The clinical utility and costs of whole-genome sequencing to detect cancer susceptibility variants-a multi-site prospective cohort study.

Diagnostic testing Familial cancer Genetics Health economics Variants Whole-genome sequencing

Journal

Genome medicine
ISSN: 1756-994X
Titre abrégé: Genome Med
Pays: England
ID NLM: 101475844

Informations de publication

Date de publication:
19 09 2023
Historique:
received: 04 10 2022
accepted: 18 08 2023
medline: 20 9 2023
pubmed: 19 9 2023
entrez: 18 9 2023
Statut: epublish

Résumé

Many families and individuals do not meet criteria for a known hereditary cancer syndrome but display unusual clusters of cancers. These families may carry pathogenic variants in cancer predisposition genes and be at higher risk for developing cancer. This multi-centre prospective study recruited 195 cancer-affected participants suspected to have a hereditary cancer syndrome for whom previous clinical targeted genetic testing was either not informative or not available. To identify pathogenic disease-causing variants explaining participant presentation, germline whole-genome sequencing (WGS) and a comprehensive cancer virtual gene panel analysis were undertaken. Pathogenic variants consistent with the presenting cancer(s) were identified in 5.1% (10/195) of participants and pathogenic variants considered secondary findings with potential risk management implications were identified in another 9.7% (19/195) of participants. Health economic analysis estimated the marginal cost per case with an actionable variant was significantly lower for upfront WGS with virtual panel ($8744AUD) compared to standard testing followed by WGS ($24,894AUD). Financial analysis suggests that national adoption of diagnostic WGS testing would require a ninefold increase in government annual expenditure compared to conventional testing. These findings make a case for replacing conventional testing with WGS to deliver clinically important benefits for cancer patients and families. The uptake of such an approach will depend on the perspectives of different payers on affordability.

Sections du résumé

BACKGROUND
Many families and individuals do not meet criteria for a known hereditary cancer syndrome but display unusual clusters of cancers. These families may carry pathogenic variants in cancer predisposition genes and be at higher risk for developing cancer.
METHODS
This multi-centre prospective study recruited 195 cancer-affected participants suspected to have a hereditary cancer syndrome for whom previous clinical targeted genetic testing was either not informative or not available. To identify pathogenic disease-causing variants explaining participant presentation, germline whole-genome sequencing (WGS) and a comprehensive cancer virtual gene panel analysis were undertaken.
RESULTS
Pathogenic variants consistent with the presenting cancer(s) were identified in 5.1% (10/195) of participants and pathogenic variants considered secondary findings with potential risk management implications were identified in another 9.7% (19/195) of participants. Health economic analysis estimated the marginal cost per case with an actionable variant was significantly lower for upfront WGS with virtual panel ($8744AUD) compared to standard testing followed by WGS ($24,894AUD). Financial analysis suggests that national adoption of diagnostic WGS testing would require a ninefold increase in government annual expenditure compared to conventional testing.
CONCLUSIONS
These findings make a case for replacing conventional testing with WGS to deliver clinically important benefits for cancer patients and families. The uptake of such an approach will depend on the perspectives of different payers on affordability.

Identifiants

pubmed: 37723522
doi: 10.1186/s13073-023-01223-1
pii: 10.1186/s13073-023-01223-1
pmc: PMC10507925
doi:

Types de publication

Multicenter Study Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

74

Informations de copyright

© 2023. BioMed Central Ltd., part of Springer Nature.

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Auteurs

Aimee L Davidson (AL)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Uwe Dressel (U)

Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Sarah Norris (S)

Faculty of Medicine and Health, University of Sydney, L2.22 The Quadrangle (A14), Sydney, NSW, 2006, Australia.

Daffodil M Canson (DM)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Dylan M Glubb (DM)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Cristina Fortuno (C)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Georgina E Hollway (GE)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Michael T Parsons (MT)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Miranda E Vidgen (ME)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Australian Genomics, Melbourne, VIC, Australia.

Oliver Holmes (O)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Lambros T Koufariotis (LT)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Vanessa Lakis (V)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Conrad Leonard (C)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Scott Wood (S)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Qinying Xu (Q)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Amy E McCart Reed (AE)

Centre for Clinical Research, University of Queensland, Brisbane, QLD, Australia.

Hilda A Pickett (HA)

Children's Medical Research Institute, University of Sydney, Westmead, NSW, Australia.

Mohammad K Al-Shinnag (MK)

Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.
Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Rachel L Austin (RL)

Australian Genomics, Melbourne, VIC, Australia.
Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Jo Burke (J)

Tasmanian Clinical Genetics Service, Royal Hobart Hospital, Hobart, TAS, Australia.

Elisa J Cops (EJ)

Parkville Familial Cancer Centre, Peter MacCallum Cancer Centre and Royal Melbourne Hospital, Melbourne, VIC, Australia.

Cassandra B Nichols (CB)

Genetic Services of Western Australia, King Edward Memorial Hospital, Subiaco, WA, Australia.

Annabel Goodwin (A)

Cancer Genetics Department, Royal Prince Alfred Hospital, Sydney, NSW, Australia.
University of Sydney, Sydney, NSW, Australia.

Marion T Harris (MT)

Monash Health Familial Cancer, Monash Health, Melbourne, VIC, Australia.
Faculty of Medicine, Nursing and Health Sciences, Monash University, Melbourne, VIC, Australia.

Megan J Higgins (MJ)

Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Emilia L Ip (EL)

Cancer Genetics, Liverpool Hospital, Sydney, NSW, Australia.

Catherine Kiraly-Borri (C)

Department of Health, Genetic Services of WA, Subiaco, WA, Australia.

Chiyan Lau (C)

Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.
Genomics, Pathology Queensland, Brisbane, QLD, Australia.

Julia L Mansour (JL)

Tasmanian Clinical Genetics Service, Royal Hobart Hospital, Hobart, TAS, Australia.

Michael W Millward (MW)

Tasmanian Clinical Genetics Service, Royal Hobart Hospital, Hobart, TAS, Australia.

Melissa J Monnik (MJ)

Adult Genetics Unit, Royal Adelaide Hospital, Adelaide, SA, Australia.

Nicholas S Pachter (NS)

Genetic Services of Western Australia, King Edward Memorial Hospital, Subiaco, WA, Australia.
Faculty of Health and Medical Sciences, University of Western Australia, Perth, WA, Australia.

Abiramy Ragunathan (A)

Familial Cancer Services, The Crown Princess Mary Cancer Centre, Westmead Hospital, Westmead, NSW, Australia.

Rachel D Susman (RD)

Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Sharron L Townshend (SL)

Genetic Services of Western Australia, King Edward Memorial Hospital, Subiaco, WA, Australia.

Alison H Trainer (AH)

Parkville Familial Cancer Centre, Peter MacCallum Cancer Centre and Royal Melbourne Hospital, Melbourne, VIC, Australia.
Department of Medicine, University of Melbourne, Melbourne, VIC, Australia.

Simon L Troth (SL)

Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Katherine M Tucker (KM)

Prince of Wales Clinical School, UNSW Medicine and Health, The University of New South Wales, Sydney, NSW, Australia.
Hereditary Cancer Centre, Prince of Wales Hospital, Sydney, NSW, Australia.

Mathew J Wallis (MJ)

Tasmanian Clinical Genetics Service, Royal Hobart Hospital, Hobart, TAS, Australia.
School of Medicine and Menzies Institute for Medical Research, University of Tasmania, Hobart, TAS, Australia.

Maie Walsh (M)

Parkville Familial Cancer Centre, Peter MacCallum Cancer Centre and Royal Melbourne Hospital, Melbourne, VIC, Australia.

Rachel A Williams (RA)

Prince of Wales Clinical School, UNSW Medicine and Health, The University of New South Wales, Sydney, NSW, Australia.
Hereditary Cancer Centre, Prince of Wales Hospital, Sydney, NSW, Australia.

Ingrid M Winship (IM)

Department of Medicine, University of Melbourne, Melbourne, VIC, Australia.
Genomic Medicine and Familial Cancer Clinic, Royal Melbourne Hospital, Melbourne, VIC, Australia.

Felicity Newell (F)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Emma Tudini (E)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Australian Genomics, Melbourne, VIC, Australia.

John V Pearson (JV)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.

Nicola K Poplawski (NK)

Adult Genetics Unit, Royal Adelaide Hospital, Adelaide, SA, Australia.
Adelaide Medical School, Faculty of Health and Medical Sciences, University of Adelaide, Adelaide, SA, Australia.

Helen G Mar Fan (HG)

Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.
Genetic Health Queensland, Royal Brisbane and Women's Hospital, Herston, QLD, Australia.

Paul A James (PA)

Parkville Familial Cancer Centre, Peter MacCallum Cancer Centre and Royal Melbourne Hospital, Melbourne, VIC, Australia.
Sir Peter MacCallum Department of Oncology, University of Melbourne, Melbourne, VIC, Australia.

Amanda B Spurdle (AB)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia. amanda.spurdle@qimrberghofer.edu.au.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia. amanda.spurdle@qimrberghofer.edu.au.

Nicola Waddell (N)

QIMR Berghofer Medical Research Institute, 300 Herston Road, Herston QLD 4006, Brisbane, QLD, Australia.
Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia.

Robyn L Ward (RL)

Faculty of Medicine, University of Queensland, Brisbane, QLD, Australia. robyn.ward@sydney.edu.au.
Faculty of Medicine and Health, University of Sydney, L2.22 The Quadrangle (A14), Sydney, NSW, 2006, Australia. robyn.ward@sydney.edu.au.

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