Lung Inflammatory Genes in Cystic Fibrosis and Their Relevance to Cystic Fibrosis Transmembrane Conductance Regulator Modulator Therapies.

CFTR CFTR modulator therapy airway epithelial cells cystic fibrosis gene polymorphisms lung disease macrophages neutrophils

Journal

Genes
ISSN: 2073-4425
Titre abrégé: Genes (Basel)
Pays: Switzerland
ID NLM: 101551097

Informations de publication

Date de publication:
20 10 2023
Historique:
received: 30 09 2023
revised: 16 10 2023
accepted: 17 10 2023
medline: 30 10 2023
pubmed: 28 10 2023
entrez: 28 10 2023
Statut: epublish

Résumé

Cystic fibrosis (CF) is a monogenic syndrome determined by over 2000 mutations in the

Identifiants

pubmed: 37895314
pii: genes14101966
doi: 10.3390/genes14101966
pmc: PMC10606852
pii:
doi:

Substances chimiques

Cystic Fibrosis Transmembrane Conductance Regulator 126880-72-6

Types de publication

Journal Article Review Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

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Auteurs

Annalucia Carbone (A)

Department of Clinical and Experimental Medicine, University of Foggia, 71122 Foggia, Italy.

Pamela Vitullo (P)

Cystic Fibrosis Support Center, Ospedale "G. Tatarella", 71042 Cerignola, Italy.

Sante Di Gioia (S)

Department of Clinical and Experimental Medicine, University of Foggia, 71122 Foggia, Italy.

Massimo Conese (M)

Department of Clinical and Experimental Medicine, University of Foggia, 71122 Foggia, Italy.

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