Loss of Neurological Disease HSAN-I-Associated Gene SPTLC2 Impairs CD8


Journal

Immunity
ISSN: 1097-4180
Titre abrégé: Immunity
Pays: United States
ID NLM: 9432918

Informations de publication

Date de publication:
21 05 2019
Historique:
received: 20 04 2018
revised: 07 01 2019
accepted: 06 03 2019
pubmed: 7 4 2019
medline: 18 10 2019
entrez: 7 4 2019
Statut: ppublish

Résumé

Patients with the neurological disorder HSAN-I suffer frequent infections, attributed to a lack of pain sensation and failure to seek care for minor injuries. Whether protective CD8

Identifiants

pubmed: 30952607
pii: S1074-7613(19)30095-0
doi: 10.1016/j.immuni.2019.03.005
pmc: PMC6531359
mid: NIHMS1523939
pii:
doi:

Substances chimiques

Cytokines 0
Sphingolipids 0
SPTLC2 protein, human EC 2.3.1.50
Serine C-Palmitoyltransferase EC 2.3.1.50
Mechanistic Target of Rapamycin Complex 1 EC 2.7.11.1

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

1218-1231.e5

Subventions

Organisme : Austrian Science Fund FWF
ID : P 27634
Pays : Austria
Organisme : NCATS NIH HHS
ID : UL1 TR001442
Pays : United States

Informations de copyright

Copyright © 2019 Elsevier Inc. All rights reserved.

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Auteurs

Jingxia Wu (J)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Sicong Ma (S)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany; Medical Faculty Heidelberg, Heidelberg University, 69120 Heidelberg, Germany.

Roger Sandhoff (R)

Lipid Pathobiochemistry Group (G131), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Yanan Ming (Y)

Internal Medicine IV, University Heidelberg Hospital, Im Neuenheimer Feld 345, 69120 Heidelberg, Germany.

Agnes Hotz-Wagenblatt (A)

Core Facility Omics IT and Data Management, German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Vincent Timmerman (V)

Peripheral Neuropathy Research Group, Department of Biomedical Sciences, Institute Born Bunge, B-2610, University of Antwerp, Antwerpen, Belgium.

Nathalie Bonello-Palot (N)

Department of Medical Genetics, Children Timone Hospital, 264 Rue Saint Pierre & Aix Marseille University, INSERM, MMG, U1251, 13385 Marseille, France.

Beate Schlotter-Weigel (B)

Friedrich-Baur-Institut, Neurologische Klinik and Poliklinik Ludwig-Maximilians-Universität, 80336 München, Germany.

Michaela Auer-Grumbach (M)

Department of Orthopaedics and Trauma Surgery, Medical University of Vienna, Vienna, Austria.

Pavel Seeman (P)

DNA Laboratory, Department of Child Neurology, 2nd Medical School, University Hospital Motol, Charles University, Prague, Czech Republic.

Wolfgang N Löscher (WN)

Clinical Department of Neurology, Medical University Innsbruck, Anichstr. 35, 6020 Innsbruck, Austria.

Markus Reindl (M)

Clinical Department of Neurology, Medical University Innsbruck, Anichstr. 35, 6020 Innsbruck, Austria.

Florian Weiss (F)

Department of Psychiatry and Psychotherapy, University Hospital of Psychiatry, Bolligenstrasse 111, 3000 Bern, Germany.

Eric Mah (E)

School of Medicine, UC San Diego, 9500 Gilman Drive, La Jolla, CA 92093, USA.

Nina Weisshaar (N)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany; Faculty of Biosciences, Heidelberg University, 69120 Heidelberg, Germany.

Alaa Madi (A)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany; Faculty of Biosciences, Heidelberg University, 69120 Heidelberg, Germany.

Kerstin Mohr (K)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Tilo Schlimbach (T)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Rubí M-H Velasco Cárdenas (RM)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Jonas Koeppel (J)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Florian Grünschläger (F)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Lisann Müller (L)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Maren Baumeister (M)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany.

Britta Brügger (B)

Heidelberg University Biochemistry Center (BZH), Im Neuenheimer Feld 328, Heidelberg, Germany.

Michael Schmitt (M)

Internal Medicine V, University Heidelberg Hospital, Im Neuenheimer Feld 410, 69120, Heidelberg, Germany.

Guido Wabnitz (G)

Section Molecular Immunology, Institute of Immunology, Heidelberg University, Im Neuenheimer Feld 305, 69120 Heidelberg, Germany.

Yvonne Samstag (Y)

Section Molecular Immunology, Institute of Immunology, Heidelberg University, Im Neuenheimer Feld 305, 69120 Heidelberg, Germany.

Guoliang Cui (G)

T Cell Metabolism Group (D140), German Cancer Research Center (DKFZ), Im Neuenheimer Feld 280, 69120 Heidelberg, Germany; Faculty of Biosciences, Heidelberg University, 69120 Heidelberg, Germany. Electronic address: g.cui@dkfz.de.

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Classifications MeSH