Aortic Root Replacement and Berlin Heart EXCOR Implantation in Marfan Syndrome.
Journal
The Annals of thoracic surgery
ISSN: 1552-6259
Titre abrégé: Ann Thorac Surg
Pays: Netherlands
ID NLM: 15030100R
Informations de publication
Date de publication:
03 2019
03 2019
Historique:
received:
29
06
2018
revised:
17
07
2018
accepted:
22
07
2018
pubmed:
30
9
2018
medline:
12
11
2019
entrez:
30
9
2018
Statut:
ppublish
Résumé
Aortic regurgitation secondary to aortic aneurysmal disease with subsequent long-term volume overload of the left ventricle is associated with left ventricular dysfunction. In Marfan syndrome, ventricular dysfunction may exist independent of valvular disease (Marfan cardiomyopathy). We report of a 20-year-old Marfan syndrome patient presenting with severe aortic regurgitation and severe heart failure. Aortic surgery with concurrent biventricular paracorporeal assist device implantation was performed to bridge the patient to heart transplantation, which was performed successfully 21 weeks after aortic surgery. While the optimal strategy for this situation has not been described, the approach applied here appears a valid option.
Identifiants
pubmed: 30266613
pii: S0003-4975(18)31315-8
doi: 10.1016/j.athoracsur.2018.07.066
pii:
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
e187-e189Informations de copyright
Copyright © 2019 The Society of Thoracic Surgeons. Published by Elsevier Inc. All rights reserved.