Titre : Érythrokératodermie variabilis

Érythrokératodermie variabilis : Questions médicales fréquentes

Termes MeSH sélectionnés :

Visual Fields
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?\nQuels signes cliniques indiquent cette maladie ?\nL'érythrokératodermie variabilis est-elle héréditaire ?\nPeut-on confondre cette maladie avec d'autres ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Érythrokératodermie variabilis", "description": "Quels sont les principaux symptômes ?\nLes symptômes varient d'une personne à l'autre ?\nY a-t-il des symptômes associés ?\nLes symptômes s'aggravent-ils avec le temps ?\nLes symptômes peuvent-ils être déclenchés par des facteurs externes ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Érythrokératodermie variabilis", "description": "Peut-on prévenir l'érythrokératodermie variabilis ?\nComment gérer les symptômes au quotidien ?\nY a-t-il des conseils pour la peau ?\nLes soins de la peau sont-ils importants ?\nLes patients doivent-ils éviter certains aliments ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Érythrokératodermie variabilis", "description": "Quels traitements sont disponibles ?\nLes traitements sont-ils efficaces ?\nDes traitements alternatifs existent-ils ?\nLes traitements nécessitent-ils un suivi médical ?\nY a-t-il des effets secondaires aux traitements ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Érythrokératodermie variabilis", "description": "Quelles complications peuvent survenir ?\nL'érythrokératodermie variabilis augmente-t-elle le risque de cancer ?\nLes complications affectent-elles la qualité de vie ?\nDes complications psychologiques peuvent-elles survenir ?\nLes complications nécessitent-elles une intervention médicale ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Érythrokératodermie variabilis", "description": "Quels sont les facteurs de risque connus ?\nL'environnement joue-t-il un rôle ?\nLes infections peuvent-elles déclencher des symptômes ?\nLe stress influence-t-il la maladie ?\nY a-t-il des groupes à risque spécifique ?", "url": "https://questionsmedicales.fr/mesh/D056266?mesh_terms=Visual+Fields&page=2#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostiquer l'érythrokératodermie variabilis ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Le diagnostic repose sur l'examen clinique et l'historique familial, parfois confirmé par une biopsie cutanée." } }, { "@type": "Question", "name": "Quels tests sont utilisés pour le diagnostic ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Des tests génétiques peuvent être effectués pour identifier des mutations spécifiques associées à la maladie." } }, { "@type": "Question", "name": "Quels signes cliniques indiquent cette maladie ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Des plaques rouges et squameuses sur la peau, souvent avec des zones de kératose, sont typiques." } }, { "@type": "Question", "name": "L'érythrokératodermie variabilis est-elle héréditaire ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elle est généralement transmise de manière autosomique dominante dans les familles." } }, { "@type": "Question", "name": "Peut-on confondre cette maladie avec d'autres ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elle peut être confondue avec d'autres dermatoses comme le psoriasis ou l'ichtyose." } }, { "@type": "Question", "name": "Quels sont les principaux symptômes ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent des plaques rouges, des démangeaisons et une peau squameuse." } }, { "@type": "Question", "name": "Les symptômes varient d'une personne à l'autre ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'intensité et l'étendue des symptômes peuvent varier considérablement entre les individus." } }, { "@type": "Question", "name": "Y a-t-il des symptômes associés ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Des anomalies des ongles et des cheveux peuvent également être observées chez certains patients." } }, { "@type": "Question", "name": "Les symptômes s'aggravent-ils avec le temps ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes peuvent fluctuer, mais ils ont tendance à persister tout au long de la vie." } }, { "@type": "Question", "name": "Les symptômes peuvent-ils être déclenchés par des facteurs externes ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des facteurs comme le stress, les infections ou les irritants cutanés peuvent aggraver les symptômes." } }, { "@type": "Question", "name": "Peut-on prévenir l'érythrokératodermie variabilis ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Étant une maladie génétique, il n'existe pas de méthode de prévention connue." } }, { "@type": "Question", "name": "Comment gérer les symptômes au quotidien ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "L'utilisation régulière d'émollients et l'évitement des irritants cutanés peuvent aider." } }, { "@type": "Question", "name": "Y a-t-il des conseils pour la peau ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Il est conseillé de garder la peau hydratée et de protéger les zones affectées du soleil." } }, { "@type": "Question", "name": "Les soins de la peau sont-ils importants ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des soins appropriés peuvent réduire l'inconfort et améliorer l'apparence de la peau." } }, { "@type": "Question", "name": "Les patients doivent-ils éviter certains aliments ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Il n'y a pas de régime spécifique, mais une alimentation équilibrée peut soutenir la santé globale." } }, { "@type": "Question", "name": "Quels traitements sont disponibles ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements incluent des émollients, des corticostéroïdes topiques et des thérapies systémiques." } }, { "@type": "Question", "name": "Les traitements sont-ils efficaces ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements peuvent aider à soulager les symptômes, mais il n'existe pas de cure définitive." } }, { "@type": "Question", "name": "Des traitements alternatifs existent-ils ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "Des thérapies comme la photothérapie peuvent être envisagées pour certains patients." } }, { "@type": "Question", "name": "Les traitements nécessitent-ils un suivi médical ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "Oui, un suivi régulier est essentiel pour ajuster les traitements et surveiller les effets secondaires." } }, { "@type": "Question", "name": "Y a-t-il des effets secondaires aux traitements ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains traitements peuvent entraîner des effets secondaires comme l'amincissement de la peau." } }, { "@type": "Question", "name": "Quelles complications peuvent survenir ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Des infections cutanées peuvent survenir en raison de la peau endommagée et des lésions." } }, { "@type": "Question", "name": "L'érythrokératodermie variabilis augmente-t-elle le risque de cancer ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Il n'y a pas de preuve claire que cette maladie augmente le risque de cancer de la peau." } }, { "@type": "Question", "name": "Les complications affectent-elles la qualité de vie ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les symptômes et les complications peuvent avoir un impact significatif sur la qualité de vie." } }, { "@type": "Question", "name": "Des complications psychologiques peuvent-elles survenir ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'impact esthétique et les démangeaisons peuvent entraîner des problèmes psychologiques." } }, { "@type": "Question", "name": "Les complications nécessitent-elles une intervention médicale ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certaines complications peuvent nécessiter des soins médicaux supplémentaires pour être gérées." } }, { "@type": "Question", "name": "Quels sont les facteurs de risque connus ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les antécédents familiaux de la maladie sont le principal facteur de risque identifié." } }, { "@type": "Question", "name": "L'environnement joue-t-il un rôle ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Bien que l'environnement ne soit pas un facteur direct, des irritants peuvent aggraver les symptômes." } }, { "@type": "Question", "name": "Les infections peuvent-elles déclencher des symptômes ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certaines infections cutanées peuvent exacerber les symptômes de la maladie." } }, { "@type": "Question", "name": "Le stress influence-t-il la maladie ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le stress peut aggraver les symptômes et provoquer des poussées cutanées." } }, { "@type": "Question", "name": "Y a-t-il des groupes à risque spécifique ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Les personnes ayant des antécédents familiaux sont plus susceptibles de développer la maladie." } } ] } ] }

Sources (10000 au total)

Humphrey visual field made easy for residents.

Visual field testing is an indispensable part of the assessment of glaucoma. Of paramount importance to both the practitioner and the perimetrist is the guidance on how to conduct the test to get the ... To simplify the basics of understanding single-field analysis of visual field tests by using the Humphrey perimeter.... The general principle and a brief overview of how the Humphrey visual field is conducted and the approach to interpreting the results of single field analysis in an easy-to-understand manner are prese... This educational video is an attempt to simplify the interpretation of Humphrey visual field single-field analysis with illustrations and video clips that would be useful to practicing ophthalmologist... https://youtu.be/x8iZLDR4XdY....

Foveal avascular zone vessel density is associated with visual field progression in early-stage glaucoma eyes with central visual field damage.

We investigated the relationship between foveal avascular zone (FAZ)-related parameters, assessed by optical coherence tomography angiography (OCT-A), and visual field (VF) progression in early-stage ...

Visual feedback in the lower visual field affects postural control during static standing.

The dorsal parietal visual system plays an important role in self-motion perception and spatial cognition. It also strongly responds to visual inputs from the lower visual field. Postural control is m... Do visual stimuli presented to the lower and upper visual fields affect postural control and sensory reweighting?... Twenty-nine healthy young adults participated in the study. Four conditions (full visual field, upper visual field, lower visual field, and no optic flow condition) were simulated in a VR environment ... Optic flow in the full and lower visual fields produced significantly smaller 95 % ellipse area and RMS of COP in the anterior-posterior direction compared to optic flow in the upper visual field. Furth... Visual feedback affects static postural control more when presented in the lower visual field compared to the upper visual field....

Five-Year Visual Field Outcomes of the HORIZON Trial.

To compare visual field (VF) progression between glaucoma patients receiving cataract surgery alone (CS) or with a Hydrus microstent (CS-HMS).... Post hoc analysis of VF data from the HORIZON multicenter randomized controlled trial.... A total of 556 patients with glaucoma and cataract were randomized 2:1 to either CS-HMS (369) or CS (187) and followed up for 5 years. VF was performed at 6 months and then every year after surgery. W... Data from 352 eyes in the CS-HMS arm and 165 in the CS arm were analyzed (2966 VFs). The mean RoP was -0.26 dB/y (95% credible interval -0.36, -0.16) for CS-HMS and -0.49 dB/y (95% credible interval -... CS-HMS has a significant effect on VF preservation in glaucoma patients compared with CS alone, reducing the proportion of fast progressors....

Effect of trabeculectomy on the rate of progression of visual field damage.

This study quantifies the effect of trabeculectomy on the rate of progression (RoP) of visual field (VF) damage utilising pre- and post-operative visual function as the outcome instead of surrogate ou... Clinical and VF data from 199 sequential patients who underwent trabeculectomy between 2015 and 2016 were extracted from the network of sites of Moorfields Eye Hospital NHS Foundation Trust. Of these,... We analysed 10 [9,12] VFs per subject (Median [Interquartile Range]). At surgery, the age was 67 [57, 72] years, mean deviation was -10.84 [-14.7, -5.6] dB and the IOP was 18 [15, 20] mmHg. One year a... Trabeculectomy leads to a significant reduction in the RoP of VF loss postoperatively....

A Consensus Statement on the Terminology for Automated Visual Field Abnormalities.

A multitude of terms have been used to describe automated visual field abnormalities. To date, there is no universally accepted system of definitions or guidelines. Variability among clinicians create... In phase one of the study, all neuro-ophthalmologists in Israel were asked to complete a survey in which they described the abnormalities in 10 selected automated visual field tests. In phase 2 of the... Twenty-six neuro-ophthalmologists participated in the initial survey. On average, there were 7.5 unique descriptions for each of the visual fields (SD 3.17), a description of only the location in 24.6... The study confirmed a great degree of variability in the use of terminology to describe automated visual field abnormalities. The creation of a consensus statement was associated with improved use of ...

Gaze tracker parameters have little association with visual field metrics of intrasession frontloaded SITA-Faster 24-2 visual field results.

To determine the usefulness of Humphrey Field Analyser (HFA) SITA-Faster 24-2 gaze tracker outputs on interpreting intra-visit visual field (VF) result pairs.... Analysis of 1380 right-left eye pairs and 1432 pairs of test 1-test 2 intrasession VF results of patients seen within a university-based glaucoma service was undertaken to understand gaze deviation di... There was no association of test order (right-left, test 1-test 2) with eye movements. There was a significant, but weak correlation between eye movements and age (r = 0.16). Correlations of eye movem... Eye movement parameters as currently reported by the HFA do not appear to be correlated with key sensitivity parameters when considering the repeatability of intrasession SITA-Faster 24-2 VF results. ...

Peripheral visual field loss and activities of daily living.

Peripheral visual field (VF) loss affects 13% of the population over 65. Its effect on activities of daily living and higher order visual processing is as important as it is inadequately understood. T... In this review, glaucoma and retrochiasmal cortical damage are utilized as examples of peripheral field loss which typically spare central vision and have patterns respecting the horizontal and vertic... Peripheral VF loss is an under-recognized cause of patient distress and disability. All peripheral field loss is not the same, differential patterns of loss affect parameters of activities of daily li...