questionsmedicales.fr
Maladies du système immunitaire
Troubles de l'activation mastocytaire
Mastocytose
Mastocytose cutanée
Mastocytose cutanée : Questions médicales fréquentes
Termes MeSH sélectionnés :
REM Sleep Behavior Disorder
Diagnostic
5
Mastocytose
Biopsie cutanée
Urticaire
Affections cutanées
Antécédents médicaux
Allergies
Symptômes
5
Démangeaisons
Lésions cutanées
Variabilité des symptômes
Individus
Symptômes systémiques
Nausées
Lésions cutanées
Contagiosité
Prévention
5
Stress
Poussées de symptômes
Soins de la peau
Irritations
Traitements
5
Antihistaminiques
Corticostéroïdes
Antihistaminiques
Démangeaisons
Photothérapie
Lésions cutanées
Gestion des symptômes
Traitements
Traitements alternatifs
Efficacité
Complications
5
Complications
Infections cutanées
Mastocytose systémique
Évolution
Gestion
Consultation spécialisée
Facteurs de risque
5
Facteurs de risque
Antécédents familiaux
Maladies auto-immunes
Risque
Produits chimiques
Exposition
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"text": "Le diagnostic repose sur l'examen clinique et la biopsie cutanée pour détecter les mastocytes."
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"@type": "Question",
"name": "Quels tests sont utilisés pour confirmer la mastocytose ?",
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"@type": "Question",
"name": "La mastocytose cutanée provoque-t-elle des douleurs ?",
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}
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"@type": "Question",
"name": "Les symptômes varient-ils d'une personne à l'autre ?",
"position": 8,
"acceptedAnswer": {
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"text": "Oui, l'intensité et la nature des symptômes peuvent varier considérablement."
}
},
{
"@type": "Question",
"name": "Y a-t-il des symptômes systémiques associés ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des symptômes systémiques comme des nausées peuvent survenir dans certains cas."
}
},
{
"@type": "Question",
"name": "Les lésions cutanées sont-elles contagieuses ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les lésions cutanées de la mastocytose ne sont pas contagieuses."
}
},
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"@type": "Question",
"name": "Peut-on prévenir la mastocytose cutanée ?",
"position": 11,
"acceptedAnswer": {
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"@type": "Question",
"name": "Les allergènes peuvent-ils aggraver la condition ?",
"position": 12,
"acceptedAnswer": {
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"text": "Oui, l'exposition à certains allergènes peut aggraver les symptômes."
}
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{
"@type": "Question",
"name": "Faut-il éviter certains médicaments ?",
"position": 13,
"acceptedAnswer": {
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"text": "Oui, certains médicaments peuvent déclencher des réactions chez les patients sensibles."
}
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{
"@type": "Question",
"name": "L'évitement du stress aide-t-il ?",
"position": 14,
"acceptedAnswer": {
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"text": "Gérer le stress peut aider à réduire les poussées de symptômes chez certains patients."
}
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{
"@type": "Question",
"name": "Les soins de la peau sont-ils importants ?",
"position": 15,
"acceptedAnswer": {
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},
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"name": "Quels traitements sont disponibles pour la mastocytose cutanée ?",
"position": 16,
"acceptedAnswer": {
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"text": "Les traitements incluent des antihistaminiques et des corticostéroïdes topiques."
}
},
{
"@type": "Question",
"name": "Les antihistaminiques sont-ils efficaces ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils aident à réduire les démangeaisons et les rougeurs."
}
},
{
"@type": "Question",
"name": "La photothérapie est-elle une option de traitement ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la photothérapie peut être utilisée pour traiter les lésions cutanées."
}
},
{
"@type": "Question",
"name": "Les traitements sont-ils permanents ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, les traitements visent à gérer les symptômes, pas à guérir la maladie."
}
},
{
"@type": "Question",
"name": "Des traitements alternatifs existent-ils ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines personnes explorent des traitements alternatifs, mais leur efficacité n'est pas prouvée."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir avec la mastocytose cutanée ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des complications comme des infections cutanées peuvent survenir en raison de lésions."
}
},
{
"@type": "Question",
"name": "La mastocytose cutanée peut-elle évoluer vers une forme plus grave ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Dans de rares cas, elle peut évoluer vers une mastocytose systémique."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles fréquentes ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications ne sont pas fréquentes mais peuvent survenir chez certains patients."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion des complications nécessite souvent une consultation spécialisée."
}
},
{
"@type": "Question",
"name": "Les complications affectent-elles la qualité de vie ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les complications peuvent affecter la qualité de vie en raison de l'inconfort."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque de la mastocytose cutanée ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs incluent des antécédents familiaux et des allergies cutanées."
}
},
{
"@type": "Question",
"name": "L'âge joue-t-il un rôle dans la mastocytose cutanée ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la mastocytose cutanée est plus fréquente chez les enfants et les jeunes adultes."
}
},
{
"@type": "Question",
"name": "Les femmes sont-elles plus touchées que les hommes ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Non, la mastocytose cutanée affecte les hommes et les femmes de manière égale."
}
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{
"@type": "Question",
"name": "Les maladies auto-immunes augmentent-elles le risque ?",
"position": 29,
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"text": "Oui, certaines maladies auto-immunes peuvent augmenter le risque de mastocytose."
}
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"@type": "Question",
"name": "L'exposition à des produits chimiques est-elle un facteur ?",
"position": 30,
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"text": "Oui, l'exposition à certains produits chimiques peut être un facteur de risque."
}
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Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 01/05/2025
Contenu vérifié selon les dernières recommandations médicales
9 publications dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland.
6 publications dans cette catégorie
Affiliations :
Allergologische Poliklinik, Klinik für Dermatologie, Universitätsspital Basel, Petersgraben 4, 4031, Basel, Schweiz. karin.hartmann@usb.ch.
5 publications dans cette catégorie
Affiliations :
Department of Dermatology and Allergy Biederstein, School of Medicine and Health, Technical University of Munich, 80802 Munich, Germany.
Department of Dermatology and Allergy Centre, Odense University Hospital, 5000 Odense, Denmark.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Dermatology, Venereology and Allergology, Medical University of Gdańsk, 80-211 Gdańsk, Poland.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology and Mastocytosis Expert Centre (CEREMAST), Necker Children's Hospital and Paris Descartes University, Assistance Publique Hôpitaux de Paris, Paris, France. Electronic address: ohermine@gmail.com.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology Oncology, Fondazione IRCCS Policlinico San Matteo, University of Pavia, Pavia, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Allergology, Medical University of Gdansk, Gdansk, Poland.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Section of Hematology, Department of Medicine, Verona University Hospital, Verona, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Allergy Unit, Verona University Hospital, Verona, Italy.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Division of Hematology, Department of Medicine, Stanford University School of Medicine, Stanford, California, USA.
Publications dans "Mastocytose cutanée" :
5 publications dans cette catégorie
Affiliations :
Department of Hematology and Oncology, University Hospital Mannheim, Heidelberg University, Mannheim, Germany.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Internal Medicine I, Division of Hematology & Hemostaseology, Medical University of Vienna, Vienna, Austria; Ludwig Boltzmann Institute for Hematology and Oncology, Medical University of Vienna, Vienna, Austria; Internal Medicine Small Animals, University Clinic for Small Animals, Department/University Clinic for Companion Animals and Horses, University of Veterinary Medicine, Vienna, Austria.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Division of Allergy and Clinical Immunology, University of Salerno, Salerno, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Pediatric Dermatology Unit, Department of Medicine, University of Padova, Padova, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Pediatric Dermatology Unit, Department of Medicine, University of Padova, Padova, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
University Hospital and Faculty of Medicine, Brno, Czechia.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Faculty of Medicine and Health Sciences, Department of Immunology-Allergology-Rheumatology, University of Antwerp and Antwerp University Hospital, Antwerpen, Belgium.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Division of Allergy and Clinical Immunology, University of Salerno, Salerno, Italy.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Hematology, University Medical Center Groningen, University of Groningen, Groningen, The Netherlands.
Publications dans "Mastocytose cutanée" :
4 publications dans cette catégorie
Affiliations :
Department of Oncology, Haematology, Haemostaseology and Stem Cell Transplantation, University Hospital RWTH Aachen, Aachen, Germany; Center for Integrated Oncology, Aachen Bonn Cologne Düsseldorf (CIO ABCD), Aachen, Germany.
Publications dans "Mastocytose cutanée" :
The present study aims to examine whether declarative memory dysfunction relates to impaired core memory mechanisms or attentional and executive dysfunction in idiopathic REM Sleep Behavior Disorder (...
In this observational, cross-sectional study, were enrolled 82 individuals with the diagnosis of iRBD according to the International Classification of Sleep Disorders and 49-matched healthy controls f...
We used Bayesian multivariate generalized linear model analysis to evaluate the effect of iRBD on memory performance controlled for effects of age and sex. Individuals with iRBD displayed worse memory...
In iRBD, we replicated findings of reduced free recall based on inefficient retrieval (retrieval deficit), which was small in terms of effect size. Importantly, the memory profile across measures does...
Rapid eye movement (REM) sleep behavior disorder is characterized by dream enactment during REM sleep. Due to different treatment requirements, it is important to distinguish REM sleep behavior disord...
It has been suggested that the loss of nigrostriatal dopaminergic axon terminals occurs before the loss of dopaminergic neurons in the substantia nigra (SN) in Parkinson's disease (PD). This study aim...
Free water values in the DPP, dorsoanterior putamen (DAP), and posterior SN were compared between the healthy controls (n = 48), iRBD (n = 43) and PD (n = 47) patients. In iRBD patients, the relations...
Free water values were significantly higher in the DPP and posterior substantia nigra (pSN), but not in the DAP, in the iRBD and PD groups than in controls. In iRBD patients, free water values in the ...
This study demonstrates that free water values in the DPP are increased cross-sectionally and longitudinally and associated with clinical manifestations and the function of the dopaminergic system in ...
Traumatic brain injury is associated with the late development of neurodegenerative diseases such as the synucleinopathies. Isolated REM sleep behavior disorder (IRBD) constitutes an early manifestati...
Prior exposure to concussions was evaluated by interviewing polysomnographically-confirmed IRBD patients and controls without IRBD, and by the BRAIN-Q questionnaire....
We recruited 199 IRBD patients aged 73.2 ± 7.7 years and 168 age and sex matched controls. Previous history of concussion was more common in patients than in controls (21.1% versus 10.1%, p = 0.004). ...
Previous history of concussion is common in IRBD. Our observations may suggest that in individuals with increased susceptibility, early-life concussions may trigger a slow neurodegenerative process le...
Synucleinopathies-related disorders such as Lewy body dementia (LBD) and isolated/idiopathic REM sleep behavior disorder (iRBD) have been associated with neuroinflammation. In this study, we examined ...
REM sleep behavior disorder (RBD) is a parasomnia with dream enactment and presence of REM sleep without atonia (RSWA). RBD diagnosed manually via polysomnography (PSG) scoring, which is time intensiv...
Idiopathic/isolated REM sleep behavior disorder (iRBD) has been strongly linked to neurodegenerative synucleinopathies such as Parkinson disease, dementia with Lewy bodies, and multiple system atrophy...
Participants were enrolled in the North American Prodromal Synucleinopathy cohort with polysomnography-confirmed iRBD, free of parkinsonism and dementia. Plasma samples were systematically screened fo...
Of 339 samples analyzed, 3 participants (0.9%) had confirmed positive IGLON5 autoantibodies in the cell-based assay, which were confirmed by the tissue-based assay. An additional participant was posit...
Our finding that nearly 1% of a large iRBD cohort may have a serious but potentially treatable autoantibody syndrome has important clinical implications. In particular, it raises the question of wheth...
NCT03623672....
To investigate the risk factors for REM sleep behavior disorder (RBD) in a case-control study....
Participants with probable RBD (pRBD) were defined using the RBD Questionnaire-Hong Kong (RBDQ-HK). Controls were collected by matching age and sex. Demographic information, lifestyle, comorbidity, pr...
A total of 278 pRBD participants (age = 58.31 ± 15.82 years) and 556 controls (age = 58.16 ± 15.84 years) were enrolled in this study. Patients with pRBD were more likely to be current alcohol drinker...
We determined several risk factors for pRBD in this case-control study. Future studies are needed to understand the mechanism underlying the association between these factors and pRBD....
Periodic limb movement disorder (PLMD) is a condition in which patients experience frequent periodic limb movements of sleep (PLMS). Synchronized arousal responses cause sleep fragmentation, resulting...
Isolated Rapid Eye Movement Sleep (REM) behaviour disorder (iRBD) is a prodromal sign of neurodegenerative disorders. Empirical findings point to a role of non-REM (NREM) sleep alterations in neurodeg...