Polymorphisms in Inflammatory Genes Modulate Clinical Complications in Patients With Sickle Cell Disease.


Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2020
Historique:
received: 20 04 2020
accepted: 27 07 2020
entrez: 5 10 2020
pubmed: 6 10 2020
medline: 1 5 2021
Statut: epublish

Résumé

Sickle cell disease (SCD), the most common monogenic disease worldwide, is marked by a phenotypic variability that is, to date, only partially understood. Because inflammation plays a major role in SCD pathophysiology, we hypothesized that single nucleotide polymorphisms (SNP) in genes encoding functionally important inflammatory proteins might modulate the occurrence of SCD complications. We assessed the association between 20 SNPs in genes encoding Toll-like receptors (TLR), NK cell receptors (NKG), histocompatibility leukocyte antigens (HLA), major histocompatibility complex class I polypeptide-related sequence A (MICA) and cytotoxic T-lymphocyte-associated antigen 4 (CTLA-4), and the occurrence of six SCD clinical complications (stroke, acute chest syndrome (ACS), leg ulcers, cholelithiasis, osteonecrosis, or retinopathy). This study was performed in a cohort of 500 patients. We found that the

Identifiants

pubmed: 33013863
doi: 10.3389/fimmu.2020.02041
pmc: PMC7510050
doi:

Substances chimiques

HLA Antigens 0
KLRK1 protein, human 0
NK Cell Lectin-Like Receptor Subfamily K 0
Toll-Like Receptors 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

2041

Informations de copyright

Copyright © 2020 Tozatto-Maio, Girot, Ly, Silva Pinto, Rocha, Fernandes, Diagne, Benzerara, Dinardo, Soler, Kashima, Araujo, Kenzey, Fonseca, Rodrigues, Volt, Jarduli, Ruggeri, Mariaselvam, Gualandro, Rafii, Cappelli, Nogueira, Scigliuolo, Guerino-Cunha, Malmegrim, Simões, Gluckman and Tamouza.

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Auteurs

Karina Tozatto-Maio (K)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.
Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.
Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Robert Girot (R)

CHU Tenon, Paris, France.

Indou Deme Ly (ID)

National Children Hospital Center Albert Royer, Cheikh Anta Diop University, Dakar, Senegal.

Ana Cristina Silva Pinto (AC)

Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.
Center for Cell-based Therapy, Regional Blood Center of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Vanderson Rocha (V)

Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Francisco Fernandes (F)

Instituto de Matematica e Estatistica da Universidade de São Paulo, São Paulo, Brazil.

Ibrahima Diagne (I)

National Children Hospital Center Albert Royer, Cheikh Anta Diop University, Dakar, Senegal.

Yahia Benzerara (Y)

Département de Bactériologie, Hôpital Saint-Antoine, Hôpitaux de l'Est parisien, Paris, France.

Carla L Dinardo (CL)

Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Julia Pavan Soler (JP)

Instituto de Matematica e Estatistica da Universidade de São Paulo, São Paulo, Brazil.

Simone Kashima (S)

Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.
Center for Cell-based Therapy, Regional Blood Center of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Itauá Leston Araujo (IL)

INSERM 1160, Université Paris 7, Paris, France.

Chantal Kenzey (C)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Guilherme H H Fonseca (GHH)

Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Evandra S Rodrigues (ES)

Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.
Center for Cell-based Therapy, Regional Blood Center of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Fernanda Volt (F)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Luciana Jarduli (L)

Center for Cell-based Therapy, Regional Blood Center of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.
School of Pharmaceutical Sciences of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Annalisa Ruggeri (A)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Haematology and Bone Marrow Transplant Unit, IRCCS San Raffaele Scientific Institute, Milan, Italy.
Cellular Therapy and Immunobiology Working Party, The European Society for Blood and Marrow Transplantation, Paris, France.

Christina Mariaselvam (C)

INSERM U955, CHU Henri Mondor, Créteil, France.

Sandra F M Gualandro (SFM)

Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Hanadi Rafii (H)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Barbara Cappelli (B)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Felipe Melo Nogueira (FM)

Disciplina de Hematologia e Hemoterapia, Faculdade de Medicina, Universidade de São Paulo, São Paulo, Brazil.

Graziana Maria Scigliuolo (GM)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Renato Luiz Guerino-Cunha (RL)

Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.
Center for Cell-based Therapy, Regional Blood Center of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Kelen Cristina Ribeiro Malmegrim (KCR)

School of Pharmaceutical Sciences of Ribeirão Preto, University of São Paulo, Ribeirão Preto, Brazil.

Belinda P Simões (BP)

Faculdade de Medicina de Ribeirão Preto, Universidade de São Paulo, Ribeirão Preto, Brazil.

Eliane Gluckman (E)

Eurocord, Université de Paris, IRSL, Hopital Saint Louis, Paris, France.
Monacord, International Observatory on Sickle Cell Disease, Centre Scientifique de Monaco, Monaco, Monaco.

Ryad Tamouza (R)

INSERM U955, CHU Henri Mondor, Créteil, France.

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Classifications MeSH