[Anti-laminin 332 mucous membrane pemphigoid with irreversible ocular and tracheobronchial involvement : Delayed diagnosis of a severe autoimmune bullous disease].
Anti-Laminin-332-Schleimhautpemphigoid mit irreversiblem okulärem und tracheobronchialem Befall : Verspätete Diagnosestellung einer schweren bullösen Autoimmunerkrankung.
Autoantibodies
Autoimmune dermatosis
Autoimmune diagnostics
Immunofluorescence
Immunosuppressive therapy
Journal
Der Hautarzt; Zeitschrift fur Dermatologie, Venerologie, und verwandte Gebiete
ISSN: 1432-1173
Titre abrégé: Hautarzt
Pays: Germany
ID NLM: 0372755
Informations de publication
Date de publication:
May 2019
May 2019
Historique:
pubmed:
10
4
2019
medline:
8
10
2019
entrez:
10
4
2019
Statut:
ppublish
Résumé
A 53-year-old man presented with a 37-year history of erosive and scarring mucosal lesions of several organs. An initial diagnosis of Stevens-Johnson syndrome was maintained for many years. Due to late correct diagnosis of an anti-laminin 332 mucous membrane pemphigoid and the fact that early, targeted, intensified immunosuppressive therapy was not initiated, the disease led to almost complete loss of vision and obstruction of airways.
Identifiants
pubmed: 30963224
doi: 10.1007/s00105-019-4402-z
pii: 10.1007/s00105-019-4402-z
doi:
Substances chimiques
Autoantibodies
0
Cell Adhesion Molecules
0
Types de publication
Case Reports
Journal Article
Langues
ger
Sous-ensembles de citation
IM
Pagination
367-370Références
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pubmed: 27456755
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pubmed: 27814419
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pubmed: 29242962