Antibody-Mediated Enzyme Therapeutics and Applications in Glycogen Storage Diseases.


Journal

Trends in molecular medicine
ISSN: 1471-499X
Titre abrégé: Trends Mol Med
Pays: England
ID NLM: 100966035

Informations de publication

Date de publication:
12 2019
Historique:
received: 27 05 2019
revised: 07 08 2019
accepted: 12 08 2019
pubmed: 17 9 2019
medline: 22 7 2020
entrez: 17 9 2019
Statut: ppublish

Résumé

The use of antibodies as targeting molecules or cell-penetrating tools has emerged at the forefront of pharmaceutical research. Antibody-directed therapies in the form of antibody-drug conjugates, immune modulators, and antibody-directed enzyme prodrugs have been most extensively utilized as hematological, rheumatological, and oncological therapies, but recent developments are identifying additional applications of antibody-mediated delivery systems. A novel application of this technology is for the treatment of glycogen storage disorders (GSDs) via an antibody-enzyme fusion (AEF) platform to penetrate cells and deliver an enzyme to the cytoplasm, nucleus, and/or other organelles. Exciting developments are currently underway for AEFs in the treatment of the GSDs Pompe disease and Lafora disease (LD). Antibody-based therapies are quickly becoming an integral part of modern disease therapeutics.

Identifiants

pubmed: 31522955
pii: S1471-4914(19)30226-6
doi: 10.1016/j.molmed.2019.08.005
pmc: PMC6889062
mid: NIHMS1537636
pii:
doi:

Substances chimiques

Antibodies 0
Immunoconjugates 0
Recombinant Fusion Proteins 0

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

1094-1109

Subventions

Organisme : NINDS NIH HHS
ID : P01 NS097197
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS070899
Pays : United States
Organisme : NCATS NIH HHS
ID : TL1 TR001997
Pays : United States
Organisme : NCATS NIH HHS
ID : UL1 TR001998
Pays : United States

Informations de copyright

Copyright © 2019 Elsevier Ltd. All rights reserved.

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Auteurs

Zhengqiu Zhou (Z)

Department of Molecular and Cellular Biochemistry, University of Kentucky College of Medicine, Lexington, KY 40536, USA.

Grant L Austin (GL)

Department of Molecular and Cellular Biochemistry, University of Kentucky College of Medicine, Lexington, KY 40536, USA.

Robert Shaffer (R)

Valerion Therapeutics, Concord, MA 01742, USA.

Dustin D Armstrong (DD)

Valerion Therapeutics, Concord, MA 01742, USA.

Matthew S Gentry (MS)

Department of Molecular and Cellular Biochemistry, University of Kentucky College of Medicine, Lexington, KY 40536, USA; Lafora Epilepsy Cure Initiative, University of Kentucky College of Medicine, Lexington, KY 40536, USA; Epilepsy and Brain Metabolism Alliance, University of Kentucky College of Medicine, Lexington, KY 40536, USA. Electronic address: matthew.gentry@uky.edu.

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