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États, signes et symptômes pathologiques
Signes et symptômes
Manifestations neurologiques
Manifestations neuromusculaires
Manifestations neuromusculaires : Questions médicales fréquentes
Termes MeSH sélectionnés :
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"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement comprend le contrôle de la glycémie, des analgésiques et des thérapies physiques."
}
},
{
"@type": "Question",
"name": "Quel est le traitement de la myasthénie ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement inclut des inhibiteurs de l'acétylcholinestérase et parfois des immunosuppresseurs."
}
},
{
"@type": "Question",
"name": "Quelles options pour la sclérose latérale amyotrophique ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les options incluent des médicaments pour ralentir la progression et des soins palliatifs."
}
},
{
"@type": "Question",
"name": "Comment gérer le syndrome de Guillain-Barré ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement peut inclure des immunoglobulines intraveineuses et une rééducation physique."
}
},
{
"@type": "Question",
"name": "Quelles complications des myopathies ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications peuvent inclure des déformations squelettiques, des problèmes respiratoires et cardiaques."
}
},
{
"@type": "Question",
"name": "Quels risques avec la neuropathie ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les risques incluent des blessures dues à une perte de sensation et des infections cutanées."
}
},
{
"@type": "Question",
"name": "Quelles complications de la myasthénie ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications peuvent inclure des crises myasthéniques, affectant la respiration et la déglutition."
}
},
{
"@type": "Question",
"name": "Quels problèmes liés à la sclérose latérale amyotrophique ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les problèmes incluent la paralysie progressive, des difficultés respiratoires et des infections."
}
},
{
"@type": "Question",
"name": "Quelles complications du syndrome de Guillain-Barré ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications peuvent inclure des problèmes respiratoires, des douleurs chroniques et des séquelles neurologiques."
}
},
{
"@type": "Question",
"name": "Quels facteurs de risque pour les myopathies ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux, des infections virales et des troubles métaboliques."
}
},
{
"@type": "Question",
"name": "Quels risques pour la neuropathie diabétique ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le diabète mal contrôlé, l'obésité et l'hypertension augmentent le risque de neuropathie."
}
},
{
"@type": "Question",
"name": "Quels facteurs de risque pour la myasthénie ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des maladies auto-immunes, des infections et des antécédents familiaux."
}
},
{
"@type": "Question",
"name": "Quels risques pour la sclérose latérale amyotrophique ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs de risque incluent l'âge avancé, le sexe masculin et des antécédents familiaux."
}
},
{
"@type": "Question",
"name": "Quels facteurs de risque pour le syndrome de Guillain-Barré ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les infections virales, notamment la grippe, et des antécédents de vaccination peuvent être des facteurs de risque."
}
}
]
}
]
}
The relationship between primary sclerosing cholangitis (PSC) and biliary bile acids (BAs) remains unclear. Although a few studies have compared PSC biliary BAs with other diseases, they did not exclu...
Bile samples were obtained using endoscopic retrograde cholangiopancreatography from patients with PSC (n = 14), non-hepato-pancreato-biliary patients without cholestasis (n = 15), and patients with c...
The BA profiles showed that patients with PSC and cholestasis controls had significantly lower secondary BAs than non-cholestasis controls, as expected, whereas the ratio of cholic acid/chenodeoxychol...
Patients with PSC showed characteristic biliary and serum BA compositions that were different from those in other groups. These findings suggest that the BA synthesis system in patients with PSC diffe...
Obeticholic acid (OCA) is a farnesoid X receptor agonist used in primary biliary cholangitis (PBC) treatment. Recent studies have expanded OCA use for NASH treatment and results from phase 3 clinical ...
A search was conducted in Medline and Embase databases for OCA randomized controlled trials in chronic liver disease. Binary events were pooled with Paule-Mandel random effects model and proportional ...
A total of 8 studies and 1878 patients were analyzed. There was a 75% [risk ratio (RR): 1.75, 95% CI: 1.43-2.15, p < 0.01] increased pruritis risk. OCA increased constipation incidence (RR: 1.88, 95% ...
OCA may represent the first pharmacological treatment approved for NASH. However, pruritis, constipation, diarrhea, and hyperlipidemia were major events with evident dose-dependent effect that affect ...
Bile acids are important for digestion of food and antimicrobial activity. Pathogenic Vibrio parahaemolyticus senses bile acids and induce pathogenesis. The bile acid taurodeoxycholate (TDC) was shown...
Excess fat accumulation is not only associated with metabolic diseases but also negatively impacts physical appearance and emotional well-being. Bile acid, the body's natural emulsifier, is one of the...
Lipoprotein-derived nanotherapeutics based on endogenous lipid supramolecules have been regarded as an exceptional and promising approach for anti-tumor drug delivery. However, certain challenges asso...
Bacterial lipopolysaccharide (LPS) induces general inflammation, by activating pathways involving cytokine production, blood coagulation, complement system activation, and acute phase protein release....
The levels of fasting-state serum bile acids (BAs) in individuals with polycystic ovary syndrome (PCOS) differ from those of control subjects. However, there is a lack of research on the BAs profile i...
Recent discoveries have demonstrated that the physiological function of bile acids extends to the regulation of diverse signaling processes through interactions with nuclear and G protein-coupled rece...
Obeticholic acid (OCA) has recently been restricted in patients with primary biliary cholangitis (PBC) with "advanced cirrhosis" because of its narrow therapeutic index. We aimed to better define the ...
Safety and efficacy of treatment were evaluated in a cohort of consecutive PBC cirrhotic patients started with OCA. OCA response was evaluated according to the Poise criteria. Risk factors for hepatic...
One hundred PBC cirrhotics were included, 97 Child-Pugh class A and 3 class B. Thirty-one had oesophageal varices and 5 had a history of ascites. Thirty-three per cent and 32% of patients achieved a b...
An accurate baseline assessment is crucial to select cirrhotic patients who can benefit from OCA. Although OCA is effective in one third of cirrhotics, bilirubin level ≥1.4 mg/dl should discourage fro...
Congenital bile acid synthesis defect (BASD) is a rare disease caused by mutations in the aldo-keto reductase 1D1 gene, which encodes the primary Δ4-3-oxosteroid 5β-reductase enzyme. Early disease dia...
Three clinical congenital bile acid synthesis defect cases in the Vietnamese population are herein reported. These pediatric patients presented with symptoms of prolonged postpartum jaundice and abnor...
The patients were diagnosed with primary Δ4-3-oxosteroid 5β-reductase deficiency. Next-generation gene sequencing revealed two homozygous mutations in the aldo-keto reductase family 1 member D1 gene. ...
Immediately after diagnosis, patients were treated with oral chenodeoxycholate 5 mg/kg/d....
The patients' symptoms, signs, and primary bile acids levels improved significantly....
Clinicians should consider genetic disorders related to cholestasis for effective and life-saving treatment. A prompt genetic analysis by next-generation gene sequencing enables patients to access bil...