Non-syndromic monogenic male infertility.


Journal

Acta bio-medica : Atenei Parmensis
ISSN: 2531-6745
Titre abrégé: Acta Biomed
Pays: Italy
ID NLM: 101295064

Informations de publication

Date de publication:
30 09 2019
Historique:
received: 06 08 2019
accepted: 06 08 2019
entrez: 3 10 2019
pubmed: 3 10 2019
medline: 24 10 2020
Statut: epublish

Résumé

Infertility is a widespread clinical problem affecting 8-12% of couples worldwide. Of these, about 30% are diagnosed with idiopathic infertility since no causative factor is found. Overall 40-50% of cases are due to male reproductive defects. Numerical or structural chromosome abnormalities have long been associated with male infertility. Monogenic mutations have only recently been addressed in the pathogenesis of this condition. Mutations of specific genes involved in meiosis, mitosis or spermiohistogenesis result in spermatogenic failure, leading to the following anomalies: insufficient (oligozoospermia) or no (azoospermia) sperm production, limited progressive and/or total sperm motility (asthenozoospermia), altered sperm morphology (teratozoospermia), or combinations thereof. Androgen insensitivity, causing hormonal and sexual impairment in males with normal karyotype, also affects male fertility. The genetic causes of non-syndromic monogenic of male infertility are summarized in this article and a gene panel is proposed.

Identifiants

pubmed: 31577257
doi: 10.23750/abm.v90i10-S.8762
pmc: PMC7233647
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

62-67

Références

Mol Hum Reprod. 2011 Dec;17(12):762-8
pubmed: 21733974
Fertil Steril. 2013 Jan;99(1):63
pubmed: 23095139
Andrology. 2016 Jan;4(1):75-81
pubmed: 26452337
Curr Genet Med Rep. 2013 Dec 1;1(4):
pubmed: 24416713
Nat Genet. 1999 Dec;23(4):429-32
pubmed: 10581029
Hum Reprod Update. 2015 Jul-Aug;21(4):455-85
pubmed: 25888788
J Hum Reprod Sci. 2015 Oct-Dec;8(4):191-6
pubmed: 26752853
Hum Genet. 2013 Feb;132(2):159-65
pubmed: 23064888
Clin Biochem Rev. 2016 Feb;37(1):3-15
pubmed: 27057074
J Med Genet. 2017 Sep;54(9):633-639
pubmed: 28536242
J Med Genet. 2014 Apr;51(4):239-44
pubmed: 24431330
Med Genet. 2018;30(1):12-20
pubmed: 29527098
Andrology. 2017 Jul;5(4):824-831
pubmed: 28718531
Proc Natl Acad Sci U S A. 1976 Mar;73(3):891-4
pubmed: 176660
Hum Mol Genet. 2012 Aug 15;21(16):3695-702
pubmed: 22653751
Lancet Diabetes Endocrinol. 2017 Jul;5(7):544-553
pubmed: 27395771
J Urol. 1989 Jul;142(1):62-5
pubmed: 2499695
PLoS Med. 2012;9(12):e1001356
pubmed: 23271957
Oncotarget. 2017 Mar 21;8(12):19914-19922
pubmed: 28199965
Saudi J Biol Sci. 2018 Jul;25(5):881-887
pubmed: 30108436
Hum Mol Genet. 2015 Oct 1;24(19):5581-8
pubmed: 26199321
Am J Hum Genet. 2017 Jun 1;100(6):854-864
pubmed: 28552195
Am J Hum Genet. 2007 Oct;81(4):813-20
pubmed: 17847006
J Assist Reprod Genet. 2015 Apr;32(4):615-23
pubmed: 25711835
Hum Genet. 2019 Feb;138(2):125-140
pubmed: 30656449
Clin Genet. 2017 Feb;91(2):208-216
pubmed: 27779755
Am J Hum Genet. 2010 Oct 8;87(4):505-12
pubmed: 20887963
J Assist Reprod Genet. 2015 Jun;32(6):887-91
pubmed: 25899990
EMBO Mol Med. 2015 Jul 01;7(9):1198-210
pubmed: 26136358
Lancet. 2003 Nov 22;362(9397):1714-9
pubmed: 14643120
Transl Androl Urol. 2013 Sep 1;2(3):137-147
pubmed: 25045626
J Endocrinol Invest. 2014 May;37(5):415-27
pubmed: 24458834
Am J Hum Genet. 2016 Oct 6;99(4):942-949
pubmed: 27640305
Clin Endocrinol (Oxf). 2006 Nov;65(5):606-10
pubmed: 17054461
Hum Mutat. 2012 May;33(5):887-94
pubmed: 22334387
Hum Mutat. 2010 Jul;31(7):788-93
pubmed: 20506135
Fertil Steril. 1987 Nov;48(5):711-34
pubmed: 3311822

Auteurs

Articles similaires

Genome, Chloroplast Phylogeny Genetic Markers Base Composition High-Throughput Nucleotide Sequencing

[Redispensing of expensive oral anticancer medicines: a practical application].

Lisanne N van Merendonk, Kübra Akgöl, Bastiaan Nuijen
1.00
Humans Antineoplastic Agents Administration, Oral Drug Costs Counterfeit Drugs

Smoking Cessation and Incident Cardiovascular Disease.

Jun Hwan Cho, Seung Yong Shin, Hoseob Kim et al.
1.00
Humans Male Smoking Cessation Cardiovascular Diseases Female
Humans United States Aged Cross-Sectional Studies Medicare Part C

Classifications MeSH