Characterizing temporal genomic heterogeneity in pediatric low-grade gliomas.


Journal

Acta neuropathologica communications
ISSN: 2051-5960
Titre abrégé: Acta Neuropathol Commun
Pays: England
ID NLM: 101610673

Informations de publication

Date de publication:
05 11 2020
Historique:
received: 25 08 2020
accepted: 10 10 2020
entrez: 6 11 2020
pubmed: 7 11 2020
medline: 11 11 2021
Statut: epublish

Résumé

Recent discoveries have provided valuable insight into the genomic landscape of pediatric low-grade gliomas (LGGs) at diagnosis, facilitating molecularly targeted treatment. However, little is known about their temporal and therapy-related genomic heterogeneity. An adequate understanding of the evolution of pediatric LGGs' genomic profiles over time is critically important in guiding decisions about targeted therapeutics and diagnostic biopsy at recurrence. Fluorescence in situ hybridization, mutation-specific immunohistochemistry, and/or targeted sequencing were performed on paired tumor samples from primary diagnostic and subsequent surgeries. Ninety-four tumor samples from 45 patients (41 with two specimens, four with three specimens) from three institutions underwent testing. Conservation of BRAF fusion, BRAF

Identifiants

pubmed: 33153497
doi: 10.1186/s40478-020-01054-w
pii: 10.1186/s40478-020-01054-w
pmc: PMC7643477
doi:

Substances chimiques

CDKN2A protein, human 0
Cyclin-Dependent Kinase Inhibitor p16 0
MYB protein, human 0
MYBL1 protein, human 0
Membrane Glycoproteins 0
Proto-Oncogene Proteins 0
Proto-Oncogene Proteins c-myb 0
Trans-Activators 0
Isocitrate Dehydrogenase EC 1.1.1.41
IDH1 protein, human EC 1.1.1.42.
FGFR1 protein, human EC 2.7.10.1
Receptor, Fibroblast Growth Factor, Type 1 EC 2.7.10.1
Receptor, trkB EC 2.7.10.1
tropomyosin-related kinase-B, human EC 2.7.10.1
BRAF protein, human EC 2.7.11.1
Proto-Oncogene Proteins B-raf EC 2.7.11.1

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

182

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Auteurs

Margot A Lazow (MA)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.

Lindsey Hoffman (L)

Department of Oncology, Phoenix Children's Hospital, Phoenix, AZ, USA.

Austin Schafer (A)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.

Diana S Osorio (DS)

Department of Oncology, Nationwide Children's Hospital, The Ohio State University, Columbus, OH, USA.

Daniel R Boué (DR)

Department of Pathology and Laboratory Medicine, Nationwide Children's Hospital, The Ohio State University, Columbus, OH, USA.

Sarah Rush (S)

Department of Oncology, Akron Children's Hospital, Akron, OH, USA.

Erin Wright (E)

Department of Oncology, Akron Children's Hospital, Akron, OH, USA.

Adam Lane (A)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Mariko D DeWire-Schottmiller (MD)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Teresa Smolarek (T)

Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.
Department of Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Jared Sipple (J)

Department of Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Heather Taggert (H)

Department of Genetics, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.

Jaime Reuss (J)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.

Ralph Salloum (R)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Trent R Hummel (TR)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Peter de Blank (P)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Natasha Pillay-Smiley (N)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Mary E Sutton (ME)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Anthony Asher (A)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.

Charles B Stevenson (CB)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Rachid Drissi (R)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA.

Jonathan L Finlay (JL)

Department of Oncology, Nationwide Children's Hospital, The Ohio State University, Columbus, OH, USA.

Maryam Fouladi (M)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA. maryam.fouladi@nationwidechildrens.org.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA. maryam.fouladi@nationwidechildrens.org.
Pediatric Neuro-Oncology, Nationwide Children's Hospital, 700 Children's Dr., Columbus, OH, 43205, USA. maryam.fouladi@nationwidechildrens.org.

Christine Fuller (C)

Brain Tumor Center, Cancer and Blood Diseases Institute, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave, Cincinnati, OH, 45229, USA. fullerch@upstate.edu.
Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, OH, USA. fullerch@upstate.edu.
Department of Pathology, Upstate Medical University, 750 E Adams St., Syracuse, NY, 13210, USA. fullerch@upstate.edu.

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Classifications MeSH