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Tétrapyrroles
Tétrapyrroles : Questions médicales fréquentes
Termes MeSH sélectionnés :
Diagnostic
5
Porphyries
Tests de laboratoire
Porphyries
Analyse d'urine
Tests génétiques
Porphyries
Antécédents médicaux
Évaluation clinique
Symptômes
5
Neuropathies
Troubles mentaux
Troubles digestifs
Symptômes
Photosensibilité
Éruptions cutanées
Prévention
5
Dépistage
Antécédents familiaux
Éducation des patients
Gestion des symptômes
Suivi médical
Traitements
Traitements
5
Suppléments de fer
Anémie
Gestion du stress
Qualité de vie
Complications
5
Troubles psychologiques
Anxiété
Foie
Dysfonctionnement hépatique
Complications cardiovasculaires
Anémie
Infections
Système immunitaire
Facteurs de risque
5
Facteurs de risque
Antécédents familiaux
Maladies hépatiques
Facteurs de risque
Infections
Facteurs de risque
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"name": "Comment diagnostiquer une carence en tétrapyrroles ?",
"position": 1,
"acceptedAnswer": {
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"text": "Un diagnostic se fait par des tests sanguins mesurant les niveaux de porphyrines."
}
},
{
"@type": "Question",
"name": "Quels examens sont utilisés pour évaluer les tétrapyrroles ?",
"position": 2,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les tests de porphyrines urinaires et sanguines sont couramment utilisés."
}
},
{
"@type": "Question",
"name": "Quels symptômes indiquent un déséquilibre des tétrapyrroles ?",
"position": 3,
"acceptedAnswer": {
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"text": "Des douleurs abdominales, des troubles neurologiques et des photosensibilités peuvent survenir."
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"@type": "Question",
"name": "Les tests génétiques sont-ils utiles pour les tétrapyrroles ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent identifier des mutations liées aux troubles des tétrapyrroles."
}
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"@type": "Question",
"name": "Quelle est l'importance de l'historique médical dans le diagnostic ?",
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"@type": "Question",
"name": "Quels sont les symptômes courants des troubles des tétrapyrroles ?",
"position": 6,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les symptômes incluent douleurs abdominales, éruptions cutanées et fatigue."
}
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"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le système nerveux ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des neuropathies, des crises et des troubles mentaux."
}
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"@type": "Question",
"name": "Les troubles digestifs sont-ils liés aux tétrapyrroles ?",
"position": 8,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des douleurs abdominales et des nausées sont fréquentes dans ces troubles."
}
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"@type": "Question",
"name": "La photosensibilité est-elle un symptôme des tétrapyrroles ?",
"position": 9,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, la photosensibilité est un symptôme courant, provoquant des éruptions cutanées."
}
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"@type": "Question",
"name": "Les symptômes varient-ils selon le type de tétrapyrroles ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les symptômes peuvent varier selon le type de porphyrie et sa gravité."
}
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"@type": "Question",
"name": "Comment prévenir les crises liées aux tétrapyrroles ?",
"position": 11,
"acceptedAnswer": {
"@type": "Answer",
"text": "Éviter les déclencheurs connus, comme certains médicaments et l'alcool, aide à prévenir."
}
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{
"@type": "Question",
"name": "Les tests de dépistage sont-ils recommandés ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le dépistage peut être utile pour les personnes à risque ou avec des antécédents familiaux."
}
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"@type": "Question",
"name": "L'éducation des patients est-elle importante ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, comprendre la maladie aide les patients à gérer leurs symptômes et à éviter les crises."
}
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"@type": "Question",
"name": "Les vaccinations sont-elles nécessaires pour ces patients ?",
"position": 14,
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"text": "Oui, les vaccinations peuvent prévenir des infections qui aggravent les symptômes."
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"text": "Ils peuvent être nécessaires en cas d'anémie, mais doivent être prescrits par un médecin."
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"name": "Comment la gestion du stress aide-t-elle les patients ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion du stress peut réduire les crises et améliorer la qualité de vie."
}
},
{
"@type": "Question",
"name": "Les changements alimentaires sont-ils bénéfiques ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un régime équilibré peut aider à gérer les symptômes et améliorer la santé."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles des tétrapyrroles ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des lésions nerveuses, des problèmes hépatiques et des anémies."
}
},
{
"@type": "Question",
"name": "Les troubles psychologiques sont-ils des complications ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles comme l'anxiété et la dépression peuvent survenir chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le foie ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des lésions hépatiques, entraînant des douleurs et des dysfonctionnements."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles possibles ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes cardiovasculaires peuvent survenir en raison de l'anémie et du stress."
}
},
{
"@type": "Question",
"name": "Les infections sont-elles une complication fréquente ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les infections peuvent survenir, surtout si le système immunitaire est affaibli."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque des troubles des tétrapyrroles ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les antécédents familiaux, l'exposition à des toxines et certains médicaments augmentent le risque."
}
},
{
"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle dans les tétrapyrroles ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation pauvre en nutriments essentiels peut augmenter le risque de troubles."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les maladies hépatiques préexistantes peuvent exacerber les troubles des tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Le stress peut-il aggraver les symptômes ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress est un facteur déclenchant connu pour les crises liées aux tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Les infections antérieures influencent-elles le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent déclencher ou aggraver les troubles des tétrapyrroles."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 19/04/2025
Contenu vérifié selon les dernières recommandations médicales
6 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
5 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
4 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
4 publications dans cette catégorie
Affiliations :
Department of Chemistry and Biochemistry, Brown Laboratory, University of Delaware, Newark, DE 19716, USA. joelr@udel.edu.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Chair of Technical Electrochemistry, Department of Chemistry and Catalysis Research Center, Technische Universität München (TUM), 85748, Garching, Germany.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Bundesanstalt für Materialforschung und -prüfung (BAM), 12203, Berlin, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Max-Planck-Institut für Molekulare Pflanzenphysiologie, Am Mühlenberg 1, D-14476, Potsdam-Golm, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, University of California, Riverside, CA 92521-0403, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Washington University, St. Louis, MO 63130-4889, USA. holten@wustl.edu.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, University of California, Riverside, CA 92521-0403, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Washington University, St. Louis, MO 63130-4889, USA. holten@wustl.edu.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Plant and Microbial Biology, North Carolina State University, Raleigh, NC 27695-7612, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Graduate School of Arts and Sciences, The University of Tokyo, 3-8-1 Komaba, Meguro-ku, Tokyo 153-8902, Japan.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Graduate School of Arts and Sciences, The University of Tokyo, 3-8-1 Komaba, Meguro-ku, Tokyo 153-8902, Japan.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13 (Haus 12), 10115 Berlin, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Humboldt-Universität zu Berlin, Institute of Biology/Plant Physiology, Philippstraße 13, Building 12,, D-10115, Berlin, Germany.
Publications dans "Tétrapyrroles" :
Brain metastases (BMs) in patients with extra-pulmonary neuroendocrine neoplasms (EP-NENs) are rare, and limited clinical information is available. The aim of this study was to detail the clinicopatho...
A retrospective single-centre analysis of consecutive patients with EP-NENs (August 2004-February 2020) was conducted. Median overall survival (OS)/survival from BMs diagnosis was estimated (Kaplan-Me...
Of 730 patients, 17 (1.9%) had BMs, median age 61 years (range 15-77); 8 (53%) male, unknown primary NEN site: 40%. Patients with BMs had grade 3 (G3) EP-NENs 11 (73%), G2: 3 (20%), G1: 1 (7%). Eight ...
BMs in patients with EP-NENs are rare and of increased risk in G3 vs. G1 + G2 EP-NENs. Survival outcomes are poor, and a greater understanding is needed to improve therapeutic outcomes....
Postradiation treatment necrosis is one of the most serious late sequelae and appears within 6 months. The magnetic resonance spectroscopy imaging (MRSI) has been used for the detection of brain tumor...
The research was performed in accordance with the preferred reporting items for systematic review and meta-analysis guidelines. International electronic databases including 15 English sources were inv...
Nine studies were enrolled in the meta-analysis with a total of 354 patients (203 male and 151 female) whose average age ranged from 4 to 74 years. Anbarloui et al., Elias et al., Nemattalla et al., S...
MR spectroscopy is effective in distinguishing recurrent brain tumors from necrosis. Our meta-analysis revealed that Cho/NAA, Cho/Cr, and NAA/Cr ratios were significantly better predictor of detected ...
Neurosurgeons often face this dilemma. Brain neoplasm patients undergoing neurosurgery are at a high risk of venous thrombosis. However, antithrombotic drugs may induce bleeding complications. Therefo...
Despite advances in endoscopic techniques for management of benign colonic neoplasms, a rise in rates of surgical treatment has been reported. We used a nationally representative cohort to characteriz...
All patients undergoing elective partial colectomy for benign or malignant colonic neoplasms were identified using the 2012-2019 National Inpatient Sample. Those presenting with inflammatory bowel dis...
Of 569,280 colectomy procedures included for analysis, 153,435 (27.0%) were performed for benign lesions. The proportion of Benign operations decreased from 28.6% in 2012 to 23.7% in 2019 (P for trend...
The present national study identifies a decrease in colectomy for benign polyps from 2012-2019. Future investigations should identify patients who would most benefit from surgical resection and addres...
Differentiating tumefactive demyelinating lesions (TDL) from neoplasms of the central nervous system continues to be a diagnostic dilemma in many cases....
Our study aimed to examine and contrast the clinical and radiological characteristics of TDL, high-grade gliomas (HGG) and primary CNS lymphoma (CNSL)....
This was a retrospective review of 66 patients (23 TDL, 31 HGG and 12 CNSL). Clinical and laboratory data were obtained. MRI brain at presentation were analyzed by two independent, blinded neuroradiol...
Patients with TDLs were younger and predominantly female. Sensorimotor deficits and ataxia were more common amongst TDL whereas headaches and altered mental status were associated with HGG and CNSL. C...
Careful evaluation of clinical and radiological features helps in differentiating TDLs at first presentation from CNS neoplasms....
The aim of the study was to investigate the concentration and activity of tissue factor (TF) and Tissue factor pathway inhibitor (TFPI) as well as the concentration of thrombin-antithrombin (TAT) comp...
Pediatric benign laryngeal tumors can often be treated as same-day surgeries. This study identified factors associated with prolonged hospital stay in children undergoing laryngeal surgery for benign ...
A retrospective analysis of records of pediatric patients who underwent laryngeal surgery with a post-op diagnosis of benign tumor was performed with the American College of Surgeons Pediatric Nationa...
1775 patients were identified with a mean age at time of surgery of 8.95 years (95% CI 8.76-9.14). 966 (54.4%) were males and 809 (45.6%) were females. Mean LOS was 0.22 days (95% CI 0.12-0.32). Only ...
This study suggests that laryngeal surgery for benign tumors is safe but recognizes that patients with comorbidities or young children may require a prolonged stay. Awareness of these implications may...
Preoperative anxiety is common among patients, particularly in neurosurgical patients. The aim of the study was to evaluate the incidence and predictive factors of preoperative anxiety using the state...
Sixty patients aged 18 to 65 years with American Society of Anesthesiologists physical status score I/II scheduled for elective craniotomy for a supratentorial neoplasm were recruited into this prospe...
Sixty percent of patients had preoperative anxiety (STAI-S ≥37). An APAIS score of 10 identified preoperative anxiety with a sensitivity, specificity, and positive predictive value of 97%, 96%, and 97...
Patients with supratentorial neoplasms have a high incidence of preoperative anxiety; an APAIS score of 10 is the optimal cutoff to identify anxious patients in the preoperative period. Need-for-infor...
During the V Siena Immuno-Oncology (IO) Think Tank meeting in 2021, conditions were discussed which favor immunotherapy responses in either primary or secondary brain malignancies. Core elements of th...
Gliomas are malignant tumors in the central nervous system. Cuproptosis is a newly discovered cell death mechanism targeting lipoylated tricarboxylic acid cycle proteins. Previous studies have found t...