Étant une maladie génétique, il n'existe pas de méthode de prévention connue.
PréventionMaladies génétiques
#2
Comment gérer les symptômes au quotidien ?
L'utilisation régulière d'émollients et l'évitement des irritants cutanés peuvent aider.
ÉmollientsIrritants cutanés
#3
Y a-t-il des conseils pour la peau ?
Il est conseillé de garder la peau hydratée et de protéger les zones affectées du soleil.
Hydratation de la peauProtection solaire
#4
Les soins de la peau sont-ils importants ?
Oui, des soins appropriés peuvent réduire l'inconfort et améliorer l'apparence de la peau.
Soins de la peauConfort cutané
#5
Les patients doivent-ils éviter certains aliments ?
Il n'y a pas de régime spécifique, mais une alimentation équilibrée peut soutenir la santé globale.
Alimentation équilibréeSanté globale
Traitements
5
#1
Quels traitements sont disponibles ?
Les traitements incluent des émollients, des corticostéroïdes topiques et des thérapies systémiques.
CorticostéroïdesThérapies systémiques
#2
Les traitements sont-ils efficaces ?
Les traitements peuvent aider à soulager les symptômes, mais il n'existe pas de cure définitive.
Efficacité des traitementsSymptomatique
#3
Des traitements alternatifs existent-ils ?
Des thérapies comme la photothérapie peuvent être envisagées pour certains patients.
PhotothérapieThérapies alternatives
#4
Les traitements nécessitent-ils un suivi médical ?
Oui, un suivi régulier est essentiel pour ajuster les traitements et surveiller les effets secondaires.
Suivi médicalEffets secondaires
#5
Y a-t-il des effets secondaires aux traitements ?
Oui, certains traitements peuvent entraîner des effets secondaires comme l'amincissement de la peau.
Effets indésirablesDermatologie
Complications
5
#1
Quelles complications peuvent survenir ?
Des infections cutanées peuvent survenir en raison de la peau endommagée et des lésions.
Infections cutanéesComplications
#2
L'érythrokératodermie variabilis augmente-t-elle le risque de cancer ?
Il n'y a pas de preuve claire que cette maladie augmente le risque de cancer de la peau.
Cancer de la peauRisque
#3
Les complications affectent-elles la qualité de vie ?
Oui, les symptômes et les complications peuvent avoir un impact significatif sur la qualité de vie.
Qualité de vieImpact
#4
Des complications psychologiques peuvent-elles survenir ?
Oui, l'impact esthétique et les démangeaisons peuvent entraîner des problèmes psychologiques.
Santé mentaleProblèmes psychologiques
#5
Les complications nécessitent-elles une intervention médicale ?
Oui, certaines complications peuvent nécessiter des soins médicaux supplémentaires pour être gérées.
Intervention médicaleGestion des complications
Facteurs de risque
5
#1
Quels sont les facteurs de risque connus ?
Les antécédents familiaux de la maladie sont le principal facteur de risque identifié.
Antécédents familiauxFacteurs de risque
#2
L'environnement joue-t-il un rôle ?
Bien que l'environnement ne soit pas un facteur direct, des irritants peuvent aggraver les symptômes.
EnvironnementIrritants
#3
Les infections peuvent-elles déclencher des symptômes ?
Oui, certaines infections cutanées peuvent exacerber les symptômes de la maladie.
InfectionsExacerbation des symptômes
#4
Le stress influence-t-il la maladie ?
Oui, le stress peut aggraver les symptômes et provoquer des poussées cutanées.
StressPoussées cutanées
#5
Y a-t-il des groupes à risque spécifique ?
Les personnes ayant des antécédents familiaux sont plus susceptibles de développer la maladie.
Groupes à risqueHérédité
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"position": 20,
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"@type": "Question",
"name": "Quelles complications peuvent survenir ?",
"position": 21,
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"@type": "Answer",
"text": "Des infections cutanées peuvent survenir en raison de la peau endommagée et des lésions."
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"position": 22,
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"position": 23,
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"name": "Des complications psychologiques peuvent-elles survenir ?",
"position": 24,
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}
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"name": "Les complications nécessitent-elles une intervention médicale ?",
"position": 25,
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"name": "Quels sont les facteurs de risque connus ?",
"position": 26,
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"text": "Les antécédents familiaux de la maladie sont le principal facteur de risque identifié."
}
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"@type": "Question",
"name": "L'environnement joue-t-il un rôle ?",
"position": 27,
"acceptedAnswer": {
"@type": "Answer",
"text": "Bien que l'environnement ne soit pas un facteur direct, des irritants peuvent aggraver les symptômes."
}
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"@type": "Question",
"name": "Les infections peuvent-elles déclencher des symptômes ?",
"position": 28,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, certaines infections cutanées peuvent exacerber les symptômes de la maladie."
}
},
{
"@type": "Question",
"name": "Le stress influence-t-il la maladie ?",
"position": 29,
"acceptedAnswer": {
"@type": "Answer",
"text": "Oui, le stress peut aggraver les symptômes et provoquer des poussées cutanées."
}
},
{
"@type": "Question",
"name": "Y a-t-il des groupes à risque spécifique ?",
"position": 30,
"acceptedAnswer": {
"@type": "Answer",
"text": "Les personnes ayant des antécédents familiaux sont plus susceptibles de développer la maladie."
}
}
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Protist Research Team, Microbial Research Department, Nakdonggang National Institute of Biological Resources, Sangju, 37242, Republic of Korea. Electronic address: cslee@nnibr.re.kr.
Publications dans "Érythrokératodermie variabilis" :
State Key Laboratory of Tree Genetics and Breeding, Chinese Academy of Forestry, Beijing, 100091, China; Research Institute of Forestry, Chinese Academy of Forestry, Beijing, 100091, China. Electronic address: jiazirui646@163.com.
Publications dans "Érythrokératodermie variabilis" :
Key Laboratory of Silviculture and Conservation of the Ministry of Education, College of Forestry, Beijing Forestry University, Beijing, 100083, China; Research Center of Deciduous Oaks, Beijing Forestry University, Beijing, 100083, China; Research Center for Efficient Cultivation and Innovation of Deciduous Oaks of State Forestry and Grassland Administration, Beijing Forestry University, Beijing, 100083, China. Electronic address: glli226@bjfu.edu.cn.
Publications dans "Érythrokératodermie variabilis" :
School of Agriculture and Biology, Shanghai Jiao Tong University, Shanghai 200240, China; School of Design, Shanghai Jiao Tong University, Shanghai 200240, China. Electronic address: kanghz@sjtu.edu.cn.
Publications dans "Érythrokératodermie variabilis" :
School of Agriculture and Biology, Shanghai Jiao Tong University, Shanghai 200240, China; Shanghai Urban Forest Ecosystem Research Station, State Forestry Administration, Shanghai 200240, China; Shanghai Yangtze River Delta Eco-environmental Change and Management Observation and Research Station, Ministry of Science and Technology, Shanghai 200240, China. Electronic address: chjliu@sjtu.edu.cn.
Publications dans "Érythrokératodermie variabilis" :
This observational-descriptive time and motion study was conducted to determine how heavy home care nurses' workload is and how they allocate their work time to home healthcare. It was carried out in ...
Nurses in psychiatric inpatient care spend less time than desired with patients and investigation of the nature of nursing in this setting is needed. This study explores how nursing activities in psyc...
Efficient planning of the oral health workforce in Primary Health Care (PHC) is paramount to ensure equitable community access to services. This requires a meticulous examination of the population's n...
Calculate the average time parameters for the activities carried out by the oral health team in primary health care....
This is a descriptive observational study using the time-motion method carried out in five Primary Health Care Units in the city of São Paulo, SP, Brazil. Direct and continuous observation of oral hea...
A total of 696.05 h of observation were conducted with 12 Dentists, three Oral Health Assistants, and five Oral Health Technicians. The Dentists' main activity was consultation with an average duratio...
The study establishes time standards for the activities performed by the dental care team and provides support for the application of workforce planning methods that allow for review and optimization ...
The aim of this study was to determine how much time nurses spend on direct and indirect patient care in acute and subacute hospital settings....
Quantifying direct and indirect nursing care provided during inpatient stay is vital to optimise the quality of care and manage resources....
Time and motion cross-sectional observational study and reported the study according to the STROBE guideline....
Nurses working in an acute or subacute medical wards of a single health service participated. Nurses were observed twice for 2 h on the same day with an observer break in between sessions. Real-time t...
Twenty-one nurses (acute n = 12, subacute n = 9) were observed during shifts between 7 AM and 9 PM in May-July 2021. A total of 7240 tasks were recorded. Nurses spent a third of their time on direct p...
Time spent on tasks was similar regardless of the setting and was consistent with previous research. We found differences in the distribution of tasks throughout the day between settings, which could ...
This time-motion study explored the amount of time clinicians spent on wound assessments in a real-world environment using wound assessment digital application utilizing Artificial Intelligence (AI) v...
Clinicians practicing at Valley Wound Center who agreed to join the study were asked to record the time needed to complete wound assessment activities for patients with active wounds referred for a ro...
A total of 91 patients with 115 wounds were assessed. The average time to capture and access wound image with the AI digital tool was significantly faster than a standard digital camera with an averag...
Using the digital assessment tool saved significant time for clinicians in assessing wounds. It also successfully captured quality wound images at the first attempt....
School-based health (SBH) programmes that are contingent on primary school teachers are options to increase access to malaria treatment among learners. However, perceptions that provision of healthcar...
A time and motion study was conducted in 10 primary schools in rural Malawi. Teachers who had been trained to diagnose and treat uncomplicated malaria were continuously observed in real time during sc...
Seventy-four teachers, trained to use LTK, were observed. Their mean age and years of teaching experience were 34.7 and 8.7, respectively. Overall, 739.8 h of teacher observations took place. The aver...
School-based health (SBH) programmes are not detrimental to teaching activities. Teachers manage their time to ensure additional time required for SBH services is not at the expense of teaching duties...
Community health workers (CHWs) are essential field-based personnel and increasingly used to deliver priority interventions to achieve universal health coverage. Existing literature allude to the pote...
A time and motion study was conducted in 7 health facilities in Malawi. Data was collected at baseline between October-July 2019, and 12 months after CCSPT implementation between July and August 2021....
Thirty-seven (n = 37) CHWs were observed. Their mean age and years of experience were 42 and 17, respectively. Overall, CHWs were observed for 323 hours (inter quartile range: 2.8-5.5). Compared with ...
Introduction of CCSPT was not very detrimental to pre-existing community services. CHWs managed their time ensuring additional efforts required for CCSPT were not at the expense of essential activitie...
Ageing populations and care workforce shortages across Europe are causing challenges for care services for older people. Therefore, it is paramount that limited care resources are allocated optimally,...
Cross-sectional observational study design with data from time and motion study, registers, and surveys was used. In total, 1477 home care clients and 1538 residents from assisted living facilities wi...
Physical functioning was the strongest predictor of received care time in both care settings. In home care, greater pain, more unstable health, and higher team autonomy were associated with increased ...
Physical functioning was the main driver of received care time. Interventions that maintain or improve physical functioning can help restrain the growing need of care resources, although it is importa...
The aim of the present study was to determine the time-motion structure of high-level taekwondo matches during the Tokyo 2020 Olympic Games in relation to sex, match outcome, weight category and match...
Overall, 7007 actions were recorded during the analysis of 134 performances (67 rounds of 24 matches: four rounds of 16, eight quarterfinals, eight semifinals and four finals) in male and female flywe...
The AT/ST ratio was ~1:1.5. Male athletes performed significantly longer (P<0.001) sum PT than female athletes. Flyweight athletes differed significantly from their heavyweight counterparts by having ...
The rule changes and the implementation of the electronic score recording system had a major impact on the time-motion structure of combat by generating a considerably higher AT/ST ratio than in the p...
Early childhood caries (ECC) is a major global health issue affecting millions of children. Mitigating this problem requires up-to-date information from reliable surveillance systems. This enables evi...
The DHIS2 Server was configured for the DHIS2 Tracker Android Capture App to allow individual-level data entry. The EOHSS indicators were selected in line with the WHO Action Plan 2030. Two modalities...
The pilot team reported positive feedback on the structure of the EOHSS. Workflow adaptations were made to prioritize surveillance tasks by collecting data from caregivers before acquiring clinical da...
The DHIS2 provides a feasible solution for developing electronic, oral health surveillance systems. The one-minute difference in data capture time in telemodality compared to face-to-face indicates th...