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Tétrapyrroles
Tétrapyrroles : Questions médicales fréquentes
Termes MeSH sélectionnés :
Ventricular Function, Left
Diagnostic
5
Porphyries
Tests de laboratoire
Porphyries
Analyse d'urine
Tests génétiques
Porphyries
Antécédents médicaux
Évaluation clinique
Symptômes
5
Neuropathies
Troubles mentaux
Troubles digestifs
Symptômes
Photosensibilité
Éruptions cutanées
Prévention
5
Dépistage
Antécédents familiaux
Éducation des patients
Gestion des symptômes
Suivi médical
Traitements
Traitements
5
Suppléments de fer
Anémie
Gestion du stress
Qualité de vie
Complications
5
Troubles psychologiques
Anxiété
Foie
Dysfonctionnement hépatique
Complications cardiovasculaires
Anémie
Infections
Système immunitaire
Facteurs de risque
5
Facteurs de risque
Antécédents familiaux
Maladies hépatiques
Facteurs de risque
Infections
Facteurs de risque
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"@type": "Question",
"name": "Comment diagnostiquer une carence en tétrapyrroles ?",
"position": 1,
"acceptedAnswer": {
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"text": "Un diagnostic se fait par des tests sanguins mesurant les niveaux de porphyrines."
}
},
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"@type": "Question",
"name": "Quels examens sont utilisés pour évaluer les tétrapyrroles ?",
"position": 2,
"acceptedAnswer": {
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"text": "Les tests de porphyrines urinaires et sanguines sont couramment utilisés."
}
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"@type": "Question",
"name": "Quels symptômes indiquent un déséquilibre des tétrapyrroles ?",
"position": 3,
"acceptedAnswer": {
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"text": "Des douleurs abdominales, des troubles neurologiques et des photosensibilités peuvent survenir."
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"name": "Les tests génétiques sont-ils utiles pour les tétrapyrroles ?",
"position": 4,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, ils peuvent identifier des mutations liées aux troubles des tétrapyrroles."
}
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"@type": "Question",
"name": "Quelle est l'importance de l'historique médical dans le diagnostic ?",
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"@type": "Question",
"name": "Quels sont les symptômes courants des troubles des tétrapyrroles ?",
"position": 6,
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"text": "Les symptômes incluent douleurs abdominales, éruptions cutanées et fatigue."
}
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"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le système nerveux ?",
"position": 7,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des neuropathies, des crises et des troubles mentaux."
}
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"@type": "Question",
"name": "Les troubles digestifs sont-ils liés aux tétrapyrroles ?",
"position": 8,
"acceptedAnswer": {
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"text": "Oui, des douleurs abdominales et des nausées sont fréquentes dans ces troubles."
}
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"@type": "Question",
"name": "La photosensibilité est-elle un symptôme des tétrapyrroles ?",
"position": 9,
"acceptedAnswer": {
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"text": "Oui, la photosensibilité est un symptôme courant, provoquant des éruptions cutanées."
}
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"@type": "Question",
"name": "Les symptômes varient-ils selon le type de tétrapyrroles ?",
"position": 10,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les symptômes peuvent varier selon le type de porphyrie et sa gravité."
}
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"@type": "Question",
"name": "Comment prévenir les crises liées aux tétrapyrroles ?",
"position": 11,
"acceptedAnswer": {
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"text": "Éviter les déclencheurs connus, comme certains médicaments et l'alcool, aide à prévenir."
}
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"@type": "Question",
"name": "Les tests de dépistage sont-ils recommandés ?",
"position": 12,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le dépistage peut être utile pour les personnes à risque ou avec des antécédents familiaux."
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"@type": "Question",
"name": "L'éducation des patients est-elle importante ?",
"position": 13,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, comprendre la maladie aide les patients à gérer leurs symptômes et à éviter les crises."
}
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"@type": "Question",
"name": "Les vaccinations sont-elles nécessaires pour ces patients ?",
"position": 14,
"acceptedAnswer": {
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"text": "Oui, les vaccinations peuvent prévenir des infections qui aggravent les symptômes."
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"text": "Ils peuvent être nécessaires en cas d'anémie, mais doivent être prescrits par un médecin."
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"name": "Comment la gestion du stress aide-t-elle les patients ?",
"position": 19,
"acceptedAnswer": {
"@type": "Answer",
"text": "La gestion du stress peut réduire les crises et améliorer la qualité de vie."
}
},
{
"@type": "Question",
"name": "Les changements alimentaires sont-ils bénéfiques ?",
"position": 20,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, un régime équilibré peut aider à gérer les symptômes et améliorer la santé."
}
},
{
"@type": "Question",
"name": "Quelles sont les complications possibles des tétrapyrroles ?",
"position": 21,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les complications incluent des lésions nerveuses, des problèmes hépatiques et des anémies."
}
},
{
"@type": "Question",
"name": "Les troubles psychologiques sont-ils des complications ?",
"position": 22,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des troubles comme l'anxiété et la dépression peuvent survenir chez ces patients."
}
},
{
"@type": "Question",
"name": "Comment les tétrapyrroles affectent-ils le foie ?",
"position": 23,
"acceptedAnswer": {
"@type": "Answer",
"text": "Ils peuvent provoquer des lésions hépatiques, entraînant des douleurs et des dysfonctionnements."
}
},
{
"@type": "Question",
"name": "Les complications cardiovasculaires sont-elles possibles ?",
"position": 24,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, des problèmes cardiovasculaires peuvent survenir en raison de l'anémie et du stress."
}
},
{
"@type": "Question",
"name": "Les infections sont-elles une complication fréquente ?",
"position": 25,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les infections peuvent survenir, surtout si le système immunitaire est affaibli."
}
},
{
"@type": "Question",
"name": "Quels sont les facteurs de risque des troubles des tétrapyrroles ?",
"position": 26,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les antécédents familiaux, l'exposition à des toxines et certains médicaments augmentent le risque."
}
},
{
"@type": "Question",
"name": "L'alimentation joue-t-elle un rôle dans les tétrapyrroles ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, une alimentation pauvre en nutriments essentiels peut augmenter le risque de troubles."
}
},
{
"@type": "Question",
"name": "Les maladies hépatiques sont-elles un facteur de risque ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, les maladies hépatiques préexistantes peuvent exacerber les troubles des tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Le stress peut-il aggraver les symptômes ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress est un facteur déclenchant connu pour les crises liées aux tétrapyrroles."
}
},
{
"@type": "Question",
"name": "Les infections antérieures influencent-elles le risque ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections peuvent déclencher ou aggraver les troubles des tétrapyrroles."
}
}
]
}
]
}
Expert en Médecine, Optimisation des Parcours de Soins et Révision Médicale
Validation scientifique effectuée le 19/04/2025
Contenu vérifié selon les dernières recommandations médicales
6 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
5 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
4 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
4 publications dans cette catégorie
Affiliations :
Department of Chemistry and Biochemistry, Brown Laboratory, University of Delaware, Newark, DE 19716, USA. joelr@udel.edu.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Chair of Technical Electrochemistry, Department of Chemistry and Catalysis Research Center, Technische Universität München (TUM), 85748, Garching, Germany.
Publications dans "Tétrapyrroles" :
3 publications dans cette catégorie
Affiliations :
Bundesanstalt für Materialforschung und -prüfung (BAM), 12203, Berlin, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13, Berlin, 10115, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Max-Planck-Institut für Molekulare Pflanzenphysiologie, Am Mühlenberg 1, D-14476, Potsdam-Golm, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, University of California, Riverside, CA 92521-0403, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Washington University, St. Louis, MO 63130-4889, USA. holten@wustl.edu.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, University of California, Riverside, CA 92521-0403, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, Washington University, St. Louis, MO 63130-4889, USA. holten@wustl.edu.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Chemistry, North Carolina State University, Raleigh, NC 27695-8204, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Department of Plant and Microbial Biology, North Carolina State University, Raleigh, NC 27695-7612, USA.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Graduate School of Arts and Sciences, The University of Tokyo, 3-8-1 Komaba, Meguro-ku, Tokyo 153-8902, Japan.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Graduate School of Arts and Sciences, The University of Tokyo, 3-8-1 Komaba, Meguro-ku, Tokyo 153-8902, Japan.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Institute of Biology/Plant Physiology, Humboldt-Universität zu Berlin, Philippstraße 13 (Haus 12), 10115 Berlin, Germany.
Publications dans "Tétrapyrroles" :
2 publications dans cette catégorie
Affiliations :
Humboldt-Universität zu Berlin, Institute of Biology/Plant Physiology, Philippstraße 13, Building 12,, D-10115, Berlin, Germany.
Publications dans "Tétrapyrroles" :
Heart failure (HF) is often categorized by left ventricular (LV) ejection fraction (LVEF). A new category of HF characterized by supra-normal LVEF (>65%), named HF with supra-normal ejection fraction ...
Ventricular arrhythmia (VA) commonly originate from the left ventricular summit (LVS) and results in left ventricular (LV) dysfunction in some patients; however, factors related to LV cardiomyopathy h...
Between 2013 and 2018, a total of 139 patients (60.7% men; mean age 53.2 ± 13.9 years old) underwent catheter ablation for LVS VA in two centers. Detailed patient demographics, electrocardiograms, ele...
Acute procedural success was achieved in 92.8% of patients. There were 40 patients (28.8%) with LV cardiomyopathy, and the mean LVEF improved from 37.5 ± 9.3% to 48.5 ± 10.2% after ablation (p < .001)...
In patients with VA from the LVS, PVC QRSd and AEAD are factors associated with deteriorating LV systolic function. Catheter ablation can reverse LV remodeling. Narrower QRSd and better LVEF are assoc...
Ascending aortic dilatation is a common clinical issue. In the present study, we aimed to evaluate the relationship between ascending aortic diameter with left ventricular (LV) and left atrial (LA) fu...
A total of 127 healthy participants with normal LV systolic function took part in the study. Echocardiographic measurements were obtained from each subject....
The mean age of the participants was 43 ± 14.1 years and 76 (59.8%) were female. The mean aortic diameter of the participants was 32.2 ± 4.7 mm. A negative correlation was found between aortic diamete...
A strong correlation between ascending aortic diameter with LV and LA functions, and LVMI in individuals with normal LV systolic function....
Positron emission tomography (PET) myocardial perfusion imaging (MPI) can be used to evaluate left ventricular (LV) volumes and function. We performed a head-to-head comparison of LV function and volu...
In this prospective study, 51 patients underwent [...
LVEF and LV wall motion can be accurately assessed using [...
CZT-SPECT has good agreement in the evaluation of mechanical synchronization compared with conventional SPECT. The aim of this study was to evaluate the correlation between left ventricular mechanical...
This retrospective study involved 371 patients (239 males and 132 females, mean age 61.06 ± 11.78 years old) who underwent GMPI at the Nuclear Medicine Department of Shanxi Cardiovascular Hospital fro...
PP, PSD, PHB, HS and HK were significantly different among the four groups (F = 5.20, 188.72, 202.88, 171.05, 101.36, P < 0.001). Pairwise comparison tests showed significant differences in PSD and PH...
CZT SPECT GMPI provided left ventricular mechanical contraction synchrony parameters that correlated well with left ventricular systolic function. Worse left ventricular mechanical contraction synchro...
Left ventricle myocardium has a complex micro-architecture, which was revealed to consist of myocyte bundles arranged in a series of laminar sheetlets. Recent imaging studies demonstrated that these s...
The perioperative quantification of left and right ventricular function is cornerstone to provide optimal patient care. Echocardiography has emerged as the most important cardiac imaging modality in t...
Myocardial contractility is poorly defined and difficult to compare between studies. Contractance or myocardial active strain energy density (MASED) measures the mechanical work done per unit volume (...
Data obtained from three previously published experimental studies using trabecular tissue was used to provide contemporaneous nominal stress and strain data in 18 different scenarios with different l...
We showed that calculating MASED was feasible and provided a measure of energy production (work done) per unit volume of myocardium during contraction. The new term for contractile function, contracta...
The right ventricle (RV) in hypertrophic cardiomyopathy (HCM) tends to be neglected, as previous efforts have predominantly focused on examining the prognostic value of left ventricular (LV) abnormali...
Two hundred and ninety HCM patients with preserved LV ejection fraction (LVEF ≥ 55%) and 30 age- and sex-matched controls underwent cardiovascular magnetic resonance (CMR). All patients were followed ...
When compared to controls, HCM patients exhibited lower RV and LV peak global longitudinal systolic strains on feature-tracking analysis of cine images, while RVEF and LVEF were within the normal rang...
In HCM, RV function, including RV strain, and LV strain decrease over time despite preserved LVEF. Reduction in RV but not LV function is associated with adverse cardiovascular outcomes. Assessing RV ...
Atrial fibrillation (AF) is the most common sustained arrhythmia in humans. The onset of the arrhythmia can significantly impair cardiac function. This hemodynamic deterioration has been explained by ...
Twelve patients undergoing catheter ablation for paroxysmal AF were paced simultaneously from the proximal coronary sinus and the His bundle region according to prescribed sequences of irregular R-R i...
Simulated AF led to significant impairment of left ventricular systolic and diastolic function. Both loss of atrial contraction and heart rate irregularity significantly contributed to hemodynamic imp...
Our findings strengthen the rationale for therapeutic strategies aiming at rhythm control and heart rate regularization in patients with AF....