Tumeur du glomus tympanique : Questions médicales fréquentes
Nom anglais: Glomus Tympanicum Tumor
Descriptor UI:D043604
Tree Number:C04.557.580.625.650.700.705.360
Termes MeSH sélectionnés :
Ear Neoplasms
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"headline": "Diagnostic sur Tumeur du glomus tympanique",
"description": "Comment diagnostique-t-on une tumeur du glomus tympanique ?\nQuels examens sont nécessaires pour confirmer la tumeur ?\nQuels signes cliniques indiquent une tumeur du glomus tympanique ?\nLa biopsie est-elle nécessaire pour le diagnostic ?\nQuels spécialistes sont impliqués dans le diagnostic ?",
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"description": "Quels sont les symptômes courants de cette tumeur ?\nLa douleur est-elle un symptôme fréquent ?\nPeut-on avoir des symptômes sans perte auditive ?\nLes symptômes peuvent-ils varier d'un patient à l'autre ?\nLes symptômes s'aggravent-ils avec le temps ?",
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"description": "Peut-on prévenir la tumeur du glomus tympanique ?\nLes facteurs environnementaux jouent-ils un rôle ?\nDes examens réguliers peuvent-ils aider ?\nLes antécédents familiaux influencent-ils le risque ?\nL'exposition au bruit peut-elle être un facteur ?",
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"description": "Quel est le traitement principal pour cette tumeur ?\nLa radiothérapie est-elle utilisée ?\nY a-t-il des traitements médicamenteux disponibles ?\nQuels sont les risques associés à la chirurgie ?\nLe suivi post-opératoire est-il nécessaire ?",
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"description": "Quelles complications peuvent survenir après traitement ?\nLa récidive de la tumeur est-elle possible ?\nDes problèmes d'équilibre peuvent-ils survenir ?\nLes complications sont-elles fréquentes ?\nComment gérer les complications auditives ?",
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"headline": "Facteurs de risque sur Tumeur du glomus tympanique",
"description": "Quels sont les facteurs de risque connus ?\nL'âge influence-t-il le risque de développer cette tumeur ?\nLes femmes sont-elles plus à risque que les hommes ?\nDes maladies préexistantes augmentent-elles le risque ?\nL'exposition à des produits chimiques est-elle un facteur ?",
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"@type": "Question",
"name": "Comment diagnostique-t-on une tumeur du glomus tympanique ?",
"position": 1,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le diagnostic repose sur l'examen clinique, l'audiométrie et l'imagerie (IRM ou scanner)."
}
},
{
"@type": "Question",
"name": "Quels examens sont nécessaires pour confirmer la tumeur ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Une otoscopie et une imagerie avancée comme l'IRM sont essentielles pour confirmer la tumeur."
}
},
{
"@type": "Question",
"name": "Quels signes cliniques indiquent une tumeur du glomus tympanique ?",
"position": 3,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les signes incluent des acouphènes, une perte auditive et parfois des douleurs auriculaires."
}
},
{
"@type": "Question",
"name": "La biopsie est-elle nécessaire pour le diagnostic ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "La biopsie n'est généralement pas nécessaire, le diagnostic se fait par imagerie et symptômes."
}
},
{
"@type": "Question",
"name": "Quels spécialistes sont impliqués dans le diagnostic ?",
"position": 5,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les oto-rhino-laryngologistes (ORL) sont les principaux spécialistes pour le diagnostic."
}
},
{
"@type": "Question",
"name": "Quels sont les symptômes courants de cette tumeur ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent acouphènes, perte auditive, et parfois des vertiges."
}
},
{
"@type": "Question",
"name": "La douleur est-elle un symptôme fréquent ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "La douleur n'est pas fréquente, mais elle peut survenir dans certains cas avancés."
}
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{
"@type": "Question",
"name": "Peut-on avoir des symptômes sans perte auditive ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certains patients peuvent présenter des acouphènes sans perte auditive significative."
}
},
{
"@type": "Question",
"name": "Les symptômes peuvent-ils varier d'un patient à l'autre ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, l'intensité et la combinaison des symptômes peuvent varier selon les individus."
}
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{
"@type": "Question",
"name": "Les symptômes s'aggravent-ils avec le temps ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, sans traitement, les symptômes peuvent s'aggraver progressivement."
}
},
{
"@type": "Question",
"name": "Peut-on prévenir la tumeur du glomus tympanique ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de mesures préventives spécifiques pour cette tumeur."
}
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{
"@type": "Question",
"name": "Les facteurs environnementaux jouent-ils un rôle ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs environnementaux ne sont pas clairement établis comme causes de cette tumeur."
}
},
{
"@type": "Question",
"name": "Des examens réguliers peuvent-ils aider ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Des examens réguliers chez un ORL peuvent aider à détecter des problèmes précocement."
}
},
{
"@type": "Question",
"name": "Les antécédents familiaux influencent-ils le risque ?",
"position": 14,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'y a pas de preuve solide que les antécédents familiaux augmentent le risque."
}
},
{
"@type": "Question",
"name": "L'exposition au bruit peut-elle être un facteur ?",
"position": 15,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'exposition au bruit n'est pas directement liée à l'apparition de cette tumeur."
}
},
{
"@type": "Question",
"name": "Quel est le traitement principal pour cette tumeur ?",
"position": 16,
"acceptedAnswer": {
"@type": "Answer",
"text": "Le traitement principal est la chirurgie pour retirer la tumeur, souvent avec succès."
}
},
{
"@type": "Question",
"name": "La radiothérapie est-elle utilisée ?",
"position": 17,
"acceptedAnswer": {
"@type": "Answer",
"text": "La radiothérapie n'est pas couramment utilisée, la chirurgie est le traitement de choix."
}
},
{
"@type": "Question",
"name": "Y a-t-il des traitements médicamenteux disponibles ?",
"position": 18,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'existe pas de traitements médicamenteux spécifiques pour cette tumeur."
}
},
{
"@type": "Question",
"name": "Quels sont les risques associés à la chirurgie ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les risques incluent des saignements, des infections et des complications auditives."
}
},
{
"@type": "Question",
"name": "Le suivi post-opératoire est-il nécessaire ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un suivi régulier est essentiel pour surveiller d'éventuelles récidives."
}
},
{
"@type": "Question",
"name": "Quelles complications peuvent survenir après traitement ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des troubles auditifs, des infections et des vertiges persistants."
}
},
{
"@type": "Question",
"name": "La récidive de la tumeur est-elle possible ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la récidive est possible, surtout si la tumeur n'est pas complètement retirée."
}
},
{
"@type": "Question",
"name": "Des problèmes d'équilibre peuvent-ils survenir ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes d'équilibre peuvent survenir en raison de l'atteinte des structures de l'oreille."
}
},
{
"@type": "Question",
"name": "Les complications sont-elles fréquentes ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications ne sont pas fréquentes mais peuvent survenir, nécessitant un suivi."
}
},
{
"@type": "Question",
"name": "Comment gérer les complications auditives ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications auditives peuvent être gérées par des appareils auditifs ou des thérapies."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque connus ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les facteurs de risque incluent des antécédents familiaux et des expositions environnementales."
}
},
{
"@type": "Question",
"name": "L'âge influence-t-il le risque de développer cette tumeur ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, cette tumeur est plus fréquente chez les adultes, généralement entre 30 et 60 ans."
}
},
{
"@type": "Question",
"name": "Les femmes sont-elles plus à risque que les hommes ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Il n'y a pas de preuve claire que le sexe influence le risque de cette tumeur."
}
},
{
"@type": "Question",
"name": "Des maladies préexistantes augmentent-elles le risque ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Certaines maladies vasculaires peuvent augmenter le risque, mais ce n'est pas systématique."
}
},
{
"@type": "Question",
"name": "L'exposition à des produits chimiques est-elle un facteur ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "L'exposition à certains produits chimiques peut être un facteur, mais les preuves sont limitées."
}
}
]
}
]
}
Cutaneous squamous cell carcinoma (cSCC) of the ear is associated with poor outcomes. No studies have evaluated current staging system performance in this specific location....
Describe clinicopathologic characteristics and outcomes of ear cSCC and evaluate the performance of current staging systems....
Retrospective study including cases diagnosed and treated at a cancer center from January 2000 to December 2014. Demographic, clinical, and pathologic data were collected from clinical records. Biopsy...
Of 125 patients, the mean age at diagnosis was 71.9 years (SD 12.5), with most men (89.6%, n = 112). Median follow-up was 22.3 months. Local recurrence and survival risk factors were similar to cSCC o...
Current staging systems perform well at stratifying risk in ear cSCC....
The external ear is a crucial part of the ear's anatomy for both functional and aesthetic purposes. We present a defect after the extirpation of an invasive squamous cell carcinoma, where the final de...
Paragangliomas in the central nervous system account for 0.6% of all head and neck neoplasms, with glomus tympanicum being the most common middle ear tumor. Carcinoid tumors are neuroendocrine tumors,...
A 70-year-old female with a history of left temporal lobe tumor underwent unsuccessful resection due to intraoperative bleeding at an outside institution. However, biopsy prior to aborting the case le...
Carcinoid tumors of the middle ear constitute a differential diagnosis for patients presenting with temporal lobe hemorrhage. A combination of immunohistochemical staining with electron microscopy can...
Microsecretory adenocarcinoma (MSA) of the salivary gland is a new entity recently added to the World Health Organization Classification of Head and Neck Tumors. This tumor is characterized by a recur...
Fibroepithelial polyps are rare benign lesions with uncertain origins. They are commonly found in the skin and genitourinary system. Fibroepithelial polyps in the external auditory canal are infrequen...
We report a 60-year-old Persian woman with an incidentally discovered painless fibroepithelial polyp in the right external auditory canal. Microscopic transcanal surgery confirmed the diagnosis after ...
Fibroepithelial polyps have an uncertain etiology and are typically asymptomatic. Surgical resection is the preferred treatment, and the prognosis following resection is generally favorable, with low ...
This case highlights the rarity of fibroepithelial polyps in the external auditory canal and underscores the importance of considering them in the differential diagnosis of external auditory canal les...
Although adenoid cystic carcinoma (ACC) of the external auditory canal (EAC) has a different pathophysiology from squamous cell carcinoma, the same staging system is used. The aim of this study was to...
A total of 25 patients who were diagnosed with ACC of the EAC were reviewed. The modified Pittsburgh staging system (mPSS) that is universally used for temporal bone malignancy was refined for ACC (rP...
When staging using mPSS, most patients (96.0%, n = 24) were classified as T4. However, when rPSS was used, T1, T2, T3, and T4 stage occupied 36.0% (n = 9), 40.0% (n = 10), 12.0% (n = 3), 12.0% (n = 3)...
Clinical T stage of mPSS was not sufficient to predict survival rate in ACC of the EAC, and we propose that the information on the lateral soft tissue involvement needs to be added to the existing sta...
Endolymphatic sac tumors are rare neoplasms originating in the endolymphatic sac. Current literature is limited to case reports and small case series. The objective of this study was to systematically...
PubMed, Embase, and Cochrane Library....
A systematic review was performed following Preferred Reporting Items for Systematic Reviews and Meta-Analyses guidelines describing human endolymphatic sac tumors. Risk of bias was assessed using a v...
A total of 82 studies met inclusion criteria, and 253 discrete tumors were analyzed. A total of 23.4% of patients had von Hippel-Lindau disease. Von Hippel-Lindau-associated tumors affected females to...
Endolymphatic sac tumors require a high degree of suspicion for early diagnosis. Complete resection is the standard of care. No strong evidence supports routine use of adjuvant radiation therapy. Give...
T4-classified squamous cell carcinoma (SCC) of external auditory canal (EAC) can potentially involve different anatomical structures, which could translate into different treatment strategies and surv...
Retrospective data, including patients with primary operated cT4-classified EAC SCC, was obtained from 12 international hospitals. We subclassified according to the T4-subclasses. The treatment strate...
A total of 130 T4-classified EAC SCC were included. We found commonly used treatment strategies per subclass according to Lavieille and the DFS seems also to differ per subclass. Subclass according to...
Our study suggests that the subclass according Lavieille might have added value in clinical practice to improve care of T4-classified EAC SCC....
Middle ear tumors are diverse, but relatively uncommon. The most frequent tumor in the middle ear is glomus tumor, followed by others such as schwannoma and cholesteatoma. We experienced a case of Muc...
This study aimed to investigate the survival outcomes and potential prognostic factors of patients with temporal bone squamous cell carcinoma (TBSCC) treated at our institution....
We retrospectively included patients who were diagnosed with TBSCC between 2008 and 2019. The Kaplan-Meier (KM) method was used to describe overall survival (OS), and the association between baseline ...
Fifty consecutive patients with TBSCC were included in this study. The results showed that patients with advanced modified Pittsburgh (MPB)- T classifications had a poorer prognosis (T3 vs. T1-2: HR: ...
MESCC and advanced MPB-T classifications might be considered predictors of unfavorable outcomes in patients with TBSCC, indicating that special attention should be paid to the original tumor subsite a...