questionsmedicales.fr
Maladies du système immunitaire
Troubles de l'activation mastocytaire
Mastocytose
Mastocytose cutanée
Mastocytose cutanée : Questions médicales fréquentes
Diagnostic
5
Mastocytose
Biopsie cutanée
Urticaire
Affections cutanées
Antécédents médicaux
Allergies
Symptômes
5
Démangeaisons
Lésions cutanées
Variabilité des symptômes
Individus
Symptômes systémiques
Nausées
Lésions cutanées
Contagiosité
Prévention
5
Stress
Poussées de symptômes
Soins de la peau
Irritations
Traitements
5
Antihistaminiques
Corticostéroïdes
Antihistaminiques
Démangeaisons
Photothérapie
Lésions cutanées
Gestion des symptômes
Traitements
Traitements alternatifs
Efficacité
Complications
5
Complications
Infections cutanées
Mastocytose systémique
Évolution
Gestion
Consultation spécialisée
Facteurs de risque
5
Facteurs de risque
Antécédents familiaux
Maladies auto-immunes
Risque
Produits chimiques
Exposition
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"@type": "Question",
"name": "Quels tests sont utilisés pour confirmer la mastocytose ?",
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"@type": "Question",
"name": "La mastocytose cutanée provoque-t-elle des douleurs ?",
"position": 7,
"acceptedAnswer": {
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"text": "Elle peut provoquer des douleurs localisées, surtout en cas de lésions étendues."
}
},
{
"@type": "Question",
"name": "Les symptômes varient-ils d'une personne à l'autre ?",
"position": 8,
"acceptedAnswer": {
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"text": "Oui, l'intensité et la nature des symptômes peuvent varier considérablement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes systémiques associés ?",
"position": 9,
"acceptedAnswer": {
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"text": "Des symptômes systémiques comme des nausées peuvent survenir dans certains cas."
}
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"@type": "Question",
"name": "Les lésions cutanées sont-elles contagieuses ?",
"position": 10,
"acceptedAnswer": {
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}
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"@type": "Question",
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"position": 11,
"acceptedAnswer": {
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"name": "Les allergènes peuvent-ils aggraver la condition ?",
"position": 12,
"acceptedAnswer": {
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"text": "Oui, l'exposition à certains allergènes peut aggraver les symptômes."
}
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{
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"name": "Faut-il éviter certains médicaments ?",
"position": 13,
"acceptedAnswer": {
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}
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"name": "L'évitement du stress aide-t-il ?",
"position": 14,
"acceptedAnswer": {
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"name": "Les soins de la peau sont-ils importants ?",
"position": 15,
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}
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"name": "Quels traitements sont disponibles pour la mastocytose cutanée ?",
"position": 16,
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"text": "Les traitements incluent des antihistaminiques et des corticostéroïdes topiques."
}
},
{
"@type": "Question",
"name": "Les antihistaminiques sont-ils efficaces ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils aident à réduire les démangeaisons et les rougeurs."
}
},
{
"@type": "Question",
"name": "La photothérapie est-elle une option de traitement ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la photothérapie peut être utilisée pour traiter les lésions cutanées."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils permanents ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les traitements visent à gérer les symptômes, pas à guérir la maladie."
}
},
{
"@type": "Question",
"name": "Des traitements alternatifs existent-ils ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines personnes explorent des traitements alternatifs, mais leur efficacité n'est pas prouvée."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec la mastocytose cutanée ?",
"position": 21,
"acceptedAnswer": {
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}
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{
"@type": "Question",
"name": "La mastocytose cutanée peut-elle évoluer vers une forme plus grave ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Dans de rares cas, elle peut évoluer vers une mastocytose systémique."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles fréquentes ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications ne sont pas fréquentes mais peuvent survenir chez certains patients."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion des complications nécessite souvent une consultation spécialisée."
}
},
{
"@type": "Question",
"name": "Les complications affectent-elles la qualité de vie ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les complications peuvent affecter la qualité de vie en raison de l'inconfort."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque de la mastocytose cutanée ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux et des allergies cutanées."
}
},
{
"@type": "Question",
"name": "L'âge joue-t-il un rôle dans la mastocytose cutanée ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la mastocytose cutanée est plus fréquente chez les enfants et les jeunes adultes."
}
},
{
"@type": "Question",
"name": "Les femmes sont-elles plus touchées que les hommes ?",
"position": 28,
"acceptedAnswer": {
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"text": "Non, la mastocytose cutanée affecte les hommes et les femmes de manière égale."
}
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{
"@type": "Question",
"name": "Les maladies auto-immunes augmentent-elles le risque ?",
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}
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"name": "L'exposition à des produits chimiques est-elle un facteur ?",
"position": 30,
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}
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Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 31/01/2025
Contenu vérifié selon les dernières recommandations médicales
9 publications dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland.
6 publications dans cette catégorie
Affiliations :
Allergologische Poliklinik, Klinik für Dermatologie, Universitätsspital Basel, Petersgraben 4, 4031, Basel, Schweiz. karin.hartmann@usb.ch.
5 publications dans cette catégorie
Affiliations :
Department of Dermatology and Allergy Biederstein, School of Medicine and Health, Technical University of Munich, 80802 Munich, Germany.
Department of Dermatology and Allergy Centre, Odense University Hospital, 5000 Odense, Denmark.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology and Mastocytosis Expert Centre (CEREMAST), Necker Children's Hospital and Paris Descartes University, Assistance Publique Hôpitaux de Paris, Paris, France. Electronic address: ohermine@gmail.com.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology Oncology, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Allergology, Medical University of Gdansk, Gdansk, Poland.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Section of Hematology, Department of Medicine, Verona University Hospital, Verona, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Allergy Unit, Verona University Hospital, Verona, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Division of Hematology, Department of Medicine, Stanford University School of Medicine, Stanford, California, USA.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology and Oncology, University Hospital Mannheim, Heidelberg University, Mannheim, Germany.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Internal Medicine I, Division of Hematology & Hemostaseology, Medical University of Vienna, Vienna, Austria; Ludwig Boltzmann Institute for Hematology and Oncology, Medical University of Vienna, Vienna, Austria; Internal Medicine Small Animals, University Clinic for Small Animals, Department/University Clinic for Companion Animals and Horses, University of Veterinary Medicine, Vienna, Austria.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Division of Allergy and Clinical Immunology, University of Salerno, Salerno, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Pediatric Dermatology Unit, Department of Medicine, University of Padova, Padova, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Pediatric Dermatology Unit, Department of Medicine, University of Padova, Padova, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
University Hospital and Faculty of Medicine, Brno, Czechia.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Faculty of Medicine and Health Sciences, Department of Immunology-Allergology-Rheumatology, University of Antwerp and Antwerp University Hospital, Antwerpen, Belgium.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Division of Allergy and Clinical Immunology, University of Salerno, Salerno, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Hematology, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Oncology, Haematology, Haemostaseology and Stem Cell Transplantation, University Hospital RWTH Aachen, Aachen, Germany; Center for Integrated Oncology, Aachen Bonn Cologne Düsseldorf (CIO ABCD), Aachen, Germany.
Publications dans "Mastocytose cutanée" :
The management of the COVID-19 vaccine in children with mastocytosis is unclear due to a lack of data. In the current study, we aimed to evaluate the adverse reactions following COVID-19 vaccination i...
This study included 27 paediatric patients who were diagnosed with CM and were followed up in the paediatric allergy department of a tertiary care children's hospital....
The median (IQR) age of the patients at the time of COVID-19 vaccination was 180 (156-203) months. Forty-four per cent of patients were vaccinated with the COVID-19 vaccine. Among all participants, th...
The COVID-19 vaccination of patients with CM in this series seems to be safe, and the rate of adverse events was comparable to that in the general population. These results found in adolescents with C...
Mastocytosis is a condition characterized by accumulation of clonal mast cells (MCs) that often involves the skin. Pathologists are often challenged with skin biopsies with a question of cutaneous les...
Mastocytosis is characterized by the accumulation of mast cells (MCs) in the skin or other organs, and can manifest at any age. A significant number of paediatric mastocytosis cases persist after pube...
To identify histopathological features that can help to distinguish mMPCM from other subtypes of paediatric mastocytosis....
This was a retrospective study using skin biopsies from patients with any subtype of mastocytosis. The localization and density of the MC infiltrate, MC morphology and expression of aberrant markers w...
In total, 33 biopsies were available for evaluation from 26 children [(10 with mMPCM, 5 with mastocytoma, 3 with diffuse cutaneous mastocytosis (DCM), 8 with pMPCM)] and 7 adults with MPCM. The MC num...
Skin histopathology might enhance the phenotypical differentiation of mMPCM from other subtypes in children, thereby increasing the accuracy of one's prognosis....
Cutaneous lesions of mastocytosis (CLM) are often subtle and may require biopsy. However, dermatohistopathological criteria for CLM remain undefined....
To establish criteria for CLM by validating histological and molecular parameters....
In skin samples from Caucasian patients with CLM and controls (atopic dermatitis, chronic urticaria, pruritus, tissue from tumor safety margin excisions), mast cell (MC) numbers, size, shape, distribu...
Forty-seven CLM patients (32 maculopapular cutaneous mastocytosis (MPCM), 15 mastocytomas) and 36 controls were included. Mastocytomas were easily identified by densely packed cuboidal MCs. In MPCM, s...
MPCM can be predicted by major and minor criteria combined in a scoring model. Presence of D816V mutation in FFPE skin and MC density > 27/HPF are >95%-specific major criteria for MPCM. MC densities 1...
Mast cell skin disease is rarely described after external beam radiation therapy in patients with breast carcinoma, with only 7 previous reports in the literature. Skin changes typically occur within ...
Mastocytosis is a KIT-related myeloproliferative disease characterised by abnormal expansion of neoplastic mast cells (MC) in the skin or virtually any other organ system. The cutaneous form of adult-...
Neonatal diffuse cutaneous mastocytosis (NDCM) is defined as the infiltration of the epidermis by a clonal proliferation of mast cells, observed at birth, without initial signs of systemic involvement...
Organomegaly, including splenomegaly, hepatomegaly, and/or lymphadenopathy, are important diagnostic and prognostic features in patients with cutaneous mastocytosis (CM) or systemic mastocytosis (SM)....
To investigate the prevalence and prognostic impact of 1 or more organomegalies on clinical course and survival in patients with CM/SM....
Therefore, 3155 patients with CM (n = 1002 [32%]) or SM (n = 2153 [68%]) enrolled within the registry of the European Competence Network on Mastocytosis were analyzed....
Overall survival (OS) was adversely affected by the number of organomegalies (OS: #0 vs #1 hazard ratio [HR], 4.9; 95% CI, 3.4-7.1, P < .001; #1 vs #2 HR, 2.1, 95% CI, 1.4-3.1, P < .001; #2 vs #3 HR, ...
Organomegalies including lymphadenopathy are often found in SSM and AdvSM. ISM with organomegaly has a similar course and prognosis compared with SSM. The number of organomegalies is adversely associa...
To a large extent, the clinical picture of pediatric mastocytosis depends on the age at which it is diagnosed. A neonate with diffuse cutaneous mastocytosis may frequently present in a severe state re...
Mastocytosis is a complex heterogenous multisystem disorder that is characterized by pathologic activation or accumulation of neoplastic mast cells (MCs) in one or more organs. This clonal MC expansio...