Rare locations of peripheral aneurysms in Marfan syndrome treated surgically: a case report.
Humans
Marfan Syndrome
/ complications
Female
Middle Aged
Treatment Outcome
Blood Vessel Prosthesis Implantation
/ adverse effects
Aneurysm
/ surgery
Axillary Artery
/ surgery
Subclavian Artery
/ diagnostic imaging
Heart Valve Prosthesis Implantation
/ adverse effects
Aortic Aneurysm
/ surgery
Computed Tomography Angiography
Marfan syndrome
aneurysm
axillary aneurysm
case report
peripheral
repair
surgery
Journal
BMC cardiovascular disorders
ISSN: 1471-2261
Titre abrégé: BMC Cardiovasc Disord
Pays: England
ID NLM: 100968539
Informations de publication
Date de publication:
01 Nov 2024
01 Nov 2024
Historique:
received:
11
02
2024
accepted:
24
10
2024
medline:
1
11
2024
pubmed:
1
11
2024
entrez:
1
11
2024
Statut:
epublish
Résumé
Marfan syndrome (MFS) is a connective tissue disorder that can lead to cardiovascular and musculoskeletal abnormalities. Aortic aneurysms and dissections are frequently seen in patients with MFS whereas peripheral vascular aneurysms in subclavian and axillary arteries territory considered very unusual. We reported a case of 54-year-old female with known history of MFS who had undergone a mechanical valve Bentall procedure due to severe aortic regurgitation and ascending aorta aneurysm in addition to thoracoabdominal aortic repair and who presented with a pulsatile painful mass in her right axillary region that turn to be significant true aneurysms of right subclavian and axillary arteries. To relive symptoms and to avoid further complications patient underwent successful surgical repair. Our case demonstrated rare locations of true peripheral aneurysms as a possible manifestation of MFS appeared several years post Bentall procedure and thoracoabdominal aortic repair and highlights also the importance of long-term monitoring to detect earlier such manifestation and avoid complications by surgical repair.
Identifiants
pubmed: 39482606
doi: 10.1186/s12872-024-04298-9
pii: 10.1186/s12872-024-04298-9
doi:
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
610Informations de copyright
© 2024. The Author(s).
Références
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