questionsmedicales.fr
Maladies cardiovasculaires
Maladies vasculaires
Embolie et thrombose
Thrombose
Thrombose veineuse
Syndrome de Budd-Chiari
Syndrome de Budd-Chiari : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Syndrome de Budd-Chiari
Échographie
Imagerie par résonance magnétique
Tests sanguins
Fonction hépatique
Coagulation
Ascite
Douleur abdominale
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Échographie Doppler
Flux sanguin
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Biopsie hépatique
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Symptômes
5
Douleur abdominale
Syndrome de Budd-Chiari
Hépatomégalie
Ascite
Hypertension portale
Cavité abdominale
Jaunisse
Bilirubine
Syndrome de Budd-Chiari
Asymptomatique
Syndrome de Budd-Chiari
Forme chronique
Prévention
5
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Troubles de la coagulation
Obésité
Anticoagulants
Prévention
Thromboses
Habitudes de vie
Alimentation équilibrée
Exercice
Vaccination
Hépatite
Complications hépatiques
Surveillance
Maladies hépatiques
Troubles de la coagulation
Traitements
5
Anticoagulants
Transplantation hépatique
Procédures endovasculaires
Anticoagulants
Thrombose veineuse
Complications
Procédure endovasculaire
Angioplastie
Stenting
Transplantation hépatique
Insuffisance hépatique
Complications
Traitements symptomatiques
Diurétiques
Ascite
Complications
5
Complications
Insuffisance hépatique
Hypertension portale
Insuffisance hépatique
Syndrome de Budd-Chiari
Complications
Hypertension portale
Veine porte
Obstruction
Complications à long terme
Cirrhose
Syndrome de Budd-Chiari
Prévention
Traitement précoce
Surveillance
Facteurs de risque
5
Facteurs de risque
Troubles de la coagulation
Obésité
Obésité
Syndrome de Budd-Chiari
Facteurs de risque
Maladies hépatiques
Cirrhose
Syndrome de Budd-Chiari
Contraceptifs oraux
Thrombose
Facteurs de risque
Tabagisme
Problèmes vasculaires
Thrombose
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"@type": "Question",
"name": "Quels tests sanguins sont utiles ?",
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"name": "Quels signes cliniques indiquent ce syndrome ?",
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"@type": "Question",
"name": "L'échographie Doppler est-elle utile ?",
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"name": "La douleur abdominale est-elle fréquente ?",
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"name": "Qu'est-ce que l'ascite ?",
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}
},
{
"@type": "Question",
"name": "La jaunisse est-elle un symptôme ?",
"position": 9,
"acceptedAnswer": {
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"text": "Oui, la jaunisse, due à une accumulation de bilirubine, est un symptôme courant du syndrome."
}
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{
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"name": "Peut-on avoir des symptômes asymptomatiques ?",
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"text": "Oui, certains patients peuvent être asymptomatiques, surtout dans les formes chroniques."
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"@type": "Question",
"name": "Les anticoagulants peuvent-ils prévenir ce syndrome ?",
"position": 12,
"acceptedAnswer": {
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}
},
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"name": "Quelles habitudes de vie adopter ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Adopter une alimentation équilibrée, faire de l'exercice et éviter le tabac sont bénéfiques."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, se faire vacciner contre l'hépatite peut réduire le risque de complications hépatiques."
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"name": "Faut-il surveiller les maladies hépatiques ?",
"position": 15,
"acceptedAnswer": {
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}
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"name": "Quels traitements sont disponibles ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des anticoagulants, des procédures endovasculaires et, dans certains cas, une transplantation hépatique."
}
},
{
"@type": "Question",
"name": "Quand utiliser des anticoagulants ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les anticoagulants sont utilisés pour traiter les thromboses veineuses hépatiques et prévenir les complications."
}
},
{
"@type": "Question",
"name": "Qu'est-ce qu'une procédure endovasculaire ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "C'est une intervention pour débloquer les veines hépatiques, souvent par angioplastie ou stenting."
}
},
{
"@type": "Question",
"name": "Quand envisager une transplantation hépatique ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "La transplantation est envisagée en cas d'insuffisance hépatique sévère ou de complications irréversibles."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements symptomatiques ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des traitements symptomatiques comme les diurétiques peuvent aider à gérer l'ascite."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent l'insuffisance hépatique, la thrombose et l'hypertension portale."
}
},
{
"@type": "Question",
"name": "L'insuffisance hépatique est-elle fréquente ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'insuffisance hépatique est une complication grave pouvant survenir dans ce syndrome."
}
},
{
"@type": "Question",
"name": "Qu'est-ce que l'hypertension portale ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'hypertension portale est une augmentation de la pression dans la veine porte, causée par l'obstruction."
}
},
{
"@type": "Question",
"name": "Peut-on avoir des complications à long terme ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des complications à long terme comme la cirrhose peuvent se développer si non traitées."
}
},
{
"@type": "Question",
"name": "Les complications peuvent-elles être évitées ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines complications peuvent être évitées par un traitement précoce et une surveillance régulière."
}
},
{
"@type": "Question",
"name": "Quels sont les principaux facteurs de risque ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent les troubles de la coagulation, l'obésité, et certaines maladies hépatiques."
}
},
{
"@type": "Question",
"name": "L'obésité augmente-t-elle le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'obésité est un facteur de risque connu pour le syndrome de Budd-Chiari."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines maladies hépatiques, comme la cirrhose, augmentent le risque de ce syndrome."
}
},
{
"@type": "Question",
"name": "Les contraceptifs oraux sont-ils un facteur ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'utilisation prolongée de contraceptifs oraux peut augmenter le risque de thrombose."
}
},
{
"@type": "Question",
"name": "Le tabagisme influence-t-il le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le tabagisme peut contribuer à des problèmes vasculaires, augmentant le risque de thrombose."
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Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 06/04/2025
Contenu vérifié selon les dernières recommandations médicales
4 publications dans cette catégorie
Affiliations :
Department of Gastroenterology, All India Institute of Medical Sciences, New Delhi, India.
Publications dans "Syndrome de Budd-Chiari" :
4 publications dans cette catégorie
Affiliations :
Department of Gastroenterology, Seth Gordhandas Sunderdas Medical College and King Edward Memorial Hospital, Mumbai, 400012, India.
Publications dans "Syndrome de Budd-Chiari" :
3 publications dans cette catégorie
Affiliations :
Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA.
Publications dans "Syndrome de Budd-Chiari" :
3 publications dans cette catégorie
Affiliations :
Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA.
Publications dans "Syndrome de Budd-Chiari" :
3 publications dans cette catégorie
Affiliations :
Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA.
Department of Medicine, University of Maryland School of Medicine, Baltimore, MD, USA.
Publications dans "Syndrome de Budd-Chiari" :
3 publications dans cette catégorie
Affiliations :
Department of Radiodiagnosis, All India Institute of Medical Sciences, New Delhi, India.
Publications dans "Syndrome de Budd-Chiari" :
3 publications dans cette catégorie
Affiliations :
Department of Gastroenterology and Human Nutrition Unit, All India Institute of Medical Sciences, New Delhi, 110 029, India.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Interventional Radiology, The Affiliated Hospital of XuZhou Medical University, Province Jiangsu, PR China.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Queen Elizabeth Hospital Birmingham, Birmingham, United Kingdom.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Queen Elizabeth Hospital Birmingham, Birmingham, United Kingdom.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Queen Elizabeth Hospital Birmingham, Birmingham, United Kingdom.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
College of Medicine and Biological Information Engineering, Northeastern University, Shenyang, China.
Liver Cirrhosis Study Group, Department of Gastroenterology, General Hospital of Northern Theater Command, Shenyang, China.
Department of Life Sciences and Biopharmaceutis, Shenyang Pharmaceutical University, Shenyang, China.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Radiology, Seth Gordhandas Sunderdas Medical College and King Edward Memorial Hospital, Mumbai, 400012, India.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Gastroenterology and Human Nutrition Unit, All India Institute of Medical Sciences, New Delhi, 110 029, India.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Gastroenterology, All India Institute of Medical Sciences, Patna 801507, India.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Gastroenterology and Human Nutrition, All India Institute of Medical Sciences, New Delhi 110029, Delhi, India.
Publications dans "Syndrome de Budd-Chiari" :
2 publications dans cette catégorie
Affiliations :
Department of Gastroenterology, Seth G S Medical College and KEM Hospital, Parel, Mumbai, 400012, India.
Publications dans "Syndrome de Budd-Chiari" :
1 publication dans cette catégorie
Affiliations :
Department of Interventional Radiology, The Affiliated Hospital of XuZhou Medical University, Province Jiangsu, PR China.
Publications dans "Syndrome de Budd-Chiari" :
1 publication dans cette catégorie
Affiliations :
Department of Interventional Radiology, The Affiliated Hospital of XuZhou Medical University, Province Jiangsu, PR China.
Publications dans "Syndrome de Budd-Chiari" :
1 publication dans cette catégorie
Affiliations :
Department of Interventional Radiology, The Affiliated Hospital of XuZhou Medical University, Province Jiangsu, PR China.
Publications dans "Syndrome de Budd-Chiari" :
Congenital fibrinogen deficiencies (CFD) are a group of rare bleeding disorders (RBD). Afibrinogenemia as a subclass of these disorders would occurs as a result of mutations in fibrinogen gene. Here i...
The FGA gene exons were amplified using PCR method and the DNA sequences were analysed to study the mutations in Aα chain of Fibrinogen....
Results showed that there was no large deletion in FGA gene. Although a frame shift mutation: c.196_197insT p.Ser66PhefsX10 in a patient and a novel mutation of IVS2-1G>A in two other patients were de...
Different mutations are responsible of afibrinogenemia deficiency which requires more relevant studies for confirmation. The type and distribution of mutations in fibrinogen gene in Iranian patients i...
Congenital afibrinogenemia treatment with plasma-derived fibrinogen concentrates in pediatric patients is limited. This study investigated the pharmacokinetics, surrogate efficacy, and safety of a pla...
Patients aged <18 years old diagnosed with congenital afibrinogenemia were included in this prospective, multinational, phase 1-2, single-arm study. After a single dose of a plasma-derived fibrinogen ...
Eleven patients with a median (range) age 8.80 (3.7-12.7) years were treated with the plasma-derived fibrinogen concentrate. Using the popPK modeling, fibrinogen activity reached a mean (standard devi...
In pediatric patients with congenital afibrinogenemia, plasma-derived fibrinogen concentrate revealed a favorable and specific pharmacokinetic profile, demonstrated efficacy in coagulation and was saf...
Afibrinogenemia is a coagulation disorder that occurs with a frequency of 1-2 cases/1,000,000 population and is characterized by a lack of capacity to synthesize fibrinogen. The predominant symptoms r...
Congenital afibrinogenemia is a rare inherited blood disorder characterized by a deficiency of fibrinogen, leading to abnormal blood clotting. It is caused by mutations in fibrinogen genes and results...
Fibrinogen deficiencies in neonates can lead to bleeding complications. In this report, we describe a case of congenital afibrinogenemia in a newborn with critical pulmonary stenosis who presented wit...
This is a case of congenital afibrinogenemia with multiple thrombotic and hemorrhagic events. His fibrinogen concentration was negatively correlated with thrombin time and prothrombin time and abnorma...
[This corrects the article DOI: 10.1002/ccr3.6395.]....
We present a case of bleeding from circumcision in a full-term newborn male resulting from a rare coagulopathy, congenital afibrinogenemia, and a review of the literature regarding the management of b...
Afibrinogenemia is an extremely rare bleeding disorder characterized by the absence or severe deficiency of fibrinogen, a major protein involved in the regulation of blood clotting. This disorder can ...
In clinical practice, the incidence of hypofibrinogenemia (HF) after tigecycline (TGC) treatment significantly exceeds the probability claimed by drug manufacturers....
We aimed to identify the risk factors for TGC-associated HF and develop prediction and survival models for TGC-associated HF and the timing of TGC-associated HF....
This single-center retrospective cohort study included 222 patients who were prescribed TGC. First, we used binary logistic regression to screen the independent factors influencing TGC-associated HF, ...
Binary logistic regression identified nine independent factors influencing TGC-associated HF, and the XGBoost model was constructed using these nine predictors. The ROC and calibration curves showed t...
The XGBoost model effectively predicts the risk of TGC-associated HF, whereas the RSF model has advantages in risk stratification. These two models have significant clinical practical value, with the ...