Germline HAVCR2/TIM-3 Checkpoint Inhibitor Receptor Deficiency in Recurrent Autoinflammatory Myocarditis.


Journal

Journal of clinical immunology
ISSN: 1573-2592
Titre abrégé: J Clin Immunol
Pays: Netherlands
ID NLM: 8102137

Informations de publication

Date de publication:
15 Mar 2024
Historique:
received: 15 12 2023
accepted: 04 03 2024
medline: 18 3 2024
pubmed: 15 3 2024
entrez: 15 3 2024
Statut: epublish

Résumé

Myocarditis can be caused by viral infection, drug reaction or general inflammatory condition. To provide understanding on inflammatory myocarditis, we describe clinical, genetic, and immunological properties of a young male patient who suffered from recurrent myocarditis episodes since the age of four years. Electrocardiography, troponin I/T, echocardiography, myocardial magnetic resonance imaging and histological findings were consistent with recurrent myocarditis episodes. Homozygous c.245 A > G p.Tyr82Cys pathogenic variant in Hepatitis A Virus Cellular Receptor 2 (HAVCR2) gene encoding T cell immunoglobulin and mucin domain-containing protein 3 (TIM-3) receptor was found. Peripheral blood mononuclear cells were collected when the patient was asymptomatic; CD4

Identifiants

pubmed: 38485795
doi: 10.1007/s10875-024-01685-x
pii: 10.1007/s10875-024-01685-x
pmc: PMC10940375
doi:

Substances chimiques

Hepatitis A Virus Cellular Receptor 2 0
Interleukin 1 Receptor Antagonist Protein 0
Interleukin-1beta 0
HAVCR2 protein, human 0

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

81

Informations de copyright

© 2024. The Author(s).

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Auteurs

Nora Pernaa (N)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.

Anni Vakkuri (A)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.

Miika Arvonen (M)

Department of Pediatrics, Kuopio University Hospital and University of Eastern Finland, Kuopio, Finland.

Outi Kuismin (O)

Department of Clinical Genetics, Oulu University Hospital, Kajaanintie 50, Oulu, 90220, Finland.

Wenny Santaniemi (W)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.

Virpi Glumoff (V)

Medical Research Laboratory Unit, Faculty of Medicine, University of Oulu, Oulu, Finland.

Elisa Lappi-Blanco (E)

Department of Pathology, University of Oulu, Aapistie 5, Oulu, Finland.

Ulla Lantto (U)

Department of Otorhinolaryngology-Head and Neck Surgery, Oulu University Hospital, Oulu, Finland.

Marjo Okkonen (M)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.

Kari Kaikkonen (K)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.

Juhani Junttila (J)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.
Biocenter Oulu, University of Oulu, Oulu, Finland.

Risto Kerkelä (R)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.
Biocenter Oulu, University of Oulu, Oulu, Finland.

Pirjo Åström (P)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland.
Biocenter Oulu, University of Oulu, Oulu, Finland.

Timo Hautala (T)

Research Unit of Biomedicine and Internal Medicine, Medical Research Center Oulu, University of Oulu and Oulu University Hospital, Oulu, FIN-90014, Finland. timo.hautala@oulu.fi.
Infectious Diseases, Oulu University Hospital, Oulu, Finland. timo.hautala@oulu.fi.

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Classifications MeSH