of Congenital Heart Disease Hôpital Privé de La Louvière Lille France.

Nicole Naccache (N)

Commission des Registres French Society of Cardiology Paris France.

Anissa Boubrit (A)

Adult Congenital Heart Disease Unit Hôpital Européen Georges Pompidou Centre de Référence des Malformations Cardiaques Congénitales Complexes Assistance Publique-Hôpitaux de Paris Paris University Paris France.

Vincent Bataille (V)

Department of Cardiology Rangueil Toulouse University Hospital University Paul Sabatier Toulouse France.

Sébastien Hascoet (S)

Division of Congenital Heart Disease, Expert Center for Complex Congenital Heart Disease (M3C Network) Marie Lannelongue Hospital Groupe Hospitalier Paris Saint Joseph Inserm UMRs-999 Paris-Saclay University Le Plessis Robinson France.

Magalie Ladouceur (M)

Adult Congenital Heart Disease Unit Hôpital Européen Georges Pompidou Centre de Référence des Malformations Cardiaques Congénitales Complexes Assistance Publique-Hôpitaux de Paris Paris University Paris France.
INSERM U970 Paris Centre de Recherche Cardiovasculaire Paris France.

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