Intravascular leiomyomatosis with extension to the inferior vena cava.


Journal

BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291

Informations de publication

Date de publication:
19 Jun 2023
Historique:
pmc-release: 19 06 2025
medline: 21 6 2023
pubmed: 20 6 2023
entrez: 19 6 2023
Statut: epublish

Résumé

Intravascular leiomyomatosis (IVL) is a rare benign smooth muscle neoplasm growing within the pelvic venous system, often with caval and intracardiac extension. It frequently coexists with uterine leiomyomas or occurs in women with a history of myomectomy or hysterectomy. IVL is often asymptomatic until intracardiac extension occurs, and carries a risk of sudden death, necessitating timely diagnosis and management. We present a case of IVL diagnosed on hysterectomy specimen with extension to the inferior vena cava found on follow-up imaging. The patient underwent complete resection with multidisciplinary involvement of Gynaecological Oncology and Vascular Surgery and remains disease free following 12 months of follow-up.

Identifiants

pubmed: 37336624
pii: 16/6/e253436
doi: 10.1136/bcr-2022-253436
pmc: PMC10314502
pii:
doi:

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© BMJ Publishing Group Limited 2023. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Jayna-Lee Garratt (JL)

King Edward Memorial Hospital for Women, Subiaco, Western Australia, Australia jlgarratt@bigpond.com.

Silipa Naiqiso (S)

King Edward Memorial Hospital for Women, Subiaco, Western Australia, Australia.

Joe Hockley (J)

Sir Charles Gairdner Hospital, Nedlands, Western Australia, Australia.
Curtin Medical School, Curtin University, Bentley, Western Australia, Australia.

Ganendra Raj Kader Ali Mohan (GRKA)

King Edward Memorial Hospital for Women, Subiaco, Western Australia, Australia.
School of Medicine, University of Notre Dame, Fremantle, Western Australia, Australia.

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Classifications MeSH