Urticarial Vasculitis.
Anti-C1q
Autoinflammatory
Complement
IL-1
Purpura
Urticaria
Vasculitis
Wheal
Journal
Immunology and allergy clinics of North America
ISSN: 1557-8607
Titre abrégé: Immunol Allergy Clin North Am
Pays: United States
ID NLM: 8805635
Informations de publication
Date de publication:
Aug 2024
Aug 2024
Historique:
medline:
28
6
2024
pubmed:
28
6
2024
entrez:
27
6
2024
Statut:
ppublish
Résumé
Urticarial vasculitis is a rare autoimmune disorder characterized by persistent edematous papules and plaques on the skin that last longer than 24 hours, often accompanied by systemic symptoms such as joint pain and fever. Unlike common urticaria, this condition involves inflammation of small blood vessels, leading to more severe and long-lasting skin lesions with a tendency to leave a bruiselike appearance. Diagnosis is challenging and may require a skin biopsy. Associated with underlying autoimmune diseases, treatment involves managing symptoms with medications such as antihistamines and corticosteroids, addressing the immune system's dysfunction, and treating any concurrent autoimmune conditions.
Identifiants
pubmed: 38937011
pii: S0889-8561(24)00028-6
doi: 10.1016/j.iac.2024.03.006
pii:
doi:
Substances chimiques
Histamine Antagonists
0
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
483-502Informations de copyright
Copyright © 2024 Elsevier Inc. All rights reserved.
Déclaration de conflit d'intérêts
Disclosure The authors declare no competing interests.