questionsmedicales.fr
Maladies cardiovasculaires
Maladies vasculaires
Maladie veino-occlusive pulmonaire
Maladie veino-occlusive pulmonaire : Questions médicales fréquentes
{
"@context": "https://schema.org",
"@graph": [
{
"@type": "MedicalWebPage",
"name": "Maladie veino-occlusive pulmonaire : Questions médicales les plus fréquentes",
"headline": "Maladie veino-occlusive pulmonaire : Comprendre les symptômes, diagnostics et traitements",
"description": "Guide complet et accessible sur les Maladie veino-occlusive pulmonaire : explications, diagnostics, traitements et prévention. Information médicale validée destinée aux patients.",
"datePublished": "2024-01-29",
"dateModified": "2026-04-18",
"inLanguage": "fr",
"medicalAudience": [
{
"@type": "MedicalAudience",
"name": "Grand public",
"audienceType": "Patient",
"healthCondition": {
"@type": "MedicalCondition",
"name": "Maladie veino-occlusive pulmonaire"
},
"suggestedMinAge": 18,
"suggestedGender": "unisex"
},
{
"@type": "MedicalAudience",
"name": "Médecins",
"audienceType": "Physician",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "France"
}
},
{
"@type": "MedicalAudience",
"name": "Chercheurs",
"audienceType": "Researcher",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "International"
}
}
],
"reviewedBy": {
"@type": "Person",
"name": "Dr Olivier Menir",
"jobTitle": "Expert en Médecine",
"description": "Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale",
"url": "/static/pages/docteur-olivier-menir.html",
"alumniOf": {
"@type": "EducationalOrganization",
"name": "Université Paris Descartes"
}
},
"isPartOf": {
"@type": "MedicalWebPage",
"name": "Maladies vasculaires",
"url": "https://questionsmedicales.fr/mesh/D014652",
"about": {
"@type": "MedicalCondition",
"name": "Maladies vasculaires",
"code": {
"@type": "MedicalCode",
"code": "D014652",
"codingSystem": "MeSH"
},
"identifier": {
"@type": "PropertyValue",
"propertyID": "MeSH Tree",
"value": "C14.907"
}
}
},
"about": {
"@type": "MedicalCondition",
"name": "Maladie veino-occlusive pulmonaire",
"alternateName": "Pulmonary Veno-Occlusive Disease",
"code": {
"@type": "MedicalCode",
"code": "D011668",
"codingSystem": "MeSH"
}
},
"author": [
{
"@type": "Person",
"name": "Marc Humbert",
"url": "https://questionsmedicales.fr/author/Marc%20Humbert",
"affiliation": {
"@type": "Organization",
"name": "School of Medicine Université Paris-Saclay Le Kremlin-Bicêtre France."
}
},
{
"@type": "Person",
"name": "David Montani",
"url": "https://questionsmedicales.fr/author/David%20Montani",
"affiliation": {
"@type": "Organization",
"name": "Université Paris-Saclay-Faculté de Médecine, Le Kremlin-Bicêtre, France."
}
},
{
"@type": "Person",
"name": "Peter Dorfmüller",
"url": "https://questionsmedicales.fr/author/Peter%20Dorfm%C3%BCller",
"affiliation": {
"@type": "Organization",
"name": "Université Paris-Saclay-Faculté de Médecine, Le Kremlin-Bicêtre, France."
}
},
{
"@type": "Person",
"name": "Frédéric Perros",
"url": "https://questionsmedicales.fr/author/Fr%C3%A9d%C3%A9ric%20Perros",
"affiliation": {
"@type": "Organization",
"name": "Université Paris-Saclay-Faculté de Médecine, Le Kremlin-Bicêtre, France."
}
},
{
"@type": "Person",
"name": "Olivier Sitbon",
"url": "https://questionsmedicales.fr/author/Olivier%20Sitbon",
"affiliation": {
"@type": "Organization",
"name": "Université Paris-Saclay, Faculté de Médecine, Le Kremlin-Bicêtre, France."
}
}
],
"citation": [
{
"@type": "ScholarlyArticle",
"name": "Utility of the refined EBMT diagnostic and severity criteria 2023 for sinusoidal obstruction syndrome/veno-occlusive disease.",
"datePublished": "2024-01-29",
"url": "https://questionsmedicales.fr/article/38287083",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1038/s41409-024-02215-4"
}
},
{
"@type": "ScholarlyArticle",
"name": "Uncovering Deletion/Insertion Mutations in Veno-Occlusive Disease with Immunodeficiency Syndrome in An Iranian Family: A Case Report.",
"datePublished": "2024-10-07",
"url": "https://questionsmedicales.fr/article/39380482",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.22074/cellj.2024.2023359.1514"
}
},
{
"@type": "ScholarlyArticle",
"name": "Early defibrotide therapy and risk factors for post-transplant veno-occlusive disease/sinusoidal obstruction syndrome in childhood.",
"datePublished": "2024-09-17",
"url": "https://questionsmedicales.fr/article/39289887",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1002/pbc.31331"
}
},
{
"@type": "ScholarlyArticle",
"name": "Veno-venous or veno-arterial extracorporeal membrane oxygenation support for massive pulmonary embolism: a case report.",
"datePublished": "2024-07-08",
"url": "https://questionsmedicales.fr/article/39091562",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.21037/acr-23-128"
}
},
{
"@type": "ScholarlyArticle",
"name": "Early-onset hepatic veno-occlusive disease after liver transplantation: an institutional experience and analysis of a literature-based cohort.",
"datePublished": "2023-12-06",
"url": "https://questionsmedicales.fr/article/38055106",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1007/s00595-023-02770-1"
}
}
],
"breadcrumb": {
"@type": "BreadcrumbList",
"itemListElement": [
{
"@type": "ListItem",
"position": 1,
"name": "questionsmedicales.fr",
"item": "https://questionsmedicales.fr"
},
{
"@type": "ListItem",
"position": 2,
"name": "Maladies cardiovasculaires",
"item": "https://questionsmedicales.fr/mesh/D002318"
},
{
"@type": "ListItem",
"position": 3,
"name": "Maladies vasculaires",
"item": "https://questionsmedicales.fr/mesh/D014652"
},
{
"@type": "ListItem",
"position": 4,
"name": "Maladie veino-occlusive pulmonaire",
"item": "https://questionsmedicales.fr/mesh/D011668"
}
]
}
},
{
"@type": "MedicalWebPage",
"name": "Article complet : Maladie veino-occlusive pulmonaire - Questions et réponses",
"headline": "Questions et réponses médicales fréquentes sur Maladie veino-occlusive pulmonaire",
"description": "Une compilation de questions et réponses structurées, validées par des experts médicaux.",
"datePublished": "2026-04-29",
"inLanguage": "fr",
"hasPart": [
{
"@type": "MedicalWebPage",
"name": "Diagnostic",
"headline": "Diagnostic sur Maladie veino-occlusive pulmonaire",
"description": "Comment diagnostique-t-on la maladie veino-occlusive pulmonaire ?\nQuels tests sont utilisés pour évaluer la fonction pulmonaire ?\nLes biopsies sont-elles nécessaires pour le diagnostic ?\nQuels signes radiologiques indiquent cette maladie ?\nLe cathétérisme cardiaque est-il utile ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-diagnostic"
},
{
"@type": "MedicalWebPage",
"name": "Symptômes",
"headline": "Symptômes sur Maladie veino-occlusive pulmonaire",
"description": "Quels sont les symptômes courants de cette maladie ?\nLa maladie provoque-t-elle des douleurs thoraciques ?\nLes symptômes s'aggravent-ils avec le temps ?\nY a-t-il des symptômes spécifiques à surveiller ?\nLes symptômes peuvent-ils être confondus avec d'autres maladies ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-symptômes"
},
{
"@type": "MedicalWebPage",
"name": "Prévention",
"headline": "Prévention sur Maladie veino-occlusive pulmonaire",
"description": "Peut-on prévenir la maladie veino-occlusive pulmonaire ?\nComment réduire le risque de complications ?\nLes vaccinations sont-elles importantes ?\nLe suivi médical régulier est-il nécessaire ?\nL'éducation des patients est-elle cruciale ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-prévention"
},
{
"@type": "MedicalWebPage",
"name": "Traitements",
"headline": "Traitements sur Maladie veino-occlusive pulmonaire",
"description": "Quels traitements sont disponibles pour cette maladie ?\nLes anticoagulants sont-ils utilisés ?\nLa thérapie par oxygène est-elle recommandée ?\nY a-t-il des traitements expérimentaux ?\nLa réhabilitation pulmonaire est-elle bénéfique ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-traitements"
},
{
"@type": "MedicalWebPage",
"name": "Complications",
"headline": "Complications sur Maladie veino-occlusive pulmonaire",
"description": "Quelles complications peuvent survenir ?\nL'insuffisance cardiaque est-elle une conséquence possible ?\nLes embolies pulmonaires sont-elles fréquentes ?\nComment les complications affectent-elles la qualité de vie ?\nLes complications peuvent-elles être évitées ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-complications"
},
{
"@type": "MedicalWebPage",
"name": "Facteurs de risque",
"headline": "Facteurs de risque sur Maladie veino-occlusive pulmonaire",
"description": "Quels sont les principaux facteurs de risque ?\nLe tabagisme influence-t-il le risque ?\nLes maladies héréditaires jouent-elles un rôle ?\nL'exposition à des produits chimiques est-elle un risque ?\nL'âge est-il un facteur de risque ?",
"url": "https://questionsmedicales.fr/mesh/D011668?page=3#section-facteurs de risque"
}
]
},
{
"@type": "FAQPage",
"mainEntity": [
{
"@type": "Question",
"name": "Comment diagnostique-t-on la maladie veino-occlusive pulmonaire ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le diagnostic repose sur l'imagerie, comme l'IRM pulmonaire, et des tests fonctionnels respiratoires."
}
},
{
"@type": "Question",
"name": "Quels tests sont utilisés pour évaluer la fonction pulmonaire ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests incluent la spirométrie et les gaz du sang pour mesurer l'oxygénation."
}
},
{
"@type": "Question",
"name": "Les biopsies sont-elles nécessaires pour le diagnostic ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une biopsie pulmonaire peut être réalisée pour confirmer le diagnostic dans certains cas."
}
},
{
"@type": "Question",
"name": "Quels signes radiologiques indiquent cette maladie ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des opacités en verre dépoli et des anomalies vasculaires peuvent être observées sur les images."
}
},
{
"@type": "Question",
"name": "Le cathétérisme cardiaque est-il utile ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, il permet de mesurer la pression dans les artères pulmonaires et d'évaluer l'hypertension."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes courants de cette maladie ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent essoufflement, fatigue, douleurs thoraciques et toux persistante."
}
},
{
"@type": "Question",
"name": "La maladie provoque-t-elle des douleurs thoraciques ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des douleurs thoraciques peuvent survenir, souvent liées à l'effort ou à la respiration."
}
},
{
"@type": "Question",
"name": "Les symptômes s'aggravent-ils avec le temps ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les symptômes peuvent s'aggraver progressivement, rendant les activités quotidiennes difficiles."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes spécifiques à surveiller ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Surveillez l'apparition d'un œdème des membres inférieurs et d'une cyanose des lèvres."
}
},
{
"@type": "Question",
"name": "Les symptômes peuvent-ils être confondus avec d'autres maladies ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent être similaires à ceux de l'hypertension pulmonaire ou de l'embolie pulmonaire."
}
},
{
"@type": "Question",
"name": "Peut-on prévenir la maladie veino-occlusive pulmonaire ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de méthode de prévention spécifique, mais éviter les facteurs de risque peut aider."
}
},
{
"@type": "Question",
"name": "Comment réduire le risque de complications ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Maintenir un mode de vie sain, éviter le tabac et gérer les maladies sous-jacentes sont essentiels."
}
},
{
"@type": "Question",
"name": "Les vaccinations sont-elles importantes ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, se faire vacciner contre la grippe et le pneumocoque peut réduire les risques d'infections respiratoires."
}
},
{
"@type": "Question",
"name": "Le suivi médical régulier est-il nécessaire ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier permet de surveiller l'évolution de la maladie et d'ajuster le traitement."
}
},
{
"@type": "Question",
"name": "L'éducation des patients est-elle cruciale ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, informer les patients sur leur maladie et les traitements disponibles est essentiel pour la gestion."
}
},
{
"@type": "Question",
"name": "Quels traitements sont disponibles pour cette maladie ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des médicaments vasodilatateurs et, dans certains cas, une transplantation pulmonaire."
}
},
{
"@type": "Question",
"name": "Les anticoagulants sont-ils utilisés ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les anticoagulants peuvent être prescrits pour prévenir la formation de caillots sanguins."
}
},
{
"@type": "Question",
"name": "La thérapie par oxygène est-elle recommandée ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'oxygénothérapie peut aider à améliorer l'oxygénation chez les patients souffrant d'hypoxie."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements expérimentaux ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des essais cliniques évaluent de nouveaux médicaments et thérapies pour la maladie veino-occlusive."
}
},
{
"@type": "Question",
"name": "La réhabilitation pulmonaire est-elle bénéfique ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la réhabilitation pulmonaire peut améliorer la qualité de vie et la capacité d'exercice."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent l'hypertension pulmonaire sévère, l'insuffisance cardiaque et les embolies."
}
},
{
"@type": "Question",
"name": "L'insuffisance cardiaque est-elle une conséquence possible ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'insuffisance cardiaque peut se développer en raison de la pression accrue sur le cœur."
}
},
{
"@type": "Question",
"name": "Les embolies pulmonaires sont-elles fréquentes ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les embolies pulmonaires peuvent survenir, surtout si la circulation sanguine est altérée."
}
},
{
"@type": "Question",
"name": "Comment les complications affectent-elles la qualité de vie ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications peuvent gravement affecter la qualité de vie, limitant les activités quotidiennes."
}
},
{
"@type": "Question",
"name": "Les complications peuvent-elles être évitées ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines complications peuvent être évitées par un traitement précoce et un suivi régulier."
}
},
{
"@type": "Question",
"name": "Quels sont les principaux facteurs de risque ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, certaines maladies auto-immunes et l'exposition à des toxines."
}
},
{
"@type": "Question",
"name": "Le tabagisme influence-t-il le risque ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le tabagisme est un facteur de risque connu pour de nombreuses maladies pulmonaires, y compris celle-ci."
}
},
{
"@type": "Question",
"name": "Les maladies héréditaires jouent-elles un rôle ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines maladies génétiques peuvent prédisposer les individus à la maladie veino-occlusive."
}
},
{
"@type": "Question",
"name": "L'exposition à des produits chimiques est-elle un risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'exposition prolongée à des produits chimiques toxiques peut augmenter le risque de cette maladie."
}
},
{
"@type": "Question",
"name": "L'âge est-il un facteur de risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le risque de développer cette maladie augmente avec l'âge, surtout après 50 ans."
}
}
]
}
]
}
Sinusoidal obstruction syndrome/veno-occlusive disease (SOS/VOD) is a life-threatening complication of hematopoietic stem cell transplantation (HSCT). Early diagnosis of SOS/VOD is associated with imp...
Veno-occlusive disease with immunodeficiency (VODI) syndrome is a rare genetic disorder characterized by immune system irregularities and a significant mortality rate, despite its infrequency....
Veno-occlusive disease (VOD), also known as sinusoidal obstruction syndrome (SOS), is a life-threatening complications of hematopoietic cell transplantation (HCT)....
We studied the impact of early defibrotide (DF) therapy on the outcomes of pediatric patients with VOD/SOS after transplantation, focusing on recent immunotherapies. A total of 111 pediatric patients ...
Among 111 patients of less than 20 years of age who underwent HCT for malignancy at a single institution between 2017 and 2023, VOD/SOS occurred in 25 (23%) patients. VOD/SOS developed more frequently...
Early DF therapy improves the severity and survival outcomes of post-transplant VOD/SOS in children. However, its incidence is increasing in the era of immunotherapy for progressive diseases....
With regard to the treatment of massive pulmonary embolism (MPE) with circulatory and respiratory collapse and thrombolytic contraindications, current guidelines and researches usually give the priori...
A 35-year-old pregnant woman with gestational mellitus suddenly presented with complaints of nausea, vomiting and dyspnea after going to the toilet, combined with increasing heart rate (HR) of 150 bpm...
V-V ECMO could be effective for some patients with MPE who suffer from successful CPR after cardiac arrest while still combined with severe hypotension and refractory hypoxemia....
Hepatic veno-occlusive disease (HVOD) after liver transplantation (LT) is almost always a fatal complication. We assessed the outcomes of HVOD in a single institute and analyzed a literature-based coh...
We reviewed the medical records of recipients of LT performed between 1995 and 2020 at our institute and the literature on HVOD after LT. We then analyzed the clinical features based on a "pooled" coh...
HVOD was diagnosed in 3 of 331 LT recipients, all of whom died in hospital, on days 164, 12, and 13, respectively. Our comprehensive review of the literature, as well as our cases, identified eight ca...
Early-onset HVOD developing within 14 days after LT has a poor prognosis....
Hepatic veno-occlusive disease (VOD)/sinusoidal obstructive syndrome (SOS) is a severe complication that can occur following haematopoietic stem cell transplant (HSCT) with high-intensity conditioning...
During the past two decades, the incidence of chronic kidney disease (CKD) in children worldwide has steadily increased and, even in children, native arteriovenous fistula (AVF) remains the access of ...
A 10 year old girl with end stage renal failure dialysing through a left brachiocephalic fistula presented with left upper limb and facial swelling. She had previously exhausted the option of ambulato...
Central venous stenosis or occlusion rates are rising due to extensive central venous catheter use in the paediatric population with end stage renal failure. In this report, an ipsilateral axillary ve...
We aimed to assess the role of liver stiffness measurement (LSM), evaluated using transient elastography (TE), for the diagnosis of sinusoidal obstruction syndrome (SOS)/veno-occlusive disease (VOD), ...
In this retrospective study, ultrasonography (US) and LSM were performed on 86 adult patients (55 men and 31 women) undergoing HSCT between January 2016 and December 2022. Characteristics and changes ...
Of the 86 patients, 14 were diagnosed with SOS/VOD. A significant increase in LS (ranging from 12.6 to 55.1 kPa, median 23.8 kPa) compared to pre-HSCT values was observed in all patients who developed...
LSM using TE may contribute to establishing the diagnosis of SOS/VOD after HSCT....
Veno-occlusive disease/sinusoidal obstruction syndrome (VOD/SOS) is a life-threatening complication after allogeneic hematopoietic cell transplantation (allo-HCT), and stratification of the high-risk ...
Multiple asparaginase products have been approved by the United States (US) Food and Drug Administration (FDA) for the treatment of acute lymphoblastic leukemia in pediatric and adult patients. Hepati...