The astrocyte-produced growth factor HB-EGF limits autoimmune CNS pathology.


Journal

Nature immunology
ISSN: 1529-2916
Titre abrégé: Nat Immunol
Pays: United States
ID NLM: 100941354

Informations de publication

Date de publication:
26 Feb 2024
Historique:
received: 09 03 2023
accepted: 12 01 2024
medline: 27 2 2024
pubmed: 27 2 2024
entrez: 26 2 2024
Statut: aheadofprint

Résumé

Central nervous system (CNS)-resident cells such as microglia, oligodendrocytes and astrocytes are gaining increasing attention in respect to their contribution to CNS pathologies including multiple sclerosis (MS). Several studies have demonstrated the involvement of pro-inflammatory glial subsets in the pathogenesis and propagation of inflammatory events in MS and its animal models. However, it has only recently become clear that the underlying heterogeneity of astrocytes and microglia can not only drive inflammation, but also lead to its resolution through direct and indirect mechanisms. Failure of these tissue-protective mechanisms may potentiate disease and increase the risk of conversion to progressive stages of MS, for which currently available therapies are limited. Using proteomic analyses of cerebrospinal fluid specimens from patients with MS in combination with experimental studies, we here identify Heparin-binding EGF-like growth factor (HB-EGF) as a central mediator of tissue-protective and anti-inflammatory effects important for the recovery from acute inflammatory lesions in CNS autoimmunity. Hypoxic conditions drive the rapid upregulation of HB-EGF by astrocytes during early CNS inflammation, while pro-inflammatory conditions suppress trophic HB-EGF signaling through epigenetic modifications. Finally, we demonstrate both anti-inflammatory and tissue-protective effects of HB-EGF in a broad variety of cell types in vitro and use intranasal administration of HB-EGF in acute and post-acute stages of autoimmune neuroinflammation to attenuate disease in a preclinical mouse model of MS. Altogether, we identify astrocyte-derived HB-EGF and its epigenetic regulation as a modulator of autoimmune CNS inflammation and potential therapeutic target in MS.

Identifiants

pubmed: 38409259
doi: 10.1038/s41590-024-01756-6
pii: 10.1038/s41590-024-01756-6
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : EC | EU Framework Programme for Research and Innovation H2020 | H2020 Priority Excellent Science | H2020 European Research Council (H2020 Excellent Science - European Research Council)
ID : HICI 851693
Organisme : EC | EU Framework Programme for Research and Innovation H2020 | H2020 Priority Excellent Science | H2020 European Research Council (H2020 Excellent Science - European Research Council)
ID : HICI 851693
Organisme : EC | EU Framework Programme for Research and Innovation H2020 | H2020 Priority Excellent Science | H2020 European Research Council (H2020 Excellent Science - European Research Council)
ID : 818170
Organisme : EC | EU Framework Programme for Research and Innovation H2020 | H2020 Priority Excellent Science | H2020 European Research Council (H2020 Excellent Science - European Research Council)
ID : 818170
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 408885537
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 270949263
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : RO4866/3-1
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 270949263 - GRK2162
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : Project ID 270949263 - GRK2162, Project ID 405969122 - FOR2886
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 3908571
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : RO4866/3-1, 408885537 - TRR 274
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 408885537 - TRR 274
Organisme : Deutsche Forschungsgemeinschaft (German Research Foundation)
ID : 505539112 - GB.com
Organisme : Foundation for the National Institutes of Health (Foundation for the National Institutes of Health, Inc.)
ID : R01MH130458, R00NS114111
Organisme : Foundation for the National Institutes of Health (Foundation for the National Institutes of Health, Inc.)
ID : NS087867, ES025530, ES032323, AI126880 and AI149699
Organisme : Forskningsrådet om Hälsa, Arbetsliv och Välfärd (Swedish Research Council for Health, Working Life and Welfare)
ID : 2018-05973
Organisme : Forskningsrådet om Hälsa, Arbetsliv och Välfärd (Swedish Research Council for Health, Working Life and Welfare)
ID : 2021-02977

Informations de copyright

© 2024. The Author(s).

Références

Lassmann, H. Multiple sclerosis pathology. Cold Spring Harb. Perspect. Med. 8, a028936 (2018).
pubmed: 29358320 pmcid: 5830904 doi: 10.1101/cshperspect.a028936
Thompson, A. J. et al. Diagnosis of multiple sclerosis: 2017 revisions of the McDonald criteria. Lancet Neurol. 17, 162–173 (2018).
pubmed: 29275977 doi: 10.1016/S1474-4422(17)30470-2
Polman, C. H. et al. Diagnostic criteria for multiple sclerosis: 2010 revisions to the McDonald criteria. Ann. Neurol. 69, 292–302 (2011).
pubmed: 21387374 pmcid: 3084507 doi: 10.1002/ana.22366
Miller, D., Barkhof, F., Montalban, X., Thompson, A. & Filippi, M. Clinically isolated syndromes suggestive of multiple sclerosis, part I: natural history, pathogenesis, diagnosis, and prognosis. Lancet Neurol. 4, 281–288 (2005).
pubmed: 15847841 doi: 10.1016/S1474-4422(05)70071-5
Lebrun-Frénay, C. et al. Risk factors and time to clinical symptoms of multiple sclerosis among patients with radiologically isolated syndrome. JAMA Netw. Open 4, e2128271 (2021).
pubmed: 34633424 pmcid: 8506228 doi: 10.1001/jamanetworkopen.2021.28271
Brownlee, W. J. et al. Early imaging predictors of long-term outcomes in relapse-onset multiple sclerosis. Brain 142, 2276–2287 (2019).
pubmed: 31342055 doi: 10.1093/brain/awz156
Kuhle, J. et al. Conversion from clinically isolated syndrome to multiple sclerosis: a large multicentre study. Mult. Scler. 21, 1013–1024 (2015).
pubmed: 25680984 doi: 10.1177/1352458514568827
Jacobs, L. D. et al. Intramuscular interferon beta-1a therapy initiated during a first demyelinating event in multiple sclerosis. CHAMPS Study Group. N. Engl. J. Med. 343, 898–904 (2000).
pubmed: 11006365 doi: 10.1056/NEJM200009283431301
Comi, G. et al. Effect of early interferon treatment on conversion to definite multiple sclerosis: a randomised study. Lancet 357, 1576–1582 (2001).
pubmed: 11377645 doi: 10.1016/S0140-6736(00)04725-5
Comi, G. et al. Effect of glatiramer acetate on conversion to clinically definite multiple sclerosis in patients with clinically isolated syndrome (PreCISe study): a randomised, double-blind, placebo-controlled trial. Lancet 374, 1503–1511 (2009).
pubmed: 19815268 doi: 10.1016/S0140-6736(09)61259-9
Linnerbauer, M. & Rothhammer, V. Protective functions of reactive astrocytes following central nervous system insult. Front. Immunol. 11, 573256 (2020).
pubmed: 33117368 pmcid: 7561408 doi: 10.3389/fimmu.2020.573256
Hohlfeld, R. Neurotrophic cross-talk between the nervous and immune systems: relevance for repair strategies in multiple sclerosis? J. Neurol. Sci. 265, 93–96 (2008).
pubmed: 17459415 doi: 10.1016/j.jns.2007.03.012
Dao, D. T., Anez-Bustillos, L., Adam, R. M., Puder, M. & Bielenberg, D. R. Heparin-binding epidermal growth factor-like growth factor as a critical mediator of tissue repair and regeneration. Am. J. Pathol. 188, 2446–2456 (2018).
pubmed: 30142332 pmcid: 6207098 doi: 10.1016/j.ajpath.2018.07.016
Jin, K. et al. Heparin-binding epidermal growth factor-like growth factor: hypoxia-inducible expression in vitro and stimulation of neurogenesis in vitro and in vivo. J. Neurosci. 22, 5365–5373 (2002).
pubmed: 12097488 pmcid: 6758221 doi: 10.1523/JNEUROSCI.22-13-05365.2002
Oyagi, A. et al. Forebrain specific heparin-binding epidermal growth factor-like growth factor knockout mice show exacerbated ischemia and reperfusion injury. Neuroscience 185, 116–124 (2011).
pubmed: 21524692 doi: 10.1016/j.neuroscience.2011.04.034
Filippi, M. et al. Intracortical lesions: relevance for new MRI diagnostic criteria for multiple sclerosis. Neurology 75, 1988–1994 (2010).
pubmed: 21115953 doi: 10.1212/WNL.0b013e3181ff96f6
Liddelow, S. A. et al. Neurotoxic reactive astrocytes are induced by activated microglia. Nature 541, 481–487 (2017).
pubmed: 28099414 pmcid: 5404890 doi: 10.1038/nature21029
Sanmarco, L. M. et al. Gut-licensed IFNγ
pubmed: 33408417 pmcid: 8039910 doi: 10.1038/s41586-020-03116-4
Berard, J. L., Wolak, K., Fournier, S. & David, S. Characterization of relapsing–remitting and chronic forms of experimental autoimmune encephalomyelitis in C57BL/6 mice. Glia 58, 434–445 (2010).
pubmed: 19780195 doi: 10.1002/glia.20935
Wheeler, M. A. et al. MAFG-driven astrocytes promote CNS inflammation. Nature 578, 593–599 (2020).
pubmed: 32051591 pmcid: 8049843 doi: 10.1038/s41586-020-1999-0
Tusher, V. G., Tibshirani, R. & Chu, G. Significance analysis of microarrays applied to the ionizing radiation response. Proc. Natl Acad. Sci. USA 98, 5116–5121 (2001).
pubmed: 11309499 pmcid: 33173 doi: 10.1073/pnas.091062498
Valentin-Torres, A. et al. Sustained TNF production by central nervous system infiltrating macrophages promotes progressive autoimmune encephalomyelitis. J. Neuroinflammation 13, 46 (2016).
pubmed: 26906225 pmcid: 4763407 doi: 10.1186/s12974-016-0513-y
Lin, C.-C. & Edelson, B. T. New insights into the role of IL-1β in experimental autoimmune encephalomyelitis and multiple sclerosis. J. Immunol. 198, 4553–4560 (2017).
pubmed: 28583987 doi: 10.4049/jimmunol.1700263
Mandl, M., Lieberum, M.-K. & Depping, R. A HIF-1α-driven feed-forward loop augments HIF signalling in Hep3B cells by upregulation of ARNT. Cell Death Dis. 7, e2284 (2016).
pubmed: 27362802 pmcid: 5108338 doi: 10.1038/cddis.2016.187
Vorrink, S. U. & Domann, F. E. Regulatory crosstalk and interference between the xenobiotic and hypoxia sensing pathways at the AhR-ARNT-HIF1α signaling node. Chem. Biol. Interact. 0, 82–88 (2014).
pmcid: 4091760 doi: 10.1016/j.cbi.2014.05.001
Chan, W. K., Yao, G., Gu, Y.-Z. & Bradfield, C. A. Cross-talk between the Aryl hydrocarbon receptor and hypoxia inducible factor signaling pathways: demonstration of competition and compensation. J. Biol. Chem. 274, 12115–12123 (1999).
pubmed: 10207038 doi: 10.1074/jbc.274.17.12115
Linnerbauer, M., Wheeler, M. A. & Quintana, F. J. Astrocyte crosstalk in CNS inflammation. Neuron 108, 608–622 (2020).
pubmed: 32898475 pmcid: 7704785 doi: 10.1016/j.neuron.2020.08.012
Browaeys, R., Saelens, W. & Saeys, Y. NicheNet: modeling intercellular communication by linking ligands to target genes. Nat. Methods 17, 159–162 (2020).
pubmed: 31819264 doi: 10.1038/s41592-019-0667-5
Foo, L. C. et al. Development of a novel method for the purification and culture of rodent astrocytes. Neuron 71, 799–811 (2011).
pubmed: 21903074 pmcid: 3172573 doi: 10.1016/j.neuron.2011.07.022
Puschmann, T. B. et al. HB-EGF affects astrocyte morphology, proliferation, differentiation, and the expression of intermediate filament proteins. J. Neurochem. 128, 878–889 (2014).
pubmed: 24188029 doi: 10.1111/jnc.12519
Bartus, K. et al. ErbB receptor signaling directly controls oligodendrocyte progenitor cell transformation and spontaneous remyelination after spinal cord injury. Glia 67, 1036–1046 (2019).
pubmed: 30637799 pmcid: 6491970 doi: 10.1002/glia.23586
Kaufmann, M. et al. Identification of early neurodegenerative pathways in progressive multiple sclerosis. Nat. Neurosci. 25, 944–955 (2022).
pubmed: 35726057 doi: 10.1038/s41593-022-01097-3
Opanashuk, L. A. et al. Heparin-binding epidermal growth factor-like growth factor in hippocampus: modulation of expression by seizures and anti-excitotoxic action. J. Neurosci. 19, 133–146 (1999).
pubmed: 9870945 pmcid: 6782387 doi: 10.1523/JNEUROSCI.19-01-00133.1999
Rothhammer, V. et al. Type I interferons and microbial metabolites of tryptophan modulate astrocyte activity and central nervous system inflammation via the aryl hydrocarbon receptor. Nat. Med. 22, 586–597 (2016).
pubmed: 27158906 pmcid: 4899206 doi: 10.1038/nm.4106
Ross, T. M. et al. Intranasal administration of interferon beta bypasses the blood-brain barrier to target the central nervous system and cervical lymph nodes: a non-invasive treatment strategy for multiple sclerosis. J. Neuroimmunol. 151, 66–77 (2004).
pubmed: 15145605 doi: 10.1016/j.jneuroim.2004.02.011
Ransohoff, R. M. Animal models of multiple sclerosis: the good, the bad and the bottom line. Nat. Neurosci. 15, 1074–1077 (2012).
pubmed: 22837037 pmcid: 7097342 doi: 10.1038/nn.3168
Kular, L. et al. DNA methylation changes in glial cells of the normal-appearing white matter in multiple sclerosis patients. Epigenetics 17, 1311–1330 (2022).
pubmed: 35094644 pmcid: 9586622 doi: 10.1080/15592294.2021.2020436
Huynh, J. L. et al. Epigenome-wide differences in pathology-free regions of multiple sclerosis–affected brains. Nat. Neurosci. 17, 121–130 (2014).
pubmed: 24270187 doi: 10.1038/nn.3588
Oh, J. & Bar-Or, A. Emerging therapies to target CNS pathophysiology in multiple sclerosis. Nat. Rev. Neurol. 18, 466–475 (2022).
pubmed: 35697862 doi: 10.1038/s41582-022-00675-0
Healy, L. M., Stratton, J. A., Kuhlmann, T. & Antel, J. The role of glial cells in multiple sclerosis disease progression. Nat. Rev. Neurol. 18, 237–248 (2022).
pubmed: 35190704 doi: 10.1038/s41582-022-00624-x
Kuhlmann, T., Lingfeld, G., Bitsch, A., Schuchardt, J. & Brück, W. Acute axonal damage in multiple sclerosis is most extensive in early disease stages and decreases over time. Brain 125, 2202–2212 (2002).
pubmed: 12244078 doi: 10.1093/brain/awf235
Elkjaer, M. L. et al. CSF proteome in multiple sclerosis subtypes related to brain lesion transcriptomes. Sci. Rep. 11, 4132 (2021).
pubmed: 33603109 pmcid: 7892884 doi: 10.1038/s41598-021-83591-5
Schenk, G. J. et al. Roles for HB-EGF and CD9 in multiple sclerosis. Glia 61, 1890–1905 (2013).
pubmed: 24038577 doi: 10.1002/glia.22565
Hoffmann, F. S. et al. Fingolimod induces neuroprotective factors in human astrocytes. J. Neuroinflammation 12, 184 (2015).
pubmed: 26419927 pmcid: 4589103 doi: 10.1186/s12974-015-0393-6
Jacob, A. et al. Hypoxia interferes with aryl hydrocarbon receptor pathway in hCMEC/D3 human cerebral microvascular endothelial cells. J. Neurochem. 132, 373–383 (2015).
pubmed: 25327972 doi: 10.1111/jnc.12972
Lassmann, H. Hypoxia-like tissue injury as a component of multiple sclerosis lesions. J. Neurol. Sci. 206, 187–191 (2003).
pubmed: 12559509 doi: 10.1016/S0022-510X(02)00421-5
Halder, S. K. & Milner, R. Chronic mild hypoxia accelerates recovery from preexisting EAE by enhancing vascular integrity and apoptosis of infiltrated monocytes. Proc. Natl Acad. Sci. USA 117, 11126–11135 (2020).
pubmed: 32371484 pmcid: 7245138 doi: 10.1073/pnas.1920935117
Chan, M. W. Y. et al. Low-dose 5-aza-2′-deoxycytidine pretreatment inhibits experimental autoimmune encephalomyelitis by induction of regulatory T cells. Mol. Med. 20, 248–256 (2014).
pubmed: 24869907 pmcid: 4107100 doi: 10.2119/molmed.2013.00159
Mangano, K. et al. Hypomethylating agent 5-aza-2′-deoxycytidine (DAC) ameliorates multiple sclerosis in mouse models. J. Cell. Physiol. 229, 1918–1925 (2014).
pubmed: 24700487 doi: 10.1002/jcp.24641
Scafidi, J. et al. Intranasal epidermal growth factor treatment rescues neonatal brain injury. Nature 506, 230–234 (2014).
pubmed: 24390343 doi: 10.1038/nature12880
Sandelin, A., Alkema, W., Engström, P., Wasserman, W. W. & Lenhard, B. JASPAR: an open-access database for eukaryotic transcription factor binding profiles. Nucleic Acids Res. 32, D91–D94 (2004).
pubmed: 14681366 pmcid: 308747 doi: 10.1093/nar/gkh012
Linnerbauer, M. et al. PD-L1 positive astrocytes attenuate inflammatory functions of PD-1 positive microglia in models of autoimmune neuroinflammation. Nat. Commun. 14, 5555 (2023).
pubmed: 37689786 pmcid: 10492803 doi: 10.1038/s41467-023-40982-8
Clark, I. C. et al. Barcoded viral tracing of single-cell interactions in central nervous system inflammation. Science 372, eabf1230 (2021).
pubmed: 33888612 pmcid: 8157482 doi: 10.1126/science.abf1230
Linnerbauer, M. et al. Astrocyte-derived pleiotrophin mitigates late-stage autoimmune CNS inflammation. Front. Immunol. 12, 800128 (2022).
pubmed: 35046956 pmcid: 8762329 doi: 10.3389/fimmu.2021.800128
McCarthy, K. D. & de Vellis, J. Preparation of separate astroglial and oligodendroglial cell cultures from rat cerebral tissue. J. Cell Biol. 85, 890–902 (1980).
pubmed: 6248568 doi: 10.1083/jcb.85.3.890
Wagner, A. et al. Metabolic modeling of single Th17 cells reveals regulators of autoimmunity. Cell 184, 4168–4185.e21 (2021).
pubmed: 34216539 pmcid: 8621950 doi: 10.1016/j.cell.2021.05.045
Rothhammer, V. et al. Th17 lymphocytes traffic to the central nervous system independently of α4 integrin expression during EAE. J. Exp. Med. 208, 2465–2476 (2011).
pubmed: 22025301 pmcid: 3256959 doi: 10.1084/jem.20110434
Bosch-Queralt, M. et al. Diet-dependent regulation of TGFβ impairs reparative innate immune responses after demyelination. Nat. Metab. 3, 211–227 (2021).
pubmed: 33619376 pmcid: 7610359 doi: 10.1038/s42255-021-00341-7
Rothhammer, V. et al. Microglial control of astrocytes in response to microbial metabolites. Nature 557, 724–728 (2018).
pubmed: 29769726 pmcid: 6422159 doi: 10.1038/s41586-018-0119-x
Linnerbauer, M. et al. Intranasal delivery of a small-molecule ErbB inhibitor promotes recovery from acute and late-stage CNS inflammation. JCI Insight 7, e154824 (2022).
pubmed: 35393953 pmcid: 9057609 doi: 10.1172/jci.insight.154824
Wolf, I. et al. The Medical Imaging Interaction Toolkit. Med. Image Anal. 9, 594–604 (2005).
pubmed: 15896995 doi: 10.1016/j.media.2005.04.005
Tsaktanis, T. et al. Aryl hydrocarbon receptor plasma agonist activity correlates with disease activity in progressive MS. Neurol. Neuroimmunol. Neuroinflamm. 8, e933 (2021).
pubmed: 33361385 doi: 10.1212/NXI.0000000000000933
Untergasser, A. et al. Primer3—new capabilities and interfaces. Nucleic Acids Res. 40, e115 (2012).
pubmed: 22730293 pmcid: 3424584 doi: 10.1093/nar/gks596
Ewels, P. A. et al. The nf-core framework for community-curated bioinformatics pipelines. Nat. Biotechnol. 38, 276–278 (2020).
pubmed: 32055031 doi: 10.1038/s41587-020-0439-x
Ritchie, M. E. et al. limma powers differential expression analyses for RNA-sequencing and microarray studies. Nucleic Acids Res. 43, e47 (2015).
pubmed: 25605792 pmcid: 4402510 doi: 10.1093/nar/gkv007
Moore, J. E. et al. Expanded encyclopaedias of DNA elements in the human and mouse genomes. Nature 583, 699–710 (2020).
pubmed: 32728249 pmcid: 7410828 doi: 10.1038/s41586-020-2493-4
Navarro Gonzalez, J. et al. The UCSC Genome Browser database: 2021 update. Nucleic Acids Res. 49, D1046–D1057 (2021).
pubmed: 33221922 doi: 10.1093/nar/gkaa1070
Hahne, F. & Ivanek, R. Visualizing genomic data using Gviz and Bioconductor. Methods Mol. Biol. 1418, 335–351 (2016).
pubmed: 27008022 doi: 10.1007/978-1-4939-3578-9_16
Morris, T. J. et al. ChAMP: 450k chip analysis methylation pipeline. Bioinformatics 30, 428–430 (2014).
pubmed: 24336642 doi: 10.1093/bioinformatics/btt684
Aryee, M. J. et al. Minfi: a flexible and comprehensive Bioconductor package for the analysis of Infinium DNA methylation microarrays. Bioinformatics 30, 1363–1369 (2014).
pubmed: 24478339 pmcid: 4016708 doi: 10.1093/bioinformatics/btu049
McCartney, D. L. et al. Identification of polymorphic and off-target probe binding sites on the Illumina Infinium MethylationEPIC BeadChip. Genom. Data 9, 22–24 (2016).
pubmed: 27330998 pmcid: 4909830 doi: 10.1016/j.gdata.2016.05.012
Pidsley, R. et al. Critical evaluation of the Illumina MethylationEPIC BeadChip microarray for whole-genome DNA methylation profiling. Genome Biol. 17, 208 (2016).
pubmed: 27717381 pmcid: 5055731 doi: 10.1186/s13059-016-1066-1
Nordlund, J. et al. Genome-wide signatures of differential DNA methylation in pediatric acute lymphoblastic leukemia. Genome Biol. 14, r105 (2013).
pubmed: 24063430 pmcid: 4014804 doi: 10.1186/gb-2013-14-9-r105
Chen, Y. et al. Discovery of cross-reactive probes and polymorphic CpGs in the Illumina Infinium HumanMethylation450 microarray. Epigenetics 8, 203–209 (2013).
pubmed: 23314698 pmcid: 3592906 doi: 10.4161/epi.23470
Johnson, W. E., Li, C. & Rabinovic, A. Adjusting batch effects in microarray expression data using empirical Bayes methods. Biostatistics 8, 118–127 (2007).
pubmed: 16632515 doi: 10.1093/biostatistics/kxj037
Houseman, E. A., Molitor, J. & Marsit, C. J. Reference-free cell mixture adjustments in analysis of DNA methylation data. Bioinformatics 30, 1431–1439 (2014).
pubmed: 24451622 pmcid: 4016702 doi: 10.1093/bioinformatics/btu029
Subramanian, A. et al. Gene set enrichment analysis: a knowledge-based approach for interpreting genome-wide expression profiles. Proc. Natl Acad. Sci. USA 102, 15545–15550 (2005).
pubmed: 16199517 pmcid: 1239896 doi: 10.1073/pnas.0506580102
Mootha, V. K. et al. PGC-1α-responsive genes involved in oxidative phosphorylation are coordinately downregulated in human diabetes. Nat. Genet. 34, 267–273 (2003).
pubmed: 12808457 doi: 10.1038/ng1180
Mi, H. et al. Protocol update for large-scale genome and gene function analysis with PANTHER classification system (v.14.0). Nat. Protoc. 14, 703–721 (2019).
pubmed: 30804569 pmcid: 6519457 doi: 10.1038/s41596-019-0128-8
Hao, Y. et al. Integrated analysis of multimodal single-cell data. Cell 184, 3573–3587.e29 (2021).
pubmed: 34062119 pmcid: 8238499 doi: 10.1016/j.cell.2021.04.048
Chen, E. Y. et al. Enrichr: interactive and collaborative HTML5 gene list enrichment analysis tool. BMC Bioinformatics 14, 128 (2013).
pubmed: 23586463 pmcid: 3637064 doi: 10.1186/1471-2105-14-128
Cao, J. et al. A human cell atlas of fetal gene expression. Science 370, eaba7721 (2020).
pubmed: 33184181 pmcid: 7780123 doi: 10.1126/science.aba7721

Auteurs

Mathias Linnerbauer (M)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Lena Lößlein (L)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Oliver Vandrey (O)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Anne Peter (A)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Yanan Han (Y)

Department of Clinical Neuroscience, Karolinska Institutet, Karolinska University Hospital, Center for Molecular Medicine, Stockholm, Sweden.

Thanos Tsaktanis (T)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Emile Wogram (E)

Institute of Neuropathology, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

Maria Needhamsen (M)

Department of Clinical Neuroscience, Karolinska Institutet, Karolinska University Hospital, Center for Molecular Medicine, Stockholm, Sweden.

Lara Kular (L)

Department of Clinical Neuroscience, Karolinska Institutet, Karolinska University Hospital, Center for Molecular Medicine, Stockholm, Sweden.

Lisa Nagel (L)

Institute of Radiology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Julia Zissler (J)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Marie Andert (M)

Department of Molecular Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Lisa Meszaros (L)

Department of Molecular Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Jannis Hanspach (J)

Institute of Radiology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Finnja Zuber (F)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Ulrike J Naumann (UJ)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Martin Diebold (M)

Institute of Neuropathology, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

Michael A Wheeler (MA)

Ann Romney Center for Neurologic Diseases, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
The Broad Institute of Harvard and MIT, Cambridge, MA, USA.

Tobias Beyer (T)

Department of Neurology, Klinikum rechts der Isar, Technical University of Munich, Munich, Germany.

Lucy Nirschl (L)

Department of Neurology, Klinikum rechts der Isar, Technical University of Munich, Munich, Germany.

Ana Cirac (A)

Department of Neurology, Klinikum rechts der Isar, Technical University of Munich, Munich, Germany.

Frederik B Laun (FB)

Institute of Radiology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Claudia Günther (C)

Department of Medicine 1, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Jürgen Winkler (J)

Institute of Neuropathology, Faculty of Medicine, University of Freiburg, Freiburg, Germany.

Tobias Bäuerle (T)

Institute of Radiology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany.

Maja Jagodic (M)

Department of Clinical Neuroscience, Karolinska Institutet, Karolinska University Hospital, Center for Molecular Medicine, Stockholm, Sweden.

Bernhard Hemmer (B)

Department of Neurology, Klinikum rechts der Isar, Technical University of Munich, Munich, Germany.
Munich Cluster for Systems Neurology (SyNergy), Munich, Germany.

Marco Prinz (M)

Institute of Neuropathology, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Center for Basics in NeuroModulation (NeuroModulBasics), Faculty of Medicine, University of Freiburg, Freiburg, Germany.
Signalling Research Centres BIOSS and CIBSS, University of Freiburg, Freiburg, Germany.

Francisco J Quintana (FJ)

Ann Romney Center for Neurologic Diseases, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
The Broad Institute of Harvard and MIT, Cambridge, MA, USA.

Veit Rothhammer (V)

Department of Neurology, University Hospital Erlangen, Friedrich-Alexander University Erlangen Nuremberg, Erlangen, Germany. veit.rothhammer@fau.de.
Deutsches Zentrum Immuntherapie (DZI), University Hospital Erlangen, Erlangen, Germany. veit.rothhammer@fau.de.

Classifications MeSH