Titre : Myopathie à axe central

Myopathie à axe central : Questions médicales fréquentes

Termes MeSH sélectionnés :

Clinical Competence
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"inLanguage": "fr", "hasPart": [ { "@type": "MedicalWebPage", "name": "Diagnostic", "headline": "Diagnostic sur Myopathie à axe central", "description": "Comment diagnostique-t-on la myopathie à axe central ?\nQuels tests génétiques sont utilisés ?\nQuels signes cliniques sont observés ?\nL'IRM est-elle utile pour le diagnostic ?\nQuel rôle joue l'historique familial ?", "url": "https://questionsmedicales.fr/mesh/D020512?mesh_terms=Clinical+Competence&page=2#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Myopathie à axe central", "description": "Quels sont les principaux symptômes ?\nLa myopathie affecte-t-elle tous les muscles ?\nY a-t-il des symptômes respiratoires ?\nLes symptômes varient-ils selon l'âge ?\nDes troubles de la marche sont-ils fréquents ?", "url": "https://questionsmedicales.fr/mesh/D020512?mesh_terms=Clinical+Competence&page=2#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": 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myopathie peut-elle affecter la vie quotidienne ?\nY a-t-il un risque de cardiomyopathie ?\nLes infections sont-elles plus fréquentes ?\nComment gérer les complications ?", "url": "https://questionsmedicales.fr/mesh/D020512?mesh_terms=Clinical+Competence&page=2#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Myopathie à axe central", "description": "Quels sont les facteurs de risque génétiques ?\nL'âge est-il un facteur de risque ?\nLe sexe influence-t-il le risque ?\nDes facteurs environnementaux jouent-ils un rôle ?\nLes maladies associées augmentent-elles le risque ?", "url": "https://questionsmedicales.fr/mesh/D020512?mesh_terms=Clinical+Competence&page=2#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostique-t-on la myopathie à axe central ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Le diagnostic repose sur l'examen clinique, l'électromyogramme et la biopsie musculaire." } }, { "@type": "Question", "name": "Quels tests génétiques sont utilisés ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Des tests génétiques peuvent identifier des mutations dans le gène RYR1, associé à cette myopathie." } }, { "@type": "Question", "name": "Quels signes cliniques sont observés ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "On observe souvent une faiblesse musculaire proximale et des anomalies dans les biopsies musculaires." } }, { "@type": "Question", "name": "L'IRM est-elle utile pour le diagnostic ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'IRM peut montrer des anomalies musculaires caractéristiques de la myopathie à axe central." } }, { "@type": "Question", "name": "Quel rôle joue l'historique familial ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Un historique familial de myopathies peut orienter le diagnostic vers une origine génétique." } }, { "@type": "Question", "name": "Quels sont les principaux symptômes ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent faiblesse musculaire, fatigue et parfois des douleurs musculaires." } }, { "@type": "Question", "name": "La myopathie affecte-t-elle tous les muscles ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Elle touche principalement les muscles proximaux, comme ceux des hanches et des épaules." } }, { "@type": "Question", "name": "Y a-t-il des symptômes respiratoires ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Dans certains cas, la faiblesse musculaire peut affecter les muscles respiratoires." } }, { "@type": "Question", "name": "Les symptômes varient-ils selon l'âge ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les symptômes peuvent apparaître dès l'enfance ou à l'âge adulte, selon les cas." } }, { "@type": "Question", "name": "Des troubles de la marche sont-ils fréquents ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la faiblesse musculaire peut entraîner des difficultés à marcher ou à se lever." } }, { "@type": "Question", "name": "Peut-on prévenir la myopathie à axe central ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Étant génétique, il n'existe pas de prévention, mais un diagnostic précoce aide à la gestion." } }, { "@type": "Question", "name": "Le dépistage est-il recommandé ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "Le dépistage génétique peut être conseillé pour les familles à risque de transmission." } }, { "@type": "Question", "name": "Des conseils de vie peuvent-ils aider ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Des conseils sur l'exercice et la nutrition peuvent améliorer la qualité de vie des patients." } }, { "@type": "Question", "name": "Les activités physiques sont-elles bénéfiques ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Des activités adaptées peuvent aider à maintenir la force musculaire et la mobilité." } }, { "@type": "Question", "name": "Les consultations régulières sont-elles nécessaires ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des suivis réguliers permettent d'ajuster les traitements et surveiller l'évolution." } }, { "@type": "Question", "name": "Quels traitements sont disponibles ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Il n'existe pas de traitement curatif, mais la physiothérapie aide à maintenir la force musculaire." } }, { "@type": "Question", "name": "Les médicaments sont-ils efficaces ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Des médicaments peuvent être prescrits pour gérer les symptômes, mais leur efficacité varie." } }, { "@type": "Question", "name": "La chirurgie est-elle une option ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "La chirurgie n'est généralement pas indiquée, sauf pour des complications spécifiques." } }, { "@type": "Question", "name": "Comment la rééducation aide-t-elle ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "La rééducation physique aide à améliorer la fonction musculaire et la qualité de vie." } }, { "@type": "Question", "name": "Y a-t-il des traitements expérimentaux ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Des essais cliniques explorent des thérapies géniques et des traitements ciblés." } }, { "@type": "Question", "name": "Quelles complications peuvent survenir ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent des problèmes respiratoires et des déformations musculo-squelettiques." } }, { "@type": "Question", "name": "La myopathie peut-elle affecter la vie quotidienne ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la faiblesse musculaire peut limiter les activités quotidiennes et l'autonomie." } }, { "@type": "Question", "name": "Y a-t-il un risque de cardiomyopathie ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "Certaines formes de myopathie peuvent être associées à des problèmes cardiaques." } }, { "@type": "Question", "name": "Les infections sont-elles plus fréquentes ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Les infections peuvent survenir en raison de la faiblesse musculaire et de l'immobilité." } }, { "@type": "Question", "name": "Comment gérer les complications ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Une prise en charge multidisciplinaire est essentielle pour gérer les complications." } }, { "@type": "Question", "name": "Quels sont les facteurs de risque génétiques ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les antécédents familiaux de myopathies augmentent le risque de développer cette maladie." } }, { "@type": "Question", "name": "L'âge est-il un facteur de risque ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "L'âge d'apparition peut varier, mais les symptômes se manifestent souvent dans l'enfance." } }, { "@type": "Question", "name": "Le sexe influence-t-il le risque ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Les myopathies peuvent affecter les deux sexes, mais certaines formes sont plus fréquentes chez les hommes." } }, { "@type": "Question", "name": "Des facteurs environnementaux jouent-ils un rôle ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Actuellement, les facteurs environnementaux ne sont pas clairement établis comme des risques." } }, { "@type": "Question", "name": "Les maladies associées augmentent-elles le risque ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Certaines maladies auto-immunes peuvent coexister avec la myopathie, mais leur lien n'est pas direct." } } ] } ] }

Sources (10000 au total)

Effects of Expert Modeling Videos on the Development of Nursing Students' Clinical Competence.

Nurse educators are called to develop innovative teaching strategies to build clinical competency. Expert modeling videos (EMVs) promote clinical competency by demonstrating exemplar nursing care.... A quasiexperimental research study was conducted using a prebriefing intervention of a nursing process video for demonstration (experimental) and discussion (control) groups of nursing students. Simul... Students in the experimental group demonstrated a statistically significant improvement in simulation competency (... The use of EMVs in simulation prebriefing is an innovative teaching strategy to prepare undergraduate nursing students with the knowledge and skills required to enter the simulated environment. Throug...

Evidence-based Surgical Competency Outcomes from the Clinical Readiness Program.

1) Evaluate the value and strength of a competency framework for identifying and measuring performance requirements for expeditionary surgeons; 2) Verify psychometric integrity of assessment instrumen... Expeditionary military surgeons provide care for patients with injuries that extend beyond the care requirements of their routine surgical practice. The readiness of these surgeons to independently pr... We implemented evidence-based processes for identifying and measuring the essential performance competencies for expeditionary surgeons. All assessment instrumentation was rigorously examined for psyc... Outcomes confirmed the integrity of assessment instrumentation and identified significant performance gaps for knowledge and skills in the domain.... Identification of domain competencies and performance benchmarks, combined with best-practices in assessment instrumentation, provided a rigorous and defensible framework for quantifying domain compet...

The impact of the evaluations made by Mini-CEX on the clinical competency of nursing students.

Clinical competency is defined as one's capabilities in terms of knowledge, attitude and practice, and is a necessity for nursing practice. Evaluation is the inseparable part of the education process,... This is a quasi-experimental study with a control group conducted on students who were taking courses "Nursing care for a sick child". The students were classified into the intervention and control gr... The results showed that the mean score of clinical competency in the intervention group was significantly higher than that of the control group.... Considering the improvement of clinical competency in the intervention group, it is recommended to use Mini-Clinical Evaluation Exercise for the evaluation of students....

Determinants of clinical nurses' patient safety competence: a systematic review protocol.

Patient safety has become a fundamental element of healthcare quality. However, despite the ongoing efforts of various organisations, patient safety issues remain a problem in the healthcare system. G... This review protocol is based on the Joanna Briggs Institute (JBI) Methodology for Systematic Reviews of Effectiveness and Preferred Reporting Items for Systematic Review and Meta-Analysis Protocols. ... Ethical review is not relevant to this study. The findings will be presented at professional conferences and published in peer-reviewed journals.... CRD42023422486....

Lesbian, gay, bisexual, and transgender clinical competence of physiotherapy students in Israel.

Clinical competence encompasses attitudes, skills, and knowledge regarding diverse client groups. Appropriate clinical competence requires an understanding of the cultural context in which healthcare ... Conducted through an anonymous online self-report survey, this study gathered personal and academic background information and self-reported data on previous LGBT education during undergraduate studie... The sample comprised of 251 PTSs, with an average age of 25.57 ± 3.07 years (34.7% men, 65.3% women). All students reported a lack of LGBT community-related courses during their undergraduate studies.... In Israel, PTSs demonstrated a low level of clinical competency in terms of self-reported knowledge and self-reported clinical preparedness but contrasting positive attitudes toward the LGBT community... Not applicable....

Perceived clinical competence and predictive role of time management in nursing students.

The purpose of this study was to determine the association between perceived clinical competence and time management among nursing students.... Given the close relationship between clinical competence and nursing care quality, it is important to investigate the nursing students' status in relation to the acquisition of nursing skills. Time ma... A cross-sectional and correlational study SETTINGS/PARTICIPANTS: This study included 221 undergraduate nursing students in Ahvaz Jundishapur University of Medical Sciences in Iran in the 2022-2023 aca... The data were collected online through a demographic information questionnaire, the clinical competency inventory, and the time management questionnaire.... Students' mean scores for the clinical-competency, and time management were 120.38 ± 22.15, and 77.91 ± 15.15, respectively. Regression models showed that overall time management (β = 0.454, p < 0.001... Time management can affect nursing students' competence in providing quality nursing care to patients. Therefore, it seems that holding training workshops on time management skills for nursing student...

Antibiotic prescription errors: the relationship with clinical competence in junior medical residents.

A large portion of prescribing errors can be attributed to deficiencies in medication knowledge. These errors are preventable and most often occur at the time of prescription. Antimicrobials are the d... To characterize the relationship between clinical competence and antibiotic prescription errors. We also investigated the frequency and severity of antibiotic prescription errors to identify items and... A cross-sectional study was applied to assess clinical competence of junior medical residents in two reference academic hospitals and a regional hospital in Mexico City. It was conducted during Februa... The number of eligible participants was ~ 255 (hospital meeting attendance), and the number of residents in this study were 51 (~ 20%), 31 were female (60.8%). The mean OSCE score was 0.692 ± 0.073. T... We observed a negative correlation between clinical competence and antibiotic prescription error ratio in graduated physicians who have been accepted in a medical specialty. The therapeutic plan, whic...

Perceived competence and related factors affecting the development of the clinical competence of nursing students at two university sites in Namibia: a cross-sectional study.

Ensuring that nursing students graduate with the required clinical competence in nursing is a global challenge. To address this challenge, several studies have looked at various aspects of competency ... A cross-sectional design was utilised. Simple random sampling was applied and 272 nursing students at two university campuses in Namibia were selected. An online questionnaire was used. Data were coll... Forty-seven percent (47%) of the students were found to be competent while more than half (53%) were not. A Chi-square test found a statistically significant difference between students studying at di... Educator's competence levels and the mode of learning were the two major factors that were more likely to influence the development of clinical competence among nursing students. Therefore, it is reco...

Effects of Standardized Patient Simulation and Mobile Applications on Nursing Students' Clinical Competence, Self-Efficacy, and Cultural Competence: A Quasi-Experimental Study.

Simulation-based education has emerged as an effective approach in nursing education worldwide. We aimed to evaluate the effectiveness of a surgical nursing education program based on a simulation usi... A mixed-methods design with a quasi-experimental longitudinal approach and focus group interviews was employed. The data were collected from 130 third-year nursing students at three different time poi... There were statistically significant differences in clinical surgical nursing competence (F = 8.68,... Simulation-based learning provides a dynamic and immersive educational experience that enables undergraduate nursing students to develop and refine essential clinical skills while also fostering confi...