Targeted next-generation sequencing panels in the diagnosis of Charcot-Marie-Tooth disease.


Journal

Neurology
ISSN: 1526-632X
Titre abrégé: Neurology
Pays: United States
ID NLM: 0401060

Informations de publication

Date de publication:
07 01 2020
Historique:
received: 14 03 2019
accepted: 24 06 2019
pubmed: 13 12 2019
medline: 24 3 2020
entrez: 13 12 2019
Statut: ppublish

Résumé

To investigate the effectiveness of targeted next-generation sequencing (NGS) panels in achieving a molecular diagnosis in Charcot-Marie-Tooth disease (CMT) and related disorders in a clinical setting. We prospectively enrolled 220 patients from 2 tertiary referral centers, one in London, United Kingdom (n = 120), and one in Iowa (n = 100), in whom a targeted CMT NGS panel had been requested as a diagnostic test. After targeted NGS sequencing, a definite molecular diagnosis, defined as a pathogenic or likely pathogenic variant, was reached in 30% of cases (n = 67). The diagnostic rate was similar in London (32%) and Iowa (29%). Variants of unknown significance were found in an additional 33% of cases. Mutations in NGS panels are effective tools in the diagnosis of CMT, leading to genetic confirmation in one-third of cases negative for

Identifiants

pubmed: 31827005
pii: WNL.0000000000008672
doi: 10.1212/WNL.0000000000008672
pmc: PMC7011687
doi:

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

e51-e61

Subventions

Organisme : Medical Research Council
ID : G108/638
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/T001712/1
Pays : United Kingdom
Organisme : Medical Research Council
ID : G0802760
Pays : United Kingdom
Organisme : Medical Research Council
ID : G1001253
Pays : United Kingdom
Organisme : The Dunhill Medical Trust
ID : R605/0717
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/S01165X/1
Pays : United Kingdom

Commentaires et corrections

Type : ErratumIn
Type : ErratumIn

Informations de copyright

Copyright © 2019 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of the American Academy of Neurology.

Références

J Neurol. 2014 May;261(5):970-82
pubmed: 24627108
Neuron. 2011 Oct 20;72(2):257-68
pubmed: 21944779
Cell Rep. 2015 Aug 18;12(7):1169-83
pubmed: 26257172
J Peripher Nerv Syst. 2016 Mar;21(1):52-4
pubmed: 26930221
J Peripher Nerv Syst. 2011 Sep;16(3):191-8
pubmed: 22003934
Mol Genet Genomic Med. 2015 Mar;3(2):143-54
pubmed: 25802885
Clin Genet. 2011 Oct;80(4):334-45
pubmed: 21291453
Curr Genomics. 2018 Sep;19(6):412-419
pubmed: 30258273
Neurology. 2017 Apr 11;88(15):1445-1453
pubmed: 28283593
J Neurol Neurosurg Psychiatry. 2015 Aug;86(8):873-8
pubmed: 25430934
Handb Clin Neurol. 2018;148:653-665
pubmed: 29478606
Orphanet J Rare Dis. 2016 Aug 22;11(1):118
pubmed: 27549087
Neurology. 2016 May 10;86(19):1762-71
pubmed: 27164712
J Neurochem. 2017 Dec;143(5):507-522
pubmed: 28902413
J Peripher Nerv Syst. 2016 Sep;21(3):142-9
pubmed: 27231023
J Neurol Neurosurg Psychiatry. 2019 Feb;90(2):195-202
pubmed: 30257968
Neurology. 2017 Aug 29;89(9):927-935
pubmed: 28768847
Neuromuscul Disord. 2018 Dec;28(12):1012-1015
pubmed: 30385095
J Mol Diagn. 2016 Mar;18(2):225-34
pubmed: 26752306
Mol Cells. 2016 May 31;39(5):382-8
pubmed: 27025386
Neuron. 2011 Oct 20;72(2):245-56
pubmed: 21944778
BMC Med Genet. 2015 Sep 21;16:84
pubmed: 26392352
Curr Opin Neurol. 2016 Oct;29(5):537-48
pubmed: 27584852
Nat Genet. 2018 Apr;50(4):581-590
pubmed: 29507423
Genet Med. 2015 May;17(5):405-24
pubmed: 25741868
Nat Genet. 2019 Apr;51(4):649-658
pubmed: 30926972
Ann Neurol. 2011 Jan;69(1):22-33
pubmed: 21280073
Biomed Res Int. 2014;2014:210401
pubmed: 25025039
Mol Genet Genomic Med. 2018 May;6(3):422-433
pubmed: 29573232
Eur J Hum Genet. 2014 Apr;22(4):522-7
pubmed: 23963299
J Neurol Neurosurg Psychiatry. 2012 Jul;83(7):706-10
pubmed: 22577229
Eur J Med Genet. 2019 Jan;62(1):1-8
pubmed: 29653220
Hum Mutat. 2012 Nov;33(11):1610-5
pubmed: 22730194
Biomed Res Int. 2015;2015:314651
pubmed: 26558264
Neuromuscul Disord. 2009 Apr;19(4):264-9
pubmed: 19272779

Auteurs

Andrea Cortese (A)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Janel E Wilcox (JE)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

James M Polke (JM)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Roy Poh (R)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Mariola Skorupinska (M)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Alexander M Rossor (AM)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Matilde Laura (M)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Pedro J Tomaselli (PJ)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Henry Houlden (H)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Michael E Shy (ME)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City.

Mary M Reilly (MM)

From the MRC Centre for Neuromuscular Diseases (A.C., J.M.P., R.P., M.S., A.M.R., M.L., P.J.T., H.H., M.M.R.), Department of Neuromuscular Diseases, National Hospital for Neurology and Neurosurgery, UCL Queen Square Institute of Neurology, London, UK; Department of Brain and Behavioral Sciences (A.C.), University of Pavia, Italy; and the Department of Neurology (J.E.W., M.E.S.), University of Iowa Carver College of Medicine, Iowa City. m.reilly@ucl.ac.uk.

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