Ankyrin-R Links Kv3.3 to the Spectrin Cytoskeleton and Is Required for Purkinje Neuron Survival.
ataxia
cytoskeleton
ion channel
neurodegeneration
Journal
The Journal of neuroscience : the official journal of the Society for Neuroscience
ISSN: 1529-2401
Titre abrégé: J Neurosci
Pays: United States
ID NLM: 8102140
Informations de publication
Date de publication:
05 01 2022
05 01 2022
Historique:
received:
01
06
2021
revised:
26
10
2021
accepted:
31
10
2021
pubmed:
18
11
2021
medline:
11
2
2022
entrez:
17
11
2021
Statut:
ppublish
Résumé
Ankyrin scaffolding proteins are critical for membrane domain organization and protein stabilization in many different cell types including neurons. In the cerebellum, Ankyrin-R (AnkR) is highly enriched in Purkinje neurons, granule cells, and in the cerebellar nuclei (CN). Using male and female mice with a floxed allele for
Identifiants
pubmed: 34785580
pii: JNEUROSCI.1132-21.2021
doi: 10.1523/JNEUROSCI.1132-21.2021
pmc: PMC8741159
doi:
Substances chimiques
Ankyrins
0
Kcnc3 protein, mouse
0
Shaw Potassium Channels
0
Spectrin
12634-43-4
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
2-15Subventions
Organisme : NICHD NIH HHS
ID : U54 HD083092
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS119301
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS089664
Pays : United States
Organisme : NINDS NIH HHS
ID : R35 NS122073
Pays : United States
Organisme : NICHD NIH HHS
ID : P50 HD103555
Pays : United States
Organisme : NINDS NIH HHS
ID : F31 NS100300
Pays : United States
Informations de copyright
Copyright © 2022 the authors.
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