The global impact of SARS-CoV-2 in 181 people with cystic fibrosis.


Journal

Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society
ISSN: 1873-5010
Titre abrégé: J Cyst Fibros
Pays: Netherlands
ID NLM: 101128966

Informations de publication

Date de publication:
11 2020
Historique:
received: 14 09 2020
revised: 21 10 2020
accepted: 23 10 2020
pubmed: 14 11 2020
medline: 31 12 2020
entrez: 13 11 2020
Statut: ppublish

Résumé

With the growing SARS-CoV-2 pandemic, we need to better understand its impact in specific patient groups like those with Cystic Fibrosis (CF). We report on 181 people with CF (32 post-transplant) from 19 countries diagnosed with SARS-CoV-2 prior to 13 June 2020. Infection with SARS-CoV-2 appears to exhibit a similar spectrum of outcomes to that seen in the general population, with 11 people admitted to intensive care (7 post-transplant), and 7 deaths (3 post-transplant). A more severe clinical course may be associated with older age, CF-related diabetes, lower lung function in the year prior to infection, and having received an organ transplant. Whilst outcomes in this large cohort are better than initially feared overall, possibly due to a protective effect of the relatively younger age of the CF population compared to other chronic conditions, SARS-CoV-2 is not a benign disease for all people in this patient group.

Identifiants

pubmed: 33183965
pii: S1569-1993(20)30877-8
doi: 10.1016/j.jcf.2020.10.003
pmc: PMC7641525
pii:
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

868-871

Investigateurs

Scott C Bell (SC)
David Reid (D)
Peter Wark (P)
Eva Van Braeckel (EV)
Sophie Gohy (S)
Christiane Knoop (C)
Jessica Pirson (J)
Elke De Wachter (E)
Lieven Dupont (L)
Laurence Hanssens (L)
Vicky Nowé (V)
Monique Lequesne (M)
Rodrigo A Athanazio (RA)
Daniela G Meneses (DG)
Véronique Boussaud (V)
Graziella Brinchault (G)
Emmanuelle Coirier-Duet (E)
Jean-Christophe Dubus (JC)
Dominique Grenet (D)
Sandra de Miranda (S)
Laurence Beaumont (L)
Reem Kanaan (R)
Muriel Lauraens (M)
Clémence Martin (C)
Marie Mittaine Martin (MM)
Anne Prévotat (A)
Martine Reynaud-Gaubert (M)
Isabelle Sermet-Gaudelus (I)
Aurelie Tatopoulos (A)
Raphael Chiron (R)
Marie-Laure Dalphin (ML)
Michele Gerardin (M)
Laurence Weiss (L)
Nathalie Wizla (N)
Sophie Ramel (S)
Barry Plant (B)
Cedric Gunaratnam (C)
Abaigeal Jackson (A)
Rosaria Casciaro (R)
Francesca Lucca (F)
Valeria Daccò (V)
Anna Folino (A)
Antonio Manca (A)
Barbara Messore (B)
Letizia Morlacchi (L)
Giovanna Pisi (G)
Piercarlo Poli (P)
Annalisa Amato (A)
Gianluca Ferrari (G)
Karin de Winter-de Groot (K)
Bart Luijk (B)
Geertjan Wesseling (G)
Elena Kondratyeva (E)
Elena Zhekayte (E)
Elena Amelina (E)
Mariya Mukhina (M)
Olga Simonova (O)
Antonio Alvarez-Fernandez (A)
Amparo Sole-Jover (A)
Isidoro Cortell-Aznar (I)
Rosa Giron-Moreno (R)
Alejandro Lopez-Neyra (A)
Isabel Ramos-Cancelo (I)
Maite Lzaro-Carrasco (M)
Marta Ruiz de Valbuena (M)
Concepcin Prados-Sanchez (C)
Jordi Costa-Colomer (J)
Silvia Gartner (S)
Layla Diab-Caceres (L)
Marita Gilljam (M)
Ulrika Lindberg (U)
Stefanie Diemer (S)
Mark Allenby (M)
Stephen J Bourke (S)
Susan C Charman (S)
Janet Collinson (J)
Owen Dempsey (O)
Sarah Denniston (S)
Maya Desai (M)
Jamie Duckers (J)
Christine Etherington (C)
Elaine Gunn (E)
Alex Higton (A)
Timothy Ho (T)
Jeremy Hull (J)
Andrew Jones (A)
Robert Ian Ketchell (R)
Susan L Madge (SL)
Anirban Maitra (A)
Ghulam Mujtaba (G)
Edward Nash (E)
Dilip Nazareth (D)
Christopher OBrien (C)
Claire Onyon (C)
Christopher Orchard (C)
Daniel Peckham (D)
Helen Rodgers (H)
Nadia Shafi (N)
Nicholas Simmonds (N)
Kevin Southern (K)
Martin Walshaw (M)
Danie Watson (D)
Joanna L Whitehouse (J)

Informations de copyright

Copyright © 2020 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.

Déclaration de conflit d'intérêts

Declaration of Competing Interest The authors have no conflicts of interest to declare relating to this work.

Auteurs

Elliot McClenaghan (E)

Cystic Fibrosis Trust, UK CF Registry, 1 Aldgate, London EC3N 1RE, UK. Electronic address: elliot.mcclenaghan@cysticfibrosis.org.uk.

Rebecca Cosgriff (R)

Cystic Fibrosis Trust, UK CF Registry, 1 Aldgate, London EC3N 1RE, UK.

Keith Brownlee (K)

Cystic Fibrosis Trust, UK CF Registry, 1 Aldgate, London EC3N 1RE, UK.

Susannah Ahern (S)

Monash University, Melbourne, Australia.

Pierre-Régis Burgel (PR)

Université de Paris, Inserm U1016, Institut Cochin and Cochin Hospital, Assistance Publique Hôpitaux de Paris (APHP), France.

Catherine A Byrnes (CA)

Starship Children's Hospital and University of Auckland, Auckland, New Zealand.

Carla Colombo (C)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, University of Milan, Milan, Italy.

Harriet Corvol (H)

Sorbonne Université, Inserm, Centre de Recherche Saint-Antoine, Assistance Publique Hôpitaux de Paris (APHP), Hôpital Trousseau, Service de Pneumologie Pédiatrique, Paris, France.

Stephanie Y Cheng (SY)

Cystic Fibrosis Canada, Canada.

Géraldine Daneau (G)

Sciensano, Belgium.

Alexander Elbert (A)

Cystic Fibrosis Foundation, USA.

Albert Faro (A)

Cystic Fibrosis Foundation, USA.

Christopher H Goss (CH)

University of Washington, Seattle, USA.

Vincent Gulmans (V)

Dutch CF Foundation NCFS, Baarn, Netherlands.

Hector Gutierrez (H)

University of Alabama at Birmingham, Alabama, USA.

Isabelle de Monestrol (I)

Stockholm CF Center, Sweden.

Andreas Jung (A)

University Children's Hospital Zurich, Switzerland.

Lutz Nährlich Justus (LN)

Department of Pediatrics, Justus-Liebig-University Giessen, Giessen, Germany.

Nataliya Kashirskaya (N)

Research Centre for Medical Genetics, Russia.

Bruce C Marshall (BC)

Cystic Fibrosis Foundation, USA.

Edward McKone (E)

St Vincent's University Hospital, Dublin, Ireland.

Peter G Middleton (PG)

Westmead Hospital, Sydney, Australia.

Pedro Mondejar-Lopez (P)

Hospital Clínico Universitario Virgen de la Arrixaca, Murcia, Spain.

M Dolores Pastor-Vivero (MD)

Hospital Universitario Cruces, Bizkaia, Spain.

Rita Padoan (R)

Cystic Fibrosis Support Center, Department of Paediatric, University of Brescia, Italy.

Samar Rizvi (S)

Cystic Fibrosis Foundation, USA.

Rasa Ruseckaite (R)

Monash University, Melbourne, Australia.

Marco Salvatore (M)

National Center Rare Diseases Undiagnosed Rare Diseases Interdepartmental Unit Istituto Superiore di Sanità, Rome, Italy.

Anne L Stephenson (AL)

Cystic Fibrosis Canada, Canada; Toronto Adult Cystic Fibrosis Centre, St. Michael's Hospital, Toronto, Canada.

Luiz Vicente R da Silva Filho (LVRDS)

Instituto da Criança HCFMUSP, São Paulo, Brazil.

Joel Melo (J)

Instituto Nacional del Tórax, Chile.

Marco Zampoli (M)

University of Cape Town and Red Cross War Memorial Children's Hospital, South Africa.

Siobhán B Carr (SB)

Royal Brompton Hospital and Imperial College London, UK.

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