Next-generation sequencing analysis of cholangiocarcinoma identifies distinct IDH1-mutated clusters.


Journal

European journal of cancer (Oxford, England : 1990)
ISSN: 1879-0852
Titre abrégé: Eur J Cancer
Pays: England
ID NLM: 9005373

Informations de publication

Date de publication:
11 2022
Historique:
received: 09 06 2022
revised: 20 08 2022
accepted: 24 08 2022
pubmed: 2 10 2022
medline: 19 10 2022
entrez: 1 10 2022
Statut: ppublish

Résumé

IDH1-mutated intrahepatic cholangiocarcinomas (IDH1m iCCAs) could be treated with anti-IDH1 drugs, although the high heterogeneity in this class of tumours could limit treatment efficacy. We selected 125 IDH1m iCCAs that were treated as resectable, locally advanced, or metastatic and were screened by the NGS-based FoundationOne gene panel. We conducted a mutation-based clustering of tumours and survival analysis. Three main clusters were identified. The most altered pathways in cluster 1 were cell cycle and apoptosis, RTK/RAS, PI3K, and chromatin modification. Of note, CDKN2A/2B were mutated in 41/44 patients of this cluster. In cluster 2, the most affected pathways were as follows: Chromatin modification, DNA damage control, PI3K, and RTK/RAS. In this cluster, the most frequently mutated genes were ARID1A and PBRM1. The most altered pathways in cluster 3 were as follows: Cell cycle and apoptosis, DNA damage control, TP53, and chromatin modification. Importantly, TP53 was mutated only in cluster 3 patients. In the cohort of patients treated with surgery, cluster 2 showed statistically significant better disease-free survival (DFS) and overall survival (OS) compared with patients in cluster 3 and cluster 1 (p = 0.0014 and p = 0.0003, respectively). In the advanced setting, cluster 2 experienced a statistically significant better PFS (p = 0.0012), a tendency toward a better OS from first-line treatment, and a better OS from first-line progression compared with patients in cluster 1 and cluster 3 (p = 0.0017). We proposed an easy-to-use algorithm able to stratify patients in the three clusters on the basis of the genomic profile. We highlighted three different mutation-based clusters with prognostic significance in a cohort of IDH1m iCCAs.

Sections du résumé

BACKGROUND
IDH1-mutated intrahepatic cholangiocarcinomas (IDH1m iCCAs) could be treated with anti-IDH1 drugs, although the high heterogeneity in this class of tumours could limit treatment efficacy.
METHODS
We selected 125 IDH1m iCCAs that were treated as resectable, locally advanced, or metastatic and were screened by the NGS-based FoundationOne gene panel. We conducted a mutation-based clustering of tumours and survival analysis.
RESULTS
Three main clusters were identified. The most altered pathways in cluster 1 were cell cycle and apoptosis, RTK/RAS, PI3K, and chromatin modification. Of note, CDKN2A/2B were mutated in 41/44 patients of this cluster. In cluster 2, the most affected pathways were as follows: Chromatin modification, DNA damage control, PI3K, and RTK/RAS. In this cluster, the most frequently mutated genes were ARID1A and PBRM1. The most altered pathways in cluster 3 were as follows: Cell cycle and apoptosis, DNA damage control, TP53, and chromatin modification. Importantly, TP53 was mutated only in cluster 3 patients. In the cohort of patients treated with surgery, cluster 2 showed statistically significant better disease-free survival (DFS) and overall survival (OS) compared with patients in cluster 3 and cluster 1 (p = 0.0014 and p = 0.0003, respectively). In the advanced setting, cluster 2 experienced a statistically significant better PFS (p = 0.0012), a tendency toward a better OS from first-line treatment, and a better OS from first-line progression compared with patients in cluster 1 and cluster 3 (p = 0.0017). We proposed an easy-to-use algorithm able to stratify patients in the three clusters on the basis of the genomic profile.
CONCLUSION
We highlighted three different mutation-based clusters with prognostic significance in a cohort of IDH1m iCCAs.

Identifiants

pubmed: 36182816
pii: S0959-8049(22)00519-6
doi: 10.1016/j.ejca.2022.08.026
pii:
doi:

Substances chimiques

Chromatin 0
Isocitrate Dehydrogenase EC 1.1.1.41
IDH1 protein, human EC 1.1.1.42.

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

299-310

Informations de copyright

Copyright © 2022 Elsevier Ltd. All rights reserved.

Déclaration de conflit d'intérêts

Conflict of interest statement MN: Travel expenses from Celgene and AstraZeneca, speaker honorarium from Accademia della Medicina; honoraria from Sandoz, Medpoint SRL for editorial collaboration. Consultant honoraria from EMD Serono, Basilea Pharmaceutica, Incyte, MSD Italia and Servier. FdB: Honoraria from Roche, Pfizer, BMS, Merck, MSD, SERVIER, Sanofi, Amgen Astellas BioPharma, Incyte. Consulting or Advisory Role for Roche, Incyte, EMD Serono, BMS, Nerviano Medical Sciences, Sanofi, Novartis Italy, Menarini, research funding (institution): Novartis, Roche, Merck Serono, Pfizer, Servier, Philogen, Loxo, Tesaro, Nerviano Medical Sciences, Kymab. Research funding: BMS/Medarex, Merck KGaA, Ignyta, MedImmune, Exelis, Bayer health, Daiichi Sangyo Europe GmbH, Incyte, Basilea Pharmaceutical, Jassen Oncology. TM: (SOBI) Swedish Orpahn Biovitrum AB, Ability Pharmaceuticals SL, Aptitude Health, AstraZeneca, Basilea Pharma, Baxter, BioLineRX Ltd, Celgene, Eisai, Ellipses, Genzyme, Got It Consulting SL, Hirslanden/GITZ, Imedex, Incyte, Ipsen Bioscience, Inc, Janssen, Lilly. Marketing Farmacéutico & Investigación Clínica, S.L, MDS, Medscape, Novocure, Paraxel, PPD Development, Polaris, QED Therapeutics, Roche Farma, Sanofi-Aventis, Servier, Scilink Comunicación Científica SC, Surface Oncology, and Zymeworks.

Auteurs

Margherita Rimini (M)

IRCCS San Raffaele Scientific Institute Hospital, Department of Oncology, Vita-Salute San Raffaele University, Milan, Italy. Electronic address: margherita.rimini@gmail.com.

Eleonora Loi (E)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042, Cagliari, Italy.

Carles Fabregat-Franco (C)

Gastrointestinal Cancer Unit, Vall d'Hebron University Hospital & Vall d'Hebron Institute of Oncology (VHIO), Barcelona, Spain.

Valentina Burgio (V)

IRCCS San Raffaele Scientific Institute Hospital, Department of Oncology, Vita-Salute San Raffaele University, Milan, Italy.

Sara Lonardi (S)

Oncology Unit 3, Veneto Institute of Oncology - IRCCS, Padua, Italy.

Monica Niger (M)

Medical Oncology Department, Fondazione IRCCS Istituto Nazionale dei Tumori di Milano, Italy.

Mario Scartozzi (M)

Medical Oncology, University and University Hospital, Cagliari, Italy.

Ilario G Raposelli (IG)

Department of Medical Oncology, IRCCS Istituto Romagnolo per lo Studio dei Tumori (IRST) "Dino Amadori", 47014, Meldola, Italy.

Giuseppe Aprile (G)

Department of Oncology, San Bortolo General Hospital, Azienda ULSS8 Berica, Vicenza, Italy.

Francesca Ratti (F)

Hepatobiliary Surgery Division, Liver Center, Vita-Salute San Raffaele University, IRCCS San Raffaele Scientific Institute, Milan, 20132, Italy.

Federica Pedica (F)

Department of Experimental Oncology, Pathology Unit, IRCCS San Raffaele Scientific Institute, Milan, 20132, Italy.

Helena Verdaguer (H)

Gastrointestinal Cancer Unit, Vall d'Hebron University Hospital & Vall d'Hebron Institute of Oncology (VHIO), Barcelona, Spain.

Mario Rizzato (M)

Oncology Unit 1, Veneto Institute of Oncology - IRCCS, Padova, Italy.

Federico Nichetti (F)

Medical Oncology Department, Fondazione IRCCS Istituto Nazionale dei Tumori di Milano, Italy.

Eleonora Lai (E)

Medical Oncology, University and University Hospital, Cagliari, Italy.

Alessandro Cappetta (A)

Department of Oncology, San Bortolo General Hospital, Azienda ULSS8 Berica, Vicenza, Italy.

Teresa Macarulla (T)

Gastrointestinal Cancer Unit, Vall d'Hebron University Hospital & Vall d'Hebron Institute of Oncology (VHIO), Barcelona, Spain.

Matteo Fassan (M)

Department of Medicine (DIMED), Surgical Pathology Unit, University of Padua, Padova, Italy; Veneto Institute of Oncology - IRCCS, Padova, Italy.

Filippo De Braud (F)

Department of Oncology and Hemato-Oncology, University of Milan, Milan, Italy.

Andrea Pretta (A)

Medical Oncology, University and University Hospital, Cagliari, Italy.

Francesca Simionato (F)

Department of Oncology, San Bortolo General Hospital, Azienda ULSS8 Berica, Vicenza, Italy.

Francesco De Cobelli (F)

School of Medicine, Vita-Salute San Raffaele University, Milan, 20132, Italy.

Luca Aldrighetti (L)

Hepatobiliary Surgery Division, Liver Center, Vita-Salute San Raffaele University, IRCCS San Raffaele Scientific Institute, Milan, 20132, Italy.

Lorenzo Fornaro (L)

School of Medicine, Vita-Salute San Raffaele University, Milan, 20132, Italy.

Stefano Cascinu (S)

Vita-Salute San Raffaele University, IRCCS San Raffaele Scientific Institute Hospital, Department of Oncology, Milan, Italy.

Patrizia Zavattari (P)

Department of Biomedical Sciences, Unit of Biology and Genetics, University of Cagliari, 09042, Cagliari, Italy.

Andrea Casadei-Gardini (A)

Vita-Salute San Raffaele University, IRCCS San Raffaele Scientific Institute Hospital, Department of Oncology, Milan, Italy.

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Classifications MeSH