Predictors of transient congenital primary hypothyroidism: data from the German registry for congenital hypothyroidism (AQUAPE "HypoDok").


Journal

European journal of pediatrics
ISSN: 1432-1076
Titre abrégé: Eur J Pediatr
Pays: Germany
ID NLM: 7603873

Informations de publication

Date de publication:
Aug 2021
Historique:
received: 04 12 2020
accepted: 12 03 2021
revised: 09 03 2021
pubmed: 27 3 2021
medline: 21 7 2021
entrez: 26 3 2021
Statut: ppublish

Résumé

Neonatal screening for congenital primary hypothyroidism (CH) may not distinguish between transient (TCH) and permanent dysfunction (PCH), causing potential overtreatment and concerns in affected families. To specify the indication for interruption of therapy, we analysed the German registry "HypoDok" for infants with CH, which oversees 1625 patients from 49 participating centres in Germany and Austria from 1997 until today. A total of 357 patients with a thyroid gland in loco typico were identified and retrospectively grouped according to cessation (TCH, n = 24) or continuation (PCH, n = 333) of L-thyroxine (L-T

Identifiants

pubmed: 33768331
doi: 10.1007/s00431-021-04031-0
pii: 10.1007/s00431-021-04031-0
pmc: PMC8285326
doi:

Substances chimiques

Thyrotropin 9002-71-5
Thyroxine Q51BO43MG4

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

2401-2408

Informations de copyright

© 2021. The Author(s).

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Auteurs

Nicola Matejek (N)

Division of Paediatric Endocrinology and Diabetes, Department of Paediatrics, University Children's Hospital Heidelberg, Im Neuenheimer Feld 430, 69120, Heidelberg, Germany. nmatejek@t-online.de.

Sascha R Tittel (SR)

Central Institute for Biomedical Technology, Institute for Epidemiology and Medical Biometry, University of Ulm, Ulm, Germany.

Holger Haberland (H)

Social-Paediatric Centre, Sana-Hospital Lichtenberg, Berlin, Germany.

Tilman Rohrer (T)

Department of Paediatrics, University Hospital Homburg-Saar, Homburg, Germany.

Eva-Maria Busemann (EM)

Catholic Children's Hospital Wilhelmstift, Hamburg, Germany.

Norbert Jorch (N)

Department of Paediatrics, Evangelical Hospital Bethel, Bielefeld, Germany.

Karl-Otfried Schwab (KO)

Division of Paediatric Endocrinology and Diabetes, University Hospital Freiburg, Freiburg, Germany.

Joachim Wölfle (J)

Department of Paediatrics, University Hospital Erlangen, Erlangen, Germany.

Reinhard W Holl (RW)

Central Institute for Biomedical Technology, Institute for Epidemiology and Medical Biometry, University of Ulm, Ulm, Germany.

Markus Bettendorf (M)

Division of Paediatric Endocrinology and Diabetes, Department of Paediatrics, University Children's Hospital Heidelberg, Im Neuenheimer Feld 430, 69120, Heidelberg, Germany.

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