Early intraventricular baclofen therapy (IVB) for children with dystonic and dysautonomic storm.


Journal

Child's nervous system : ChNS : official journal of the International Society for Pediatric Neurosurgery
ISSN: 1433-0350
Titre abrégé: Childs Nerv Syst
Pays: Germany
ID NLM: 8503227

Informations de publication

Date de publication:
01 2019
Historique:
received: 25 09 2018
accepted: 04 11 2018
pubmed: 13 11 2018
medline: 25 2 2020
entrez: 13 11 2018
Statut: ppublish

Résumé

Intrathecal baclofen (ITB) is an effective treatment for managing primary and secondary dystonia. Intraventricular baclofen (IVB) was first developed to allow treating patients in which the use of ITB was difficult due to anatomic anomalies. After that, several studies indicate that intraventricular administration of baclofen, is more effective than ITB in refractory dystonia. We report three cases of children with acute dystonic and dysautonomic storm, treated with IVB. The clinical outcome was satisfactory. The response to the treatment continued after the pump disconnection, suggesting that in this kind of cerebral dysregulations, short-term IVB is an effective treatment. Early treatment with IVB may be an effective option in patients with post-anoxic dysautonomic and dystonic storm.

Identifiants

pubmed: 30417210
doi: 10.1007/s00381-018-4002-8
pii: 10.1007/s00381-018-4002-8
doi:

Substances chimiques

Muscle Relaxants, Central 0
Baclofen H789N3FKE8

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

15-18

Références

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Auteurs

Claudio Ruggiero (C)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy.

Giulia Meccariello (G)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy.

Pietro Spennato (P)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy. pierospen@gmail.com.

Giuseppe Mirone (G)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy.

Stefania Graziano (S)

Department Pediatric Neurology, Santobono-Pausilipon Children's Hospital, Naples, Italy.

Marco Gilone (M)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy.

Giuseppe Cinalli (G)

Department of Pediatric Neurosurgery, Santobono-Pausilipon Children's Hospital, Via Mario Fiore 6, 80121, Naples, Italy.

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Classifications MeSH