Patient experiences of interprofessional collaboration and intersectoral communication in rare disease healthcare in Germany - a mixed-methods study.


Journal

Orphanet journal of rare diseases
ISSN: 1750-1172
Titre abrégé: Orphanet J Rare Dis
Pays: England
ID NLM: 101266602

Informations de publication

Date de publication:
13 May 2024
Historique:
received: 21 12 2023
accepted: 05 05 2024
medline: 14 5 2024
pubmed: 14 5 2024
entrez: 13 5 2024
Statut: epublish

Résumé

Rare diseases are often complex, chronic and many of them life-shortening. In Germany, healthcare for rare diseases is organized in expert centers for rare diseases. Most patients additionally have regional general practicioners and specialists for basic medical care. Thus, collaboration and information exchange between sectors is highly relevant. Our study focuses on the patient and caregiver perspective on intersectoral and interdisciplinary care between local healthcare professionals (HCPs) and centers for rare diseases in Germany. The aims were (1) to investigate patients' and caregivers' general experience of healthcare, (2) to analyse patients' and caregivers' perception of collaboration and cooperation between local healthcare professionals and expert centers for rare diseases and (3) to investigate patients' and caregivers' satisfaction with healthcare in the expert centers for rare diseases. In total 299 individuals of whom 176 were patients and 123 were caregivers to pediatric patients participated in a survey using a questionnaire comprising several instruments and constructs. Fifty participants were additionally interviewed using a semistructured guideline. Most patients reported to receive written information about their care, have a contact person for medical issues and experienced interdisciplinary exchange within the centers for rare diseases. Patients and caregivers in our sample were mainly satisfied with the healthcare in the centers for rare diseases. The qualitative interviews showed a rather mixed picture including experiences of uncoordinated care, low engagement and communication difficulties between professionals of different sectors. Patients reported several factors that influenced the organization and quality of healthcare e.g. engagement and health literacy in patients or engagement of HCPs. Our findings indicate the high relevance of transferring affected patients to specialized care as fast as possible to provide best medical treatment and increase patient satisfaction. Intersectoral collaboration should exceed written information exchange and should unburden patients of being and feeling responsible for communication between sectors and specialists. Results indicate a lack of inclusion of psychosocial aspects in routine care, which suggests opportunities for necessary improvements.

Sections du résumé

BACKGROUND BACKGROUND
Rare diseases are often complex, chronic and many of them life-shortening. In Germany, healthcare for rare diseases is organized in expert centers for rare diseases. Most patients additionally have regional general practicioners and specialists for basic medical care. Thus, collaboration and information exchange between sectors is highly relevant. Our study focuses on the patient and caregiver perspective on intersectoral and interdisciplinary care between local healthcare professionals (HCPs) and centers for rare diseases in Germany. The aims were (1) to investigate patients' and caregivers' general experience of healthcare, (2) to analyse patients' and caregivers' perception of collaboration and cooperation between local healthcare professionals and expert centers for rare diseases and (3) to investigate patients' and caregivers' satisfaction with healthcare in the expert centers for rare diseases.
RESULTS RESULTS
In total 299 individuals of whom 176 were patients and 123 were caregivers to pediatric patients participated in a survey using a questionnaire comprising several instruments and constructs. Fifty participants were additionally interviewed using a semistructured guideline. Most patients reported to receive written information about their care, have a contact person for medical issues and experienced interdisciplinary exchange within the centers for rare diseases. Patients and caregivers in our sample were mainly satisfied with the healthcare in the centers for rare diseases. The qualitative interviews showed a rather mixed picture including experiences of uncoordinated care, low engagement and communication difficulties between professionals of different sectors. Patients reported several factors that influenced the organization and quality of healthcare e.g. engagement and health literacy in patients or engagement of HCPs.
CONCLUSIONS CONCLUSIONS
Our findings indicate the high relevance of transferring affected patients to specialized care as fast as possible to provide best medical treatment and increase patient satisfaction. Intersectoral collaboration should exceed written information exchange and should unburden patients of being and feeling responsible for communication between sectors and specialists. Results indicate a lack of inclusion of psychosocial aspects in routine care, which suggests opportunities for necessary improvements.

Identifiants

pubmed: 38741100
doi: 10.1186/s13023-024-03207-9
pii: 10.1186/s13023-024-03207-9
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

197

Informations de copyright

© 2024. The Author(s).

Références

European Union. Regulation (EC) N°141/2000 of the European Parliament and of the Council of 16 December 1999 on orphan medicinal products… 2000 14.08.2022]; http://eurlex.europa.eu/LexUriServ/LexUriServ.do?uri=OJ:L:2000:018:0001:0005:EN:PDF
Nguengang Wakap S, et al. Estimating cumulative point prevalence of rare diseases: analysis of the Orphanet database. Eur J Hum Genet. 2020;28(2):165–73.
doi: 10.1038/s41431-019-0508-0 pubmed: 31527858
Haendel M, et al. How many rare diseases are there? Nat Rev Drug Discovery. 2020;19(2):77–8.
doi: 10.1038/d41573-019-00180-y pubmed: 32020066
Vicente E, Pruneda L, Ardanaz E. Regarding the estimations of people affected by rare diseases. Eur J Hum Genet. 2021;29(6):1032–3.
doi: 10.1038/s41431-020-00763-z pubmed: 33262443
Gunne E, et al. An estimate of the cumulative paediatric prevalence of rare diseases in Ireland and comment on the literature. Eur J Hum Genet. 2022;30(11):1211–5.
doi: 10.1038/s41431-022-01144-4 pubmed: 35853949 pmcid: 9626478
Zurynski Y, et al. Australian children living with rare diseases: experiences of diagnosis and perceived consequences of diagnostic delays. Orphanet J Rare Dis. 2017;12(1):68.
doi: 10.1186/s13023-017-0622-4 pubmed: 28399928 pmcid: 5387276
Austin CP, et al. Future of Rare diseases Research 2017–2027: an IRDiRC perspective. Clin Transl Sci. 2018;11(1):21–7.
doi: 10.1111/cts.12500 pubmed: 28796445
von der Lippe C, Neteland I, Feragen KB. Children with a rare congenital genetic disorder: a systematic review of parent experiences. Orphanet J Rare Dis. 2022;17(1):375.
doi: 10.1186/s13023-022-02525-0 pubmed: 36253830 pmcid: 9575260
NAMSE. Nationaler Aktionsplan für Menschen mit seltenen Erkrankungen. 2013 24.11.2022]; https://www.bundesgesundheitsministerium.de/fileadmin/Dateien/3_Downloads/N/NAMSE/Nationaler_Aktionsplan_fuer_Menschen_mit_Seltenen_Erkrankungen_-_Handlungsfelder__Empfehlungen_und_Massnahmenvorschlaege.pdf
Hebestreit H. Centers for rare diseases-Structures, tasks and networks. Gefasschirurgie: Z fur Vaskulare und Endovaskulare Chirurgie : Organ Der Deutschen Und Der Osterreichischen Gesellschaft fur Gefasschirurgie Unter Mitarbeit Der Schweizerischen Gesellschaft fur Gefasschirurgie. 2021;26(8):577–82.
24.11.2022]. https://www.clarcert.com/systeme/namse/news/start-des-neuen-zertifizierungssystem-fur-namse-typ-a-zentren-fur-seltene-erkrankungen.html
se-atlas: Kartenansicht mit Versorgungseinrichtungen. 08.09.2022].
Thiel R. # SmartHealthSystems Digitalisierungsstrategien Im Internationalen Vergleich. Bertelsmann Stiftung; 2018.
Reitzle L, et al. Perceived Access to Health Care Services and Relevance of Telemedicine during the COVID-19 pandemic in Germany. Int J Environ Res Public Health. 2021;18(14):7661.
doi: 10.3390/ijerph18147661 pubmed: 34300110 pmcid: 8303178
Pauer F, et al. [Healthcare services for people in Lower Saxony (Germany) suffering from a rare disease: findings from a survey among medical professionals]. Z Evid Fortbild Qual Gesundhwes. 2016;113:36–44.
doi: 10.1016/j.zefq.2016.05.003 pubmed: 27480187
Kripalani S, et al. Deficits in communication and information transfer between hospital-based and primary care physicians: implications for patient safety and continuity of care. JAMA. 2007;297(8):831–41.
doi: 10.1001/jama.297.8.831 pubmed: 17327525
Smits RM, et al. Common needs in uncommon conditions: a qualitative study to explore the need for care in pediatric patients with rare diseases. Orphanet J Rare Dis. 2022;17(1):153.
doi: 10.1186/s13023-022-02305-w pubmed: 35379257 pmcid: 8981675
Baumbusch J, Mayer S, Sloan-Yip I. Alone in a crowd? Parents of children with rare diseases’ experiences of navigating the Healthcare System. Journal of Genetic Counseling; 2018.
Pasquini TL, Goff SL, Whitehill JM. Navigating the US health insurance landscape for children with rare diseases: a qualitative study of parents’ experiences. Orphanet J Rare Dis. 2021;16(1):1–14.
doi: 10.1186/s13023-021-01943-w
Inhestern L, et al. Interface management concepts in healthcare for rare diseases in Germany: a study protocol for a mixed-methods study to develop best practice recommendations. BMJ Open. 2020;10(11):e040470.
doi: 10.1136/bmjopen-2020-040470 pubmed: 33257484 pmcid: 7705519
Winkler J, Stolzenberg H. Adjustierung Des Sozialen-Schicht-Index für die Anwendung Im Kinder-Und Jugendgesundheitssurvey (KiGGS). Wismarer Diskussionspapiere; 2009.
Scholl I, et al. Fragebogen Zur Zufriedenheit in Der Ambulanten versorgung–schwerpunkt patientenbeteiligung (ZAPA). Klinische Diagnostik und Evaluation. 2011;4(1):50–62.
Schmidt J, Wittman W. Fragebogen zur Messung der Patientenzufriedenheit–ZUF-8 Bengel, J., Wirtz, M. & Zwingmann,. C, Herausgeber: Diagnostische Verfahren in der Rehabilitation (S. 255–258). Göttingen, Hogrefe, 2008.
Mayring P. Qualitative content analysis: theoretical foundation, basic procedures and software solution 2014.
Simpson A, et al. How are patients with rare diseases and their carers in the UK impacted by the way care is coordinated? An exploratory qualitative interview study. Orphanet J Rare Dis. 2021;16(1):76.
doi: 10.1186/s13023-020-01664-6 pubmed: 33568181 pmcid: 7874609
Walton H, et al. Development of models of care coordination for rare conditions: a qualitative study. Orphanet J Rare Dis. 2022;17(1):49.
doi: 10.1186/s13023-022-02190-3 pubmed: 35164822 pmcid: 8843018
von der Lippe C, Diesen PS, Feragen KB. Living with a rare disorder: a systematic review of the qualitative literature. Mol Genet Genomic Med. 2017;5(6):758–73.
doi: 10.1002/mgg3.315 pubmed: 29178638 pmcid: 5702559
Garrino L, et al. Living with and treating rare diseases: experiences of patients and professional health care providers. Qual Health Res. 2015;25(5):636–51.
doi: 10.1177/1049732315570116 pubmed: 25667160
Byrne N, et al. The role of primary care in management of rare diseases in Ireland. Ir J Med Sci (1971 -). 2020;189(3):771–6.
doi: 10.1007/s11845-019-02168-4
Brandt F, Salm F. Management Komplexer Behandlungsbedarfe durch patientenlotsen–eine qualitative Studie Zur Erfassung Des Status quo in Der GKV. Gesundheitsökonomie Qualitätsmanagement. 2022;27(01):46–54.
doi: 10.1055/a-1652-9623
Kenny T, Bogart K, Freedman A, Garthwaite C, Henley SMD, Bolz-Johnson M, Mohammed S, Walton J, Winter K, Woodman D. The importance of psychological support for parents and caregivers of children with a rare disease at diagnosis. Rare Disease Orphan Drugs J. 2022;1(2):7.
doi: 10.20517/rdodj.2022.04
Ward AJ, et al. Designing rare disease care pathways in the Republic of Ireland: a cooperative model. Orphanet J Rare Dis. 2022;17(1):162.
doi: 10.1186/s13023-022-02309-6 pubmed: 35410222 pmcid: 8996209

Auteurs

Laura Inhestern (L)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany. l.inhestern@uke.de.

Ramona Otto (R)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Maja Brandt (M)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

David Zybarth (D)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Ralf Oheim (R)

Institute of Osteology and Biomechanics, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Helke Schüler (H)

Department of Cardiology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Thomas S Mir (TS)

Department of Pediatric Cardiology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Konstantinos Tsiakas (K)

University Children's Hospital, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Payam Dibaj (P)

Center for Rare Diseases Göttingen (ZSEG), Department of Pediatrics, University Medical Center Göttingen, Göttingen, Germany.

Jana Zschüntzsch (J)

Department of Neurology, University Medical Center Göttingen, Göttingen, Germany.

Pamela M Okun (PM)

Center for Rare Diseases Heidelberg, Medical Center, University of Heidelberg, Heidelberg, Germany.

Ute Hegenbart (U)

Center for Rare Diseases Heidelberg, Medical Center, University of Heidelberg, Heidelberg, Germany.
Amyloidosis Center, Heidelberg University Hospital, Heidelberg, Germany.

Olaf Sommerburg (O)

Center for Rare Diseases Heidelberg, Medical Center, University of Heidelberg, Heidelberg, Germany.
Division of Pediatric Pulmonology, Allergy, and Cystic Fibrosis Center, Department of Pediatrics III, Heidelberg University Hospital, Heidelberg, Germany.
Translational Lung Research Center Heidelberg (TLRC), German Center for Lung Research (DZL), Heidelberg, Germany.

Christoph Schramm (C)

Martin Zeitz Center for Rare Diseases, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Christina Weiler-Normann (C)

Martin Zeitz Center for Rare Diseases, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Martin Härter (M)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.

Corinna Bergelt (C)

Department of Medical Psychology, University Medical Center Hamburg-Eppendorf, Hamburg, Germany.
Department of Medical Psychology, University Medicine Greifswald, Greifswald, Germany.

Articles similaires

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C
1.00
Humans Yoga Low Back Pain Female Male

Classifications MeSH