Interferon Gamma Enhances Cytoprotective Pathways via Nrf2 and MnSOD Induction in Friedreich's Ataxia Cells.
Friedreich’s ataxia
MnSOD
Nrf2
cytoprotection
interferon gamma
Journal
International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791
Informations de publication
Date de publication:
11 Aug 2023
11 Aug 2023
Historique:
received:
08
06
2023
revised:
27
07
2023
accepted:
08
08
2023
medline:
28
8
2023
pubmed:
26
8
2023
entrez:
26
8
2023
Statut:
epublish
Résumé
Friedreich's ataxia (FRDA) is a rare monogenic disease characterized by multisystem, slowly progressive degeneration. Because of the genetic defect in a non-coding region of
Identifiants
pubmed: 37628866
pii: ijms241612687
doi: 10.3390/ijms241612687
pmc: PMC10454386
pii:
doi:
Substances chimiques
Interferon-gamma
82115-62-6
NF-E2-Related Factor 2
0
Antioxidants
0
Hydrogen Peroxide
BBX060AN9V
Superoxide Dismutase
EC 1.15.1.1
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Subventions
Organisme : University of Rome Tor Vergata
ID : NA
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