Cytokine storm syndrome in a young patient with cystic fibrosis.
hemophagocytic lymphohistiocytosis
macrophage activation syndrome
multisystem inflammatory syndrome related to SARS CoV2
Journal
Pediatric pulmonology
ISSN: 1099-0496
Titre abrégé: Pediatr Pulmonol
Pays: United States
ID NLM: 8510590
Informations de publication
Date de publication:
10 2021
10 2021
Historique:
revised:
06
07
2021
received:
16
06
2021
accepted:
11
07
2021
pubmed:
23
7
2021
medline:
15
12
2021
entrez:
22
7
2021
Statut:
ppublish
Résumé
We report the case of a patient with cystic fibrosis (CF) presenting with a full-blown cytokine storm syndrome probably triggered by infection. This condition is rare and the diagnosis can be particularly difficult in patients with a complex chronic disease such as CF. However, timely recognition and appropriate treatment in the early stages are key to avoiding a potentially fatal course.
Types de publication
Case Reports
Letter
Langues
eng
Sous-ensembles de citation
IM
Pagination
3435-3437Informations de copyright
© 2021 Wiley Periodicals LLC.
Références
Fajgenbaum DC, June CH. Cytokine storm. N Engl J Med. 2020;383(23):2255-2273.
Casciaro R, Cresta F, Favilli F, Naselli A, De Alessandri A, Minicucci L. Macrophage activation syndrome induced by A/H1N1 influenza in cystic fibrosis. Pediatr Pulmonol. 2014;49(2):E10-E12.
Şişmanlar Eyüboğlu T, Aslan AT, Ramaslı Gursoy T, et al. Macrophage activation syndrome due to Nocardia spp in a pediatric patient with cystic fibrosis. Pediatr Pulmonol. 2019;54(4):E10-E12.
Radia T, Williams N, Agrawal P, et al. Multi-system inflammatory syndrome in children & adolescents (MIS-C): a systematic review of clinical features and presentation. Paediatr Respir Rev. 2020;38(2):51-57.
Ravelli A, Minoia F, Davì S, et al. Classification criteria for macrophage activation syndrome complicating systemic juvenile idiopathic arthritis: a European League Against Rheumatism/American College of Rheumatology/Paediatric Rheumatology International Trials Organisation collaborative initiative. Arthritis Rheumatol. 2016;68(3):566-576. https://pubmed.ncbi.nlm.nih.gov/26314788/