Hand surgery and hand therapy clinical practice guideline for epidermolysis bullosa.
Journal
Orphanet journal of rare diseases
ISSN: 1750-1172
Titre abrégé: Orphanet J Rare Dis
Pays: England
ID NLM: 101266602
Informations de publication
Date de publication:
07 11 2022
07 11 2022
Historique:
received:
08
08
2021
accepted:
07
03
2022
entrez:
8
11
2022
pubmed:
9
11
2022
medline:
10
11
2022
Statut:
epublish
Résumé
WHAT IS ALREADY KNOWN ABOUT THIS TOPIC?: Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. WHAT DOES THIS STUDY ADD?: These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount.
Identifiants
pubmed: 36345025
doi: 10.1186/s13023-022-02282-0
pii: 10.1186/s13023-022-02282-0
pmc: PMC9641806
doi:
Types de publication
Journal Article
Review
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
406Commentaires et corrections
Type : ErratumIn
Informations de copyright
© 2022. The Author(s).
Références
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