Local Inhibition of MEK/Akt Prevents Cellular Growth in Human Congenital Melanocytic Nevi.


Journal

The Journal of investigative dermatology
ISSN: 1523-1747
Titre abrégé: J Invest Dermatol
Pays: United States
ID NLM: 0426720

Informations de publication

Date de publication:
09 2019
Historique:
received: 11 07 2018
revised: 20 03 2019
accepted: 26 03 2019
pubmed: 7 5 2019
medline: 17 6 2020
entrez: 7 5 2019
Statut: ppublish

Résumé

The management of large congenital melanocytic nevi (lCMN) is based exclusively on iterative surgical procedures in the absence of validated medical therapy. The aim of our study was to develop an intra-lesional medical treatment for lCMN. Seventeen patients harboring NRAS-mutated lCMN were included. Nevocytes obtained from lCMN displayed an overactivation of mitogen-activated protein kinase and phosphoinositide 3-kinase (Akt) pathways. Mitogen-activated protein kinase/extracellular signal-regulated kinase (MEK) and Akt inhibitors reduced the nevosphere diameter in sphere-forming assays, as well as cell viability and proliferation in in vitro assays. Standardized lCMN explants were then cultured ex vivo with the same inhibitors, which induced a decrease in MelanA+ and Sox10+ cells in both epidermis and dermis. Finally, intradermal injections of these inhibitors were administered within standardized lCMN xenografts in Rag2

Identifiants

pubmed: 31059696
pii: S0022-202X(19)31499-X
doi: 10.1016/j.jid.2019.03.1156
pii:
doi:

Substances chimiques

Antineoplastic Agents 0
MART-1 Antigen 0
MLANA protein, human 0
Membrane Proteins 0
SOX10 protein, human 0
SOXE Transcription Factors 0
Proto-Oncogene Proteins c-akt EC 2.7.11.1
Mitogen-Activated Protein Kinase Kinases EC 2.7.12.2
GTP Phosphohydrolases EC 3.6.1.-
NRAS protein, human EC 3.6.1.-

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

2004-2015.e13

Commentaires et corrections

Type : CommentIn

Informations de copyright

Copyright © 2019 The Authors. Published by Elsevier Inc. All rights reserved.

Auteurs

Thomas Rouillé (T)

Saint-Antoine Research Center, INSERM UMRS_938, Paris, France; Sorbonne Université, Paris, France.

Selim Aractingi (S)

Saint-Antoine Research Center, INSERM UMRS_938, Paris, France; Université Paris-Descartes, Paris, France; AP-HP, Hôpital Cochin, Department of Dermatology, Paris, France.

Natacha Kadlub (N)

Université Paris-Descartes, Paris, France; AP-HP, Hôpital Necker-Enfants-Malades, Department of Maxillofacial and Plastic Surgery, Paris, France.

Sylvie Fraitag (S)

AP-HP, Hôpital Necker-Enfants-Malades, Department of Pathology, Paris, France.

Alexandre How-Kit (A)

Laboratory for Functional Genomics, Fondation Jean Dausset-CEPH, Paris, France.

Antoine Daunay (A)

Laboratory for Functional Genomics, Fondation Jean Dausset-CEPH, Paris, France.

Mikael Hivelin (M)

Université Paris-Descartes, Paris, France; AP-HP, Hôpital Européen Georges-Pompidou, Department of Plastic Surgery, Paris, France.

Philippe Moguelet (P)

AP-HP, Hôpital Tenon, Department of Pathology, Paris, France.

Arnaud Picard (A)

Université Paris-Descartes, Paris, France; AP-HP, Hôpital Necker-Enfants-Malades, Department of Maxillofacial and Plastic Surgery, Paris, France.

Romain H Fontaine (RH)

Saint-Antoine Research Center, INSERM UMRS_938, Paris, France; Sorbonne Université, Paris, France.

Sarah Guégan (S)

Saint-Antoine Research Center, INSERM UMRS_938, Paris, France; Université Paris-Descartes, Paris, France; AP-HP, Hôpital Cochin, Department of Dermatology, Paris, France. Electronic address: sarah.guegan.bart@gmail.com.

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Classifications MeSH