questionsmedicales.fr
Maladies du système immunitaire
Troubles de l'activation mastocytaire
Mastocytose
Mastocytose cutanée
Mastocytose cutanée : Questions médicales fréquentes
Termes MeSH sélectionnés :
{
"@context": "https://schema.org",
"@graph": [
{
"@type": "MedicalWebPage",
"name": "Mastocytose cutanée : Questions médicales les plus fréquentes",
"headline": "Mastocytose cutanée : Comprendre les symptômes, diagnostics et traitements",
"description": "Guide complet et accessible sur les Mastocytose cutanée : explications, diagnostics, traitements et prévention. Information médicale validée destinée aux patients.",
"datePublished": "2024-08-04",
"dateModified": "2025-05-01",
"inLanguage": "fr",
"medicalAudience": [
{
"@type": "MedicalAudience",
"name": "Grand public",
"audienceType": "Patient",
"healthCondition": {
"@type": "MedicalCondition",
"name": "Mastocytose cutanée"
},
"suggestedMinAge": 18,
"suggestedGender": "unisex"
},
{
"@type": "MedicalAudience",
"name": "Médecins",
"audienceType": "Physician",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "France"
}
},
{
"@type": "MedicalAudience",
"name": "Chercheurs",
"audienceType": "Researcher",
"geographicArea": {
"@type": "AdministrativeArea",
"name": "International"
}
}
],
"reviewedBy": {
"@type": "Person",
"name": "Dr Olivier Menir",
"jobTitle": "Expert en Médecine",
"description": "Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale",
"url": "/static/pages/docteur-olivier-menir.html",
"alumniOf": {
"@type": "EducationalOrganization",
"name": "Université Paris Descartes"
}
},
"isPartOf": {
"@type": "MedicalWebPage",
"name": "Mastocytose",
"url": "https://questionsmedicales.fr/mesh/D008415",
"about": {
"@type": "MedicalCondition",
"name": "Mastocytose",
"code": {
"@type": "MedicalCode",
"code": "D008415",
"codingSystem": "MeSH"
},
"identifier": {
"@type": "PropertyValue",
"propertyID": "MeSH Tree",
"value": "C20.762.750"
}
}
},
"hasPart": [
{
"@type": "MedicalWebPage",
"name": "Mastocytome cutané",
"alternateName": "Mastocytoma, Skin",
"url": "https://questionsmedicales.fr/mesh/D054705",
"about": {
"@type": "MedicalCondition",
"name": "Mastocytome cutané",
"code": {
"@type": "MedicalCode",
"code": "D054705",
"codingSystem": "MeSH"
},
"identifier": {
"@type": "PropertyValue",
"propertyID": "MeSH Tree",
"value": "C20.762.750.563.500"
}
}
},
{
"@type": "MedicalWebPage",
"name": "Urticaire pigmentaire",
"alternateName": "Urticaria Pigmentosa",
"url": "https://questionsmedicales.fr/mesh/D014582",
"about": {
"@type": "MedicalCondition",
"name": "Urticaire pigmentaire",
"code": {
"@type": "MedicalCode",
"code": "D014582",
"codingSystem": "MeSH"
},
"identifier": {
"@type": "PropertyValue",
"propertyID": "MeSH Tree",
"value": "C20.762.750.563.850"
}
}
}
],
"about": {
"@type": "MedicalCondition",
"name": "Mastocytose cutanée",
"alternateName": "Mastocytosis, Cutaneous",
"code": {
"@type": "MedicalCode",
"code": "D034701",
"codingSystem": "MeSH"
}
},
"author": [
{
"@type": "Person",
"name": "Magdalena Lange",
"url": "https://questionsmedicales.fr/author/Magdalena%20Lange",
"affiliation": {
"@type": "Organization",
"name": "Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland."
}
},
{
"@type": "Person",
"name": "Karin Hartmann",
"url": "https://questionsmedicales.fr/author/Karin%20Hartmann",
"affiliation": {
"@type": "Organization",
"name": "Allergologische Poliklinik, Klinik für Dermatologie, Universitätsspital Basel, Petersgraben 4, 4031, Basel, Schweiz. karin.hartmann@usb.ch."
}
},
{
"@type": "Person",
"name": "Knut Brockow",
"url": "https://questionsmedicales.fr/author/Knut%20Brockow",
"affiliation": {
"@type": "Organization",
"name": "Department of Dermatology and Allergy Biederstein, School of Medicine and Health, Technical University of Munich, 80802 Munich, Germany."
}
},
{
"@type": "Person",
"name": "Roman J Nowicki",
"url": "https://questionsmedicales.fr/author/Roman%20J%20Nowicki",
"affiliation": {
"@type": "Organization",
"name": "Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland."
}
},
{
"@type": "Person",
"name": "Olivier Hermine",
"url": "https://questionsmedicales.fr/author/Olivier%20Hermine",
"affiliation": {
"@type": "Organization",
"name": "Department of Hematology and Mastocytosis Expert Centre (CEREMAST), Necker Children's Hospital and Paris Descartes University, Assistance Publique Hôpitaux de Paris, Paris, France. Electronic address: ohermine@gmail.com."
}
}
],
"citation": [
{
"@type": "ScholarlyArticle",
"name": "[Overview of care management principles in functional neurological disorders].",
"datePublished": "2023-07-01",
"url": "https://questionsmedicales.fr/article/37400336",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1016/j.encep.2023.06.007"
}
},
{
"@type": "ScholarlyArticle",
"name": "Functional Neurological Disorder-Old Problem New Perspective.",
"datePublished": "2023-01-08",
"url": "https://questionsmedicales.fr/article/36673871",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.3390/ijerph20021099"
}
},
{
"@type": "ScholarlyArticle",
"name": "Functional Neurological Disorders: Clinical Spectrum, Diagnosis, and Treatment.",
"datePublished": "2022-09-01",
"url": "https://questionsmedicales.fr/article/35858632",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1097/NRL.0000000000000453"
}
},
{
"@type": "ScholarlyArticle",
"name": "Neurometabolic alterations in children and adolescents with functional neurological disorder.",
"datePublished": "2023-12-21",
"url": "https://questionsmedicales.fr/article/38219534",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.1016/j.nicl.2023.103557"
}
},
{
"@type": "ScholarlyArticle",
"name": "Understanding Functional Neurological Disorder: Recent Insights and Diagnostic Challenges.",
"datePublished": "2024-04-18",
"url": "https://questionsmedicales.fr/article/38674056",
"identifier": {
"@type": "PropertyValue",
"propertyID": "DOI",
"value": "10.3390/ijms25084470"
}
}
],
"breadcrumb": {
"@type": "BreadcrumbList",
"itemListElement": [
{
"@type": "ListItem",
"position": 1,
"name": "questionsmedicales.fr",
"item": "https://questionsmedicales.fr"
},
{
"@type": "ListItem",
"position": 2,
"name": "Maladies du système immunitaire",
"item": "https://questionsmedicales.fr/mesh/D007154"
},
{
"@type": "ListItem",
"position": 3,
"name": "Troubles de l'activation mastocytaire",
"item": "https://questionsmedicales.fr/mesh/D000090362"
},
{
"@type": "ListItem",
"position": 4,
"name": "Mastocytose",
"item": "https://questionsmedicales.fr/mesh/D008415"
},
{
"@type": "ListItem",
"position": 5,
"name": "Mastocytose cutanée",
"item": "https://questionsmedicales.fr/mesh/D034701"
}
]
}
},
{
"@type": "MedicalWebPage",
"name": "Article complet : Mastocytose cutanée - Questions et réponses",
"headline": "Questions et réponses médicales fréquentes sur Mastocytose cutanée",
"description": "Une compilation de questions et réponses structurées, validées par des experts médicaux.",
"datePublished": "2025-05-09",
"inLanguage": "fr",
"hasPart": [
{
"@type": "MedicalWebPage",
"name": "Diagnostic",
"headline": "Diagnostic sur Mastocytose cutanée",
"description": "Comment diagnostique-t-on la mastocytose cutanée ?\nQuels tests sont utilisés pour confirmer la mastocytose ?\nLes symptômes sont-ils suffisants pour le diagnostic ?\nLa mastocytose cutanée est-elle confondue avec d'autres maladies ?\nQuel rôle joue l'historique médical dans le diagnostic ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-diagnostic"
},
{
"@type": "MedicalWebPage",
"name": "Symptômes",
"headline": "Symptômes sur Mastocytose cutanée",
"description": "Quels sont les symptômes courants de la mastocytose cutanée ?\nLa mastocytose cutanée provoque-t-elle des douleurs ?\nLes symptômes varient-ils d'une personne à l'autre ?\nY a-t-il des symptômes systémiques associés ?\nLes lésions cutanées sont-elles contagieuses ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-symptômes"
},
{
"@type": "MedicalWebPage",
"name": "Prévention",
"headline": "Prévention sur Mastocytose cutanée",
"description": "Peut-on prévenir la mastocytose cutanée ?\nLes allergènes peuvent-ils aggraver la condition ?\nFaut-il éviter certains médicaments ?\nL'évitement du stress aide-t-il ?\nLes soins de la peau sont-ils importants ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-prévention"
},
{
"@type": "MedicalWebPage",
"name": "Traitements",
"headline": "Traitements sur Mastocytose cutanée",
"description": "Quels traitements sont disponibles pour la mastocytose cutanée ?\nLes antihistaminiques sont-ils efficaces ?\nLa photothérapie est-elle une option de traitement ?\nLes traitements sont-ils permanents ?\nDes traitements alternatifs existent-ils ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-traitements"
},
{
"@type": "MedicalWebPage",
"name": "Complications",
"headline": "Complications sur Mastocytose cutanée",
"description": "Quelles complications peuvent survenir avec la mastocytose cutanée ?\nLa mastocytose cutanée peut-elle évoluer vers une forme plus grave ?\nLes complications sont-elles fréquentes ?\nComment gérer les complications ?\nLes complications affectent-elles la qualité de vie ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-complications"
},
{
"@type": "MedicalWebPage",
"name": "Facteurs de risque",
"headline": "Facteurs de risque sur Mastocytose cutanée",
"description": "Quels sont les facteurs de risque de la mastocytose cutanée ?\nL'âge joue-t-il un rôle dans la mastocytose cutanée ?\nLes femmes sont-elles plus touchées que les hommes ?\nLes maladies auto-immunes augmentent-elles le risque ?\nL'exposition à des produits chimiques est-elle un facteur ?",
"url": "https://questionsmedicales.fr/mesh/D034701?mesh_terms=Conversion+Disorder&page=3#section-facteurs de risque"
}
]
},
{
"@type": "FAQPage",
"mainEntity": [
{
"@type": "Question",
"name": "Comment diagnostique-t-on la mastocytose cutanée ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le diagnostic repose sur l'examen clinique et la biopsie cutanée pour détecter les mastocytes."
}
},
{
"@type": "Question",
"name": "Quels tests sont utilisés pour confirmer la mastocytose ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des tests sanguins pour mesurer les niveaux de tryptase peuvent être effectués."
}
},
{
"@type": "Question",
"name": "Les symptômes sont-ils suffisants pour le diagnostic ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les symptômes doivent être corroborés par des examens histologiques."
}
},
{
"@type": "Question",
"name": "La mastocytose cutanée est-elle confondue avec d'autres maladies ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, elle peut être confondue avec d'autres affections cutanées comme l'urticaire."
}
},
{
"@type": "Question",
"name": "Quel rôle joue l'historique médical dans le diagnostic ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'historique médical aide à identifier des antécédents d'allergies ou d'autres maladies liées."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes courants de la mastocytose cutanée ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent des démangeaisons, des rougeurs et des lésions cutanées."
}
},
{
"@type": "Question",
"name": "La mastocytose cutanée provoque-t-elle des douleurs ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Elle peut provoquer des douleurs localisées, surtout en cas de lésions étendues."
}
},
{
"@type": "Question",
"name": "Les symptômes varient-ils d'une personne à l'autre ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'intensité et la nature des symptômes peuvent varier considérablement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes systémiques associés ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des symptômes systémiques comme des nausées peuvent survenir dans certains cas."
}
},
{
"@type": "Question",
"name": "Les lésions cutanées sont-elles contagieuses ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les lésions cutanées de la mastocytose ne sont pas contagieuses."
}
},
{
"@type": "Question",
"name": "Peut-on prévenir la mastocytose cutanée ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de méthode de prévention spécifique pour la mastocytose cutanée."
}
},
{
"@type": "Question",
"name": "Les allergènes peuvent-ils aggraver la condition ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'exposition à certains allergènes peut aggraver les symptômes."
}
},
{
"@type": "Question",
"name": "Faut-il éviter certains médicaments ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains médicaments peuvent déclencher des réactions chez les patients sensibles."
}
},
{
"@type": "Question",
"name": "L'évitement du stress aide-t-il ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Gérer le stress peut aider à réduire les poussées de symptômes chez certains patients."
}
},
{
"@type": "Question",
"name": "Les soins de la peau sont-ils importants ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des soins appropriés de la peau peuvent aider à minimiser les irritations."
}
},
{
"@type": "Question",
"name": "Quels traitements sont disponibles pour la mastocytose cutanée ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les traitements incluent des antihistaminiques et des corticostéroïdes topiques."
}
},
{
"@type": "Question",
"name": "Les antihistaminiques sont-ils efficaces ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils aident à réduire les démangeaisons et les rougeurs."
}
},
{
"@type": "Question",
"name": "La photothérapie est-elle une option de traitement ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la photothérapie peut être utilisée pour traiter les lésions cutanées."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils permanents ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les traitements visent à gérer les symptômes, pas à guérir la maladie."
}
},
{
"@type": "Question",
"name": "Des traitements alternatifs existent-ils ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines personnes explorent des traitements alternatifs, mais leur efficacité n'est pas prouvée."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec la mastocytose cutanée ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des complications comme des infections cutanées peuvent survenir en raison de lésions."
}
},
{
"@type": "Question",
"name": "La mastocytose cutanée peut-elle évoluer vers une forme plus grave ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Dans de rares cas, elle peut évoluer vers une mastocytose systémique."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles fréquentes ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications ne sont pas fréquentes mais peuvent survenir chez certains patients."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion des complications nécessite souvent une consultation spécialisée."
}
},
{
"@type": "Question",
"name": "Les complications affectent-elles la qualité de vie ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les complications peuvent affecter la qualité de vie en raison de l'inconfort."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque de la mastocytose cutanée ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux et des allergies cutanées."
}
},
{
"@type": "Question",
"name": "L'âge joue-t-il un rôle dans la mastocytose cutanée ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la mastocytose cutanée est plus fréquente chez les enfants et les jeunes adultes."
}
},
{
"@type": "Question",
"name": "Les femmes sont-elles plus touchées que les hommes ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, la mastocytose cutanée affecte les hommes et les femmes de manière égale."
}
},
{
"@type": "Question",
"name": "Les maladies auto-immunes augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines maladies auto-immunes peuvent augmenter le risque de mastocytose."
}
},
{
"@type": "Question",
"name": "L'exposition à des produits chimiques est-elle un facteur ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'exposition à certains produits chimiques peut être un facteur de risque."
}
}
]
}
]
}
After more than twenty years of academic research on functional neurological disorders (FND) throughout the world, a standardized care management strategy has emerged to allow a more adapted care offe...
Functional neurological disorder (FND) is a common issue in the pediatric population. The concept and our understanding of functional neurological disorders have changed over the past years, and new e...
Functional neurological disorders (FNDs) are common but often misdiagnosed....
The incidence of FNDs is between 4 and 12 per 100,000, comparable to multiple sclerosis and amyotrophic lateral sclerosis, and it is the second most common diagnosis in neurology clinics. Some clues i...
A positive diagnosis of FNDs can be made on the basis of history and neurological signs without reliance on psychological stressors. Past sensitizing events and neurobiological abnormalities contribut...
In vivo magnetic resonance spectroscopy (MRS) was used to investigate neurometabolic homeostasis in children with functional neurological disorder (FND) in three regions of interest: supplementary mot...
MRS data were acquired for 32 children with mixed FND (25 girls, 7 boys, aged 10.00 to 16.08 years) and 41 healthy controls of similar age using both short echo point-resolved spectroscopy (PRESS) and...
In the SMA, children with FND had lower NAA/Cr, mI/Cr (trend level), and GABA/Cr ratios. In the aDMN, no group differences in metabolite ratios were found. In the pDMN, children with FND had lower NAA...
Our findings of multiple differences in neurometabolites in children with FND suggest dysfunction on multiple levels of the biological system: the neuron (lower NAA), the glial cell (lower mI), and in...
Functional neurological disorder (FND), formerly called conversion disorder, is a condition characterized by neurological symptoms that lack an identifiable organic purpose. These signs, which can con...
Functional Gait Disorders (FGD) are a common presentation of motor-Functional Neurological Disorders (motor-FND) that affect walking ability....
To provide a narrative review of the current literature on FGD....
A narrative overview of published literature was undertaken, based on a systematic search of relevant databases, authoritative texts and citation tracking....
FGD is multidimensional and disabling, with numerous phenotypes described in the literature, including 'knee buckling,' 'astasia-abasia' and 'excessive slowness.' Motor symptoms such as weakness or tr...
The relative contribution of motor and non-motor symptoms in FGD remains unknown, but it is likely that non-motor symptoms increase the illness burden and should be considered during assessment and tr...
To date, there have been no reviews bringing together evidence on the clinical management of functional neurological disorder (FND) and patients', caregivers', and healthcare workers' experiences. Thi...
Four databases were searched, and a consultation exercise was conducted to retrieve relevant records dated from September 2010 to September 2020. Articles documenting diagnostic methods, treatments or...
In total, 2756 records were retrieved, with 162 included in this review. The diagnostic methods reported predominantly included positive clinical signs, v-EEG and EEG. Psychological treatments and med...
The literature describing the clinical management for FND has increased considerably in recent times. A wide variety of diagnostic tools and treatments and interventions were found, with more focus be...
Acute health events, including infections, can trigger the onset of functional neurological disorder (FND). It was hypothesized that a proportion of people with long COVID might be experiencing functi...
A systematic review of studies containing original data on long COVID was performed. The frequency and characteristics of neurological symptoms were reviewed, looking for positive evidence suggesting ...
In all, 102 studies were included in our narrative synthesis. The most consistently reported neurological symptoms were cognitive difficulties, headaches, pain, dizziness, fatigue, sleep-related sympt...
Neurological symptoms are prevalent in long COVID, but poorly characterized. The similarities between some manifestations of long COVID and functional disorders triggered by acute illnesses are striki...
Functional neurological disorder (FND) is characterized by neurological symptoms that cannot be explained by a structural neurological cause. Among the different aetiological models that have been pro...
To report incidence, demographic and clinical characteristics, and symptom outcome of functional neurological disorder (FND) in children....
Children diagnosed with FND at a regional children's hospital were prospectively recruited by weekly active surveillance for 36 months. Demographic, clinical, and follow-up data were retrospectively e...
Ninety-seven children (age range 5-15 years) met the case definition of FND (annual incidence 18.3 per 100 000 children). Children with FND were likely to be female (n = 68 [70%]) and older (median 13...
At this regional centre, FND in children had a higher incidence than previously reported and a less optimistic outcome than in some other studies....