Large ventricular myxoma causing inflow and outflow obstruction of the right ventricle; A Case Report.
Cardiothoracic
Myxoma
Palestine
Surgery
Journal
Journal of cardiothoracic surgery
ISSN: 1749-8090
Titre abrégé: J Cardiothorac Surg
Pays: England
ID NLM: 101265113
Informations de publication
Date de publication:
20 Sep 2024
20 Sep 2024
Historique:
received:
07
07
2024
accepted:
14
09
2024
medline:
21
9
2024
pubmed:
21
9
2024
entrez:
20
9
2024
Statut:
epublish
Résumé
Myxomas are the most common primary benign heart tumors, typically found in the left atrium, with only 2-4% occurring in the right ventricle. Clinical presentations vary widely, including congestive heart failure and systemic embolic phenomena. This case report describes a rare right ventricular myxoma causing both inflow and outflow obstruction, presenting as progressive exertional dyspnea. A 23-year-old male presented with two weeks of worsening exertional dyspnea. He was stable but tachypneic with a systolic murmur over the tricuspid area. Elevated erythrocyte sedimentation rate (ESR) and C-Reactive protein (CRP) were noted, while other lab tests were normal. Imaging, including echocardiography and chest tomography scan (CT) revealed a 4 × 3.8 × 4.6 cm mass in the right ventricle extending to the pulmonary trunk. Surgical resection via right ventriculotomy was performed, and histopathology confirmed myxoma. The patient recovered uneventfully. Right ventricular myxomas, though rare, can cause significant obstruction and present with diverse symptoms. Timely diagnosis using imaging techniques like echocardiography is crucial. Surgical resection remains the definitive treatment, offering excellent outcomes and low recurrence rates. Early intervention is vital to prevent serious complications and ensure favorable patient prognosis.
Sections du résumé
BACKGROUND
BACKGROUND
Myxomas are the most common primary benign heart tumors, typically found in the left atrium, with only 2-4% occurring in the right ventricle. Clinical presentations vary widely, including congestive heart failure and systemic embolic phenomena. This case report describes a rare right ventricular myxoma causing both inflow and outflow obstruction, presenting as progressive exertional dyspnea.
CASE PRESENTATION
METHODS
A 23-year-old male presented with two weeks of worsening exertional dyspnea. He was stable but tachypneic with a systolic murmur over the tricuspid area. Elevated erythrocyte sedimentation rate (ESR) and C-Reactive protein (CRP) were noted, while other lab tests were normal. Imaging, including echocardiography and chest tomography scan (CT) revealed a 4 × 3.8 × 4.6 cm mass in the right ventricle extending to the pulmonary trunk. Surgical resection via right ventriculotomy was performed, and histopathology confirmed myxoma. The patient recovered uneventfully.
CONCLUSION
CONCLUSIONS
Right ventricular myxomas, though rare, can cause significant obstruction and present with diverse symptoms. Timely diagnosis using imaging techniques like echocardiography is crucial. Surgical resection remains the definitive treatment, offering excellent outcomes and low recurrence rates. Early intervention is vital to prevent serious complications and ensure favorable patient prognosis.
Identifiants
pubmed: 39304907
doi: 10.1186/s13019-024-03056-4
pii: 10.1186/s13019-024-03056-4
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
540Informations de copyright
© 2024. The Author(s).
Références
Katiyar G, Vernekar JA, Lawande A, Caculo V. Cardiac MRI in right ventricular outflow tract myxoma: Case report with review of literature. J Cardiol Cases [Internet]. 2020;22(3):128–31. https://linkinghub.elsevier.com/retrieve/pii/S187854092030044X
D’Anna C, Villani A, Ammirati A, Francalanci P, Ragni L, Cecconi G et al. New Onset Cardiac Murmur and Exertional Dyspnea in an Apparently Healthy Child: A Rare Localization of Obstructive Myxoma in the Right Ventricle Outflow Tract without Pulmonary Embolization-A Case Report and Literature Review. Int J Environ Res Public Health [Internet]. 2022;19(19). http://www.ncbi.nlm.nih.gov/pubmed/36232202
Islam AKMM. Cardiac myxomas: A narrative review. World J Cardiol [Internet]. 2022;14(4):206–19. http://www.ncbi.nlm.nih.gov/pubmed/35582466
Lu C, Yang P, Hu J. Giant right ventricular myxoma presenting as right heart failure with systemic congestion: a rare case report. BMC Surg [Internet]. 2021;21(1):64. https://bmcsurg.biomedcentral.com/articles/ https://doi.org/10.1186/s12893-020-00977-4
Gajjar TP, Shah GB, Desai NB. Mixoma ventricular direito gigante obstruindo via de saída do ventrículo direito. REVISTA BRASILEIRA DE CIRURGIA CARDIOVASCULAR [Internet]. 2011;26(4):663–6. http://www.gnresearch.org/doi/ https://doi.org/10.5935/1678-9741.20110060