Unexpected fatal intramyocardial cartilaginous tumor: pathophysiology, mechanism of death and review of the literature.
Autopsy
Cartilage
Myocardium
Pediatric
Sudden death
Journal
Forensic science, medicine, and pathology
ISSN: 1556-2891
Titre abrégé: Forensic Sci Med Pathol
Pays: United States
ID NLM: 101236111
Informations de publication
Date de publication:
Jun 2021
Jun 2021
Historique:
accepted:
28
12
2020
pubmed:
26
1
2021
medline:
9
11
2021
entrez:
25
1
2021
Statut:
ppublish
Résumé
Intramyocardial cartilage has never been reported in the human heart before. In the literature, the only reported localizations of cartilage in the heart were in the central fibrous body and the valves. We report a case of an unusual presence of cartilage tissue within the myocardial wall of the left ventricle in a 10-year-old boy who died unexpectedly. This case presents an interesting, unusual and apparently asymptomatic sudden cardiac death related to a cartilaginous myocardial tumor. Conducting system disturbance secondary to the myocardial tumor is the probable cause of death. This case is relevant not only for its singularity and originality, but also for the diverse and controversial hypotheses related to the onset of cartilaginous tissue in the myocardial wall. Early detection of this tumor by modern thoracic imaging may have prevented a fatal unexpected outcome.
Identifiants
pubmed: 33492632
doi: 10.1007/s12024-020-00351-z
pii: 10.1007/s12024-020-00351-z
doi:
Types de publication
Case Reports
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
308-311Références
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