questionsmedicales.fr
Maladies cardiovasculaires
Maladies vasculaires
Embolie et thrombose
Thrombose
Thrombose veineuse
Syndrome de Budd-Chiari
Syndrome de Budd-Chiari : Questions médicales fréquentes
Termes MeSH sélectionnés :
{
"@context": "https://schema.org",
"@graph": [
{
"@type": "MedicalWebPage",
"name": "Syndrome de Budd-Chiari : Questions médicales les plus fréquentes",
"headline": "Syndrome de Budd-Chiari : Comprendre les symptômes, diagnostics et traitements",
"description": "Guide complet et accessible sur les Syndrome de Budd-Chiari : explications, diagnostics, traitements et prévention. Information médicale validée destinée aux patients.",
"datePublished": "2024-04-11",
"dateModified": "2025-04-06",
"inLanguage": "fr",
"medicalAudience": [
{
"@type": "MedicalAudience",
"name": "Grand public",
"audienceType": "Patient",
"healthCondition": {
"@type": "MedicalCondition",
"name": "Syndrome de Budd-Chiari"
},
"suggestedMinAge": 18,
"suggestedGender": "unisex"
},
{
"@type": "MedicalAudience",
"name": "Médecins",
"audienceType": "Physician",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "France"
}
},
{
"@type": "MedicalAudience",
"name": "Chercheurs",
"audienceType": "Researcher",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "International"
}
}
],
"reviewedBy": {
"@type": "Person",
"name": "Dr Olivier Menir",
"jobTitle": "Expert en Médecine",
"description": "Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale",
"url": "/static/pages/docteur-olivier-menir.html",
"alumniOf": {
"@type": "EducationalOrganization",
"name": "Université Paris Descartes"
}
},
"isPartOf": {
"@type": "MedicalWebPage",
"name": "Thrombose veineuse",
"url": "https://questionsmedicales.fr/mesh/D020246",
"about": {
"@type": "MedicalCondition",
"name": "Thrombose veineuse",
"code": {
"@type": "MedicalCode",
"code": "D020246",
"codingSystem": "MeSH"
},
"identifier": {
"@type": "PropertyValue",
"propertyID": "MeSH Tree",
"value": "C14.907.355.830.925"
}
}
},
"about": {
"@type": "MedicalCondition",
"name": "Syndrome de Budd-Chiari",
"alternateName": "Budd-Chiari Syndrome",
"code": {
"@type": "MedicalCode",
"code": "D006502",
"codingSystem": "MeSH"
}
},
"author": [
{
"@type": "Person",
"name": "None Shalimar",
"url": "https://questionsmedicales.fr/author/None%20Shalimar",
"affiliation": {
"@type": "Organization",
"name": "Department of Gastroenterology, All India Institute of Medical Sciences, New Delhi, India."
}
},
{
"@type": "Person",
"name": "Akash Shukla",
"url": "https://questionsmedicales.fr/author/Akash%20Shukla",
"affiliation": {
"@type": "Organization",
"name": "Department of Gastroenterology, Seth Gordhandas Sunderdas Medical College and King Edward Memorial Hospital, Mumbai, 400012, India."
}
},
{
"@type": "Person",
"name": "Joseph J Alukal",
"url": "https://questionsmedicales.fr/author/Joseph%20J%20Alukal",
"affiliation": {
"@type": "Organization",
"name": "Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA."
}
},
{
"@type": "Person",
"name": "Talan Zhang",
"url": "https://questionsmedicales.fr/author/Talan%20Zhang",
"affiliation": {
"@type": "Organization",
"name": "Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA."
}
},
{
"@type": "Person",
"name": "Paul J Thuluvath",
"url": "https://questionsmedicales.fr/author/Paul%20J%20Thuluvath",
"affiliation": {
"@type": "Organization",
"name": "Institute of Digestive Health & Liver Diseases, Mercy Medical Center, Baltimore, MD, USA."
}
}
],
"citation": [
{
"@type": "ScholarlyArticle",
"name": "Ceramide-rich microdomains facilitate nuclear envelope budding for non-conventional exosome formation.",
"datePublished": "2022-06-23",
"url": "https://questionsmedicales.fr/article/35739317",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1038/s41556-022-00934-8"
}
},
{
"@type": "ScholarlyArticle",
"name": "A novel role for CSA in the regulation of nuclear envelope integrity: uncovering a non-canonical function.",
"datePublished": "2024-08-29",
"url": "https://questionsmedicales.fr/article/39209536",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.26508/lsa.202402745"
}
},
{
"@type": "ScholarlyArticle",
"name": "Nuclear envelope-remodeling events as models to assess the potential role of membranes on genome stability.",
"datePublished": "2023-06-26",
"url": "https://questionsmedicales.fr/article/37339935",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1002/1873-3468.14688"
}
},
{
"@type": "ScholarlyArticle",
"name": "Rapid meiotic prophase chromosome movements in Arabidopsis thaliana are linked to essential reorganization at the nuclear envelope.",
"datePublished": "2024-07-16",
"url": "https://questionsmedicales.fr/article/39013853",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1038/s41467-024-50169-4"
}
},
{
"@type": "ScholarlyArticle",
"name": "DNA damage induces nuclear envelope rupture through ATR-mediated phosphorylation of lamin A/C.",
"datePublished": "2023-10-12",
"url": "https://questionsmedicales.fr/article/37832547",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1016/j.molcel.2023.09.023"
}
}
],
"breadcrumb": {
"@type": "BreadcrumbList",
"itemListElement": [
{
"@type": "ListItem",
"position": 1,
"name": "questionsmedicales.fr",
"item": "https://questionsmedicales.fr"
},
{
"@type": "ListItem",
"position": 2,
"name": "Maladies cardiovasculaires",
"item": "https://questionsmedicales.fr/mesh/D002318"
},
{
"@type": "ListItem",
"position": 3,
"name": "Maladies vasculaires",
"item": "https://questionsmedicales.fr/mesh/D014652"
},
{
"@type": "ListItem",
"position": 4,
"name": "Embolie et thrombose",
"item": "https://questionsmedicales.fr/mesh/D016769"
},
{
"@type": "ListItem",
"position": 5,
"name": "Thrombose",
"item": "https://questionsmedicales.fr/mesh/D013927"
},
{
"@type": "ListItem",
"position": 6,
"name": "Thrombose veineuse",
"item": "https://questionsmedicales.fr/mesh/D020246"
},
{
"@type": "ListItem",
"position": 7,
"name": "Syndrome de Budd-Chiari",
"item": "https://questionsmedicales.fr/mesh/D006502"
}
]
}
},
{
"@type": "MedicalWebPage",
"name": "Article complet : Syndrome de Budd-Chiari - Questions et réponses",
"headline": "Questions et réponses médicales fréquentes sur Syndrome de Budd-Chiari",
"description": "Une compilation de questions et réponses structurées, validées par des experts médicaux.",
"datePublished": "2025-05-07",
"inLanguage": "fr",
"hasPart": [
{
"@type": "MedicalWebPage",
"name": "Diagnostic",
"headline": "Diagnostic sur Syndrome de Budd-Chiari",
"description": "Comment diagnostiquer le syndrome de Budd-Chiari ?\nQuels tests sanguins sont utiles ?\nQuels signes cliniques indiquent ce syndrome ?\nL'échographie Doppler est-elle utile ?\nQuand envisager une biopsie hépatique ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-diagnostic"
},
{
"@type": "MedicalWebPage",
"name": "Symptômes",
"headline": "Symptômes sur Syndrome de Budd-Chiari",
"description": "Quels sont les symptômes courants ?\nLa douleur abdominale est-elle fréquente ?\nQu'est-ce que l'ascite ?\nLa jaunisse est-elle un symptôme ?\nPeut-on avoir des symptômes asymptomatiques ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-symptômes"
},
{
"@type": "MedicalWebPage",
"name": "Prévention",
"headline": "Prévention sur Syndrome de Budd-Chiari",
"description": "Comment prévenir le syndrome de Budd-Chiari ?\nLes anticoagulants peuvent-ils prévenir ce syndrome ?\nQuelles habitudes de vie adopter ?\nLes vaccinations sont-elles importantes ?\nFaut-il surveiller les maladies hépatiques ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-prévention"
},
{
"@type": "MedicalWebPage",
"name": "Traitements",
"headline": "Traitements sur Syndrome de Budd-Chiari",
"description": "Quels traitements sont disponibles ?\nQuand utiliser des anticoagulants ?\nQu'est-ce qu'une procédure endovasculaire ?\nQuand envisager une transplantation hépatique ?\nY a-t-il des traitements symptomatiques ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-traitements"
},
{
"@type": "MedicalWebPage",
"name": "Complications",
"headline": "Complications sur Syndrome de Budd-Chiari",
"description": "Quelles sont les complications possibles ?\nL'insuffisance hépatique est-elle fréquente ?\nQu'est-ce que l'hypertension portale ?\nPeut-on avoir des complications à long terme ?\nLes complications peuvent-elles être évitées ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-complications"
},
{
"@type": "MedicalWebPage",
"name": "Facteurs de risque",
"headline": "Facteurs de risque sur Syndrome de Budd-Chiari",
"description": "Quels sont les principaux facteurs de risque ?\nL'obésité augmente-t-elle le risque ?\nLes maladies hépatiques sont-elles un risque ?\nLes contraceptifs oraux sont-ils un facteur ?\nLe tabagisme influence-t-il le risque ?",
"url": "https://questionsmedicales.fr/mesh/D006502?mesh_terms=Nuclear+Envelope&page=4#section-facteurs de risque"
}
]
},
{
"@type": "FAQPage",
"mainEntity": [
{
"@type": "Question",
"name": "Comment diagnostiquer le syndrome de Budd-Chiari ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le diagnostic repose sur l'échographie, l'IRM et des tests sanguins pour évaluer la fonction hépatique."
}
},
{
"@type": "Question",
"name": "Quels tests sanguins sont utiles ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests incluent les marqueurs de la fonction hépatique et les tests de coagulation."
}
},
{
"@type": "Question",
"name": "Quels signes cliniques indiquent ce syndrome ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les signes incluent l'ascite, la douleur abdominale et l'hypertrophie du foie."
}
},
{
"@type": "Question",
"name": "L'échographie Doppler est-elle utile ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elle permet d'évaluer le flux sanguin dans les veines hépatiques et de détecter des obstructions."
}
},
{
"@type": "Question",
"name": "Quand envisager une biopsie hépatique ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une biopsie peut être envisagée si le diagnostic est incertain ou pour évaluer des lésions hépatiques."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes courants ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent fatigue, douleur abdominale, jaunisse et ascite."
}
},
{
"@type": "Question",
"name": "La douleur abdominale est-elle fréquente ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la douleur abdominale est un symptôme fréquent, souvent localisée dans la partie supérieure droite."
}
},
{
"@type": "Question",
"name": "Qu'est-ce que l'ascite ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'ascite est l'accumulation de liquide dans la cavité abdominale, souvent causée par une hypertension portale."
}
},
{
"@type": "Question",
"name": "La jaunisse est-elle un symptôme ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la jaunisse, due à une accumulation de bilirubine, est un symptôme courant du syndrome."
}
},
{
"@type": "Question",
"name": "Peut-on avoir des symptômes asymptomatiques ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains patients peuvent être asymptomatiques, surtout dans les formes chroniques."
}
},
{
"@type": "Question",
"name": "Comment prévenir le syndrome de Budd-Chiari ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "La prévention inclut la gestion des facteurs de risque comme les troubles de la coagulation et l'obésité."
}
},
{
"@type": "Question",
"name": "Les anticoagulants peuvent-ils prévenir ce syndrome ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les anticoagulants peuvent prévenir les thromboses chez les patients à risque."
}
},
{
"@type": "Question",
"name": "Quelles habitudes de vie adopter ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Adopter une alimentation équilibrée, faire de l'exercice et éviter le tabac sont bénéfiques."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, se faire vacciner contre l'hépatite peut réduire le risque de complications hépatiques."
}
},
{
"@type": "Question",
"name": "Faut-il surveiller les maladies hépatiques ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, surveiller les maladies hépatiques et les troubles de la coagulation est crucial pour la prévention."
}
},
{
"@type": "Question",
"name": "Quels traitements sont disponibles ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des anticoagulants, des procédures endovasculaires et, dans certains cas, une transplantation hépatique."
}
},
{
"@type": "Question",
"name": "Quand utiliser des anticoagulants ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les anticoagulants sont utilisés pour traiter les thromboses veineuses hépatiques et prévenir les complications."
}
},
{
"@type": "Question",
"name": "Qu'est-ce qu'une procédure endovasculaire ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "C'est une intervention pour débloquer les veines hépatiques, souvent par angioplastie ou stenting."
}
},
{
"@type": "Question",
"name": "Quand envisager une transplantation hépatique ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "La transplantation est envisagée en cas d'insuffisance hépatique sévère ou de complications irréversibles."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements symptomatiques ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des traitements symptomatiques comme les diurétiques peuvent aider à gérer l'ascite."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent l'insuffisance hépatique, la thrombose et l'hypertension portale."
}
},
{
"@type": "Question",
"name": "L'insuffisance hépatique est-elle fréquente ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'insuffisance hépatique est une complication grave pouvant survenir dans ce syndrome."
}
},
{
"@type": "Question",
"name": "Qu'est-ce que l'hypertension portale ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'hypertension portale est une augmentation de la pression dans la veine porte, causée par l'obstruction."
}
},
{
"@type": "Question",
"name": "Peut-on avoir des complications à long terme ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des complications à long terme comme la cirrhose peuvent se développer si non traitées."
}
},
{
"@type": "Question",
"name": "Les complications peuvent-elles être évitées ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines complications peuvent être évitées par un traitement précoce et une surveillance régulière."
}
},
{
"@type": "Question",
"name": "Quels sont les principaux facteurs de risque ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent les troubles de la coagulation, l'obésité, et certaines maladies hépatiques."
}
},
{
"@type": "Question",
"name": "L'obésité augmente-t-elle le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'obésité est un facteur de risque connu pour le syndrome de Budd-Chiari."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines maladies hépatiques, comme la cirrhose, augmentent le risque de ce syndrome."
}
},
{
"@type": "Question",
"name": "Les contraceptifs oraux sont-ils un facteur ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'utilisation prolongée de contraceptifs oraux peut augmenter le risque de thrombose."
}
},
{
"@type": "Question",
"name": "Le tabagisme influence-t-il le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le tabagisme peut contribuer à des problèmes vasculaires, augmentant le risque de thrombose."
}
}
]
}
]
}
Neutrophils migrating towards chemoattractant gradients amplify their recruitment range by releasing the secondary chemoattractant leukotriene B...
Cockayne syndrome (CS) is a premature ageing condition characterized by microcephaly, growth failure, and neurodegeneration. It is caused by mutations in...
The nuclear envelope (NE) encloses the genetic material and functions in chromatin organization and stability. In Saccharomyces cerevisiae, the NE is bound to the ribosomal DNA (rDNA), highly repeated...
Meiotic rapid prophase chromosome movements (RPMs) require connections between the chromosomes and the cytoskeleton, involving SUN (Sad1/UNC-84)-domain-containing proteins at the inner nuclear envelop...
The integrity of the nuclear envelope (NE) is essential for maintaining the structural stability of the nucleus. Rupture of the NE has been frequently observed in cancer cells, especially in the conte...
DYT1 dystonia is a debilitating neurological movement disorder arising from mutation in the AAA+ ATPase TorsinA. The hallmark of Torsin dysfunction is nuclear envelope blebbing resulting from defects ...
Classically associated with gap junction-mediated intercellular communication, connexin43 (Cx43) is increasingly recognized to possess non-canonical biological functions, including gene expression reg...
Cell motility is related to the higher-order structure of chromatin. Stimuli that induce cell migration change chromatin organization; such stimuli include elevated histone H3 lysine 9 trimethylation ...
Maintaining the integrity of the nuclear envelope (NE) is essential for preventing genomic DNA damage. Recent studies have shown that enzymes that catalyze lipid synthesis are involved in NE maintenan...
Double-strand breaks (DSBs) due to genotoxic stress represent potential threats to genome stability. Dysfunctional telomeres are recognized as DSBs and are repaired by distinct DNA repair mechanisms. ...