Cerebellar and subcortical atrophy contribute to psychiatric symptoms in frontotemporal dementia.


Journal

Human brain mapping
ISSN: 1097-0193
Titre abrégé: Hum Brain Mapp
Pays: United States
ID NLM: 9419065

Informations de publication

Date de publication:
05 2023
Historique:
revised: 18 01 2023
received: 18 08 2022
accepted: 19 01 2023
medline: 13 4 2023
pubmed: 11 3 2023
entrez: 10 3 2023
Statut: ppublish

Résumé

Recent studies have reported early cerebellar and subcortical impact in the disease progression of genetic frontotemporal dementia (FTD) due to microtubule-associated protein tau (MAPT), progranulin (GRN) and chromosome 9 open reading frame 72 (C9orf72). However, the cerebello-subcortical circuitry in FTD has been understudied despite its essential role in cognition and behaviors related to FTD symptomatology. The present study aims to investigate the association between cerebellar and subcortical atrophy, and neuropsychiatric symptoms across genetic mutations. Our study included 983 participants from the Genetic Frontotemporal dementia Initiative including mutation carriers and noncarrier first-degree relatives of known symptomatic carriers. Voxel-wise analysis of the thalamus, striatum, globus pallidus, amygdala, and the cerebellum was performed, and partial least squares analyses (PLS) were used to link morphometry and behavior. In presymptomatic C9orf72 expansion carriers, thalamic atrophy was found compared to noncarriers, suggesting the importance of this structure in FTD prodromes. PLS analyses demonstrated that the cerebello-subcortical circuitry is related to neuropsychiatric symptoms, with significant overlap in brain/behavior patterns, but also specificity for each genetic mutation group. The largest differences were in the cerebellar atrophy (larger extent in C9orf72 expansion group) and more prominent amygdalar volume reduction in the MAPT group. Brain scores in the C9orf72 expansion carriers and MAPT carriers demonstrated covariation patterns concordant with atrophy patterns detectable up to 20 years before expected symptom onset. Overall, these results demonstrated the important role of the subcortical structures in genetic FTD symptom expression, particularly the cerebellum in C9orf72 and the amygdala in MAPT carriers.

Identifiants

pubmed: 36895129
doi: 10.1002/hbm.26220
pmc: PMC10089095
doi:

Substances chimiques

C9orf72 Protein 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

2684-2700

Subventions

Organisme : Medical Research Council
ID : MC_UU_00005/12
Pays : United Kingdom
Organisme : Department of Health
ID : BRC149/NS/MH
Pays : United Kingdom
Organisme : Department of Health
ID : BRC-1215-20014
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/K010395/1
Pays : United Kingdom
Organisme : Medical Research Council
ID : MC_U105597119
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/M023664/1
Pays : United Kingdom
Organisme : Alzheimer's Society
ID : AS-PG-16-007
Pays : United Kingdom
Organisme : Alzheimer's Society
ID : AS-JF-19a-004-517
Pays : United Kingdom
Organisme : Medical Research Council
ID : MR/M008525/1
Pays : United Kingdom

Investigateurs

Aitana Sogorb Esteve (AS)
Annabel Nelson (A)
Arabella Bouzigues (A)
Carolin Heller (C)
Caroline V Greaves (CV)
David Cash (D)
David L Thomas (DL)
Emily Todd (E)
Hanya Benotmane (H)
Henrik Zetterberg (H)
Imogen J Swift (IJ)
Jennifer Nicholas (J)
Kiran Samra (K)
Lucy L Russell (LL)
Martina Bocchetta (M)
Rachelle Shafei (R)
Rhian S Convery (RS)
Carolyn Timberlake (C)
Thomas Cope (T)
Timothy Rittman (T)
Alberto Benussi (A)
Enrico Premi (E)
Roberto Gasparotti (R)
Silvana Archetti (S)
Stefano Gazzina (S)
Valentina Cantoni (V)
Andrea Arighi (A)
Chiara Fenoglio (C)
Elio Scarpini (E)
Giorgio Fumagalli (G)
Vittoria Borracci (V)
Giacomina Rossi (G)
Giorgio Giaccone (G)
Giuseppe Di Fede (G)
Paola Caroppo (P)
Pietro Tiraboschi (P)
Sara Prioni (S)
Veronica Redaelli (V)
David Tang-Wai (D)
Ekaterina Rogaeva (E)
Miguel Castelo-Branco (M)
Morris Freedman (M)
Ron Keren (R)
Sandra Black (S)
Sara Mitchell (S)
Christen Shoesmith (C)
Robart Bartha (R)
Rosa Rademakers (R)
Jackie Poos (J)
Janne M Papma (JM)
Lucia Giannini (L)
Rick van Minkelen (R)
Yolande Pijnenburg (Y)
Benedetta Nacmias (B)
Camilla Ferrari (C)
Cristina Polito (C)
Gemma Lombardi (G)
Valentina Bessi (V)
Michele Veldsman (M)
Christin Andersson (C)
Hakan Thonberg (H)
Linn Öijerstedt (L)
Vesna Jelic (V)
Paul Thompson (P)
Tobias Langheinrich (T)
Albert Lladó (A)
Anna Antonell (A)
Jaume Olives (J)
Mircea Balasa (M)
Nuria Bargalló (N)
Sergi Borrego-Ecija (S)
Ana Verdelho (A)
Carolina Maruta (C)
Catarina B Ferreira (CB)
Gabriel Miltenberger (G)
Frederico Simões do Couto (FS)
Alazne Gabilondo (A)
Ana Gorostidi (A)
Jorge Villanua (J)
Marta Cañada (M)
Mikel Tainta (M)
Miren Zulaica (M)
Myriam Barandiaran (M)
Patricia Alves (P)
Benjamin Bender (B)
Carlo Wilke (C)
Lisa Graf (L)
Annick Vogels (A)
Mathieu Vandenbulcke (M)
Philip Van Damme (P)
Rose Bruffaerts (R)
Koen Poesen (K)
Pedro Rosa-Neto (P)
Serge Gauthier (S)
Agnès Camuzat (A)
Alexis Brice (A)
Anne Bertrand (A)
Aurélie Funkiewiez (A)
Daisy Rinaldi (D)
Dario Saracino (D)
Olivier Colliot (O)
Sabrina Sayah (S)
Catharina Prix (C)
Elisabeth Wlasich (E)
Olivia Wagemann (O)
Sandra Loosli (S)
Sonja Schönecker (S)
Tobias Hoegen (T)
Jolina Lombardi (J)
Sarah Anderl-Straub (S)
Adeline Rollin (A)
Gregory Kuchcinski (G)
Maxime Bertoux (M)
Thibaud Lebouvier (T)
Vincent Deramecourt (V)
Beatriz Santiago (B)
Diana Duro (D)
Maria João Leitão (MJ)
Maria Rosario Almeida (MR)
Miguel Tábuas-Pereira (M)
Sónia Afonso (S)
Annerose Engel (A)
Maryna Polyakova (M)

Informations de copyright

© 2023 The Authors. Human Brain Mapping published by Wiley Periodicals LLC.

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Auteurs

Aurélie Bussy (A)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Douglas Mental Health University Institute, McGill University, Montreal, Quebec, Canada.
Integrated Program in Neuroscience, McGill University, Montreal, Canada.

Jake P Levy (JP)

Integrated Program in Neuroscience, McGill University, Montreal, Canada.
McConnell Brain Imaging Centre, Montreal Neurological Institute, McGill University, Montreal, Quebec, Canada.

Tristin Best (T)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Douglas Mental Health University Institute, McGill University, Montreal, Quebec, Canada.
Integrated Program in Neuroscience, McGill University, Montreal, Canada.

Raihaan Patel (R)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Douglas Mental Health University Institute, McGill University, Montreal, Quebec, Canada.
Department of Biomedical Engineering, McGill University, Montreal, Quebec, Canada.

Lani Cupo (L)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Douglas Mental Health University Institute, McGill University, Montreal, Quebec, Canada.
Integrated Program in Neuroscience, McGill University, Montreal, Canada.

Tim Van Langenhove (T)

Department of Neurology, Ghent University Hospital, Ghent, Belgium.

Jørgen E Nielsen (JE)

Neurogenetics Clinic & Research Lab, Danish Dementia Research Centre, Department of Neurology, Rigshospitalet, Copenhagen University Hospital, Copenhagen, Denmark.

Yolande Pijnenburg (Y)

Alzheimer Center Amsterdam, Department of Neurology, Amsterdam Neuroscience, Vrije Universiteit Amsterdam, Amsterdam, The Netherlands.

Maria Landqvist Waldö (ML)

Division of Clinical Sciences Helsingborg, Department of Clinical Sciences Lund, Lund University, Lund, Sweden.

Anne M Remes (AM)

Research Unit of Clinical Medicine, Neurology, University of Oulu, Finland.
Medical Research Center, Oulu University Hospital, Oulu, Finland.

Matthias L Schroeter (ML)

Clinic for Cognitive Neurology, University Clinic Leipzig, Max Planck Institute for Human Cognitive and Brain Sciences, Leipzig, Germany.
Clinic for Cognitive Neurology, University Clinic Leipzig, Leipzig, Germany.

Isabel Santana (I)

University Hospital of Coimbra (HUC), Neurology Service, Faculty of Medicine, University of Coimbra, Coimbra, Portugal.
Center for Neuroscience and Cell Biology, Faculty of Medicine, University of Coimbra, Coimbra, Portugal.

Florence Pasquier (F)

Universite de Lille, Lille, France.
Inserm 1172, Lille, France.
CHU, CNR-MAJ, Labex Distalz, Lille, France.

Markus Otto (M)

Department of Neurology, University of Ulm, Ulm, Germany.

Adrian Danek (A)

Neurologische Klinik und Poliklinik, Ludwig-Maximilians-Universität, Munich, Germany.

Johannes Levin (J)

Neurologische Klinik und Poliklinik, Ludwig-Maximilians-Universität, Munich, Germany.
Department of Neurodegenerative Diseases, Hertie-Institute for Clinical Brain Research and Center of Neurology, Center for Neurodegenerative Diseases (DZNE), University of Tübingen, Tübingen, Germany.

Isabelle Le Ber (I)

Sorbonne Université, Paris Brain Institute-Institut du Cerveau-ICM, Inserm U1127, Paris, France.
Centre de référence des démences rares ou précoces, IM2A, Département de Neurologie, AP-HP - Hôpital Pitié-Salpêtrière, Paris, France.
Département de Neurologie, AP-HP - Hôpital Pitié-Salpêtrière, Paris, France.

Rik Vandenberghe (R)

Department of Neurosciences, Laboratory for Cognitive Neurology, Leuven, Belgium.
Neurology Service, University Hospitals Leuven, Leuven, Belgium.
Leuven Brain Institute, KU Leuven, Leuven, Belgium.

Matthis Synofzik (M)

Department of Neurodegenerative Diseases, Hertie-Institute for Clinical Brain Research and Center of Neurology, Center for Neurodegenerative Diseases (DZNE), University of Tübingen, Tübingen, Germany.

Fermin Moreno (F)

Neuroscience Area, Biodonostia Health Research Institute, San Sebastian, Spain.
Cognitive Disorders Unit, Department of Neurology, Donostia University Hospital, San Sebastian, Gipuzkoa, Spain.

Alexandre de Mendonça (A)

Faculty of Medicine, University of Lisbon, Lisbon, Portugal.

Raquel Sanchez-Valle (R)

Alzheimer's disease and Other Cognitive Disorders Unit, Neurology Service, Hospital Clínic, Institut d'Investigacións Biomèdiques August Pi I Sunyer, University of Barcelona, Barcelona, Spain.

Robert Laforce (R)

Clinique Interdisciplinaire de Mémoire, Département des Sciences Neurologiques, CHU de Québec, and Faculté de Médecine, Université Laval, Quebec, Canada.

Tobias Langheinrich (T)

Division of Neuroscience, Wolfson Molecular Imaging Centre, University of Manchester, Manchester, UK.
Cerebral Function Unit, Manchester Centre for Clinical Neurosciences, Salford Royal NHS Foundation Trust, Salford, UK.

Alexander Gerhard (A)

Division of Neuroscience, Wolfson Molecular Imaging Centre, University of Manchester, Manchester, UK.
Departments of Geriatric Medicine and Nuclear Medicine, University of Duisburg, Essen, Germany.

Caroline Graff (C)

Center for Alzheimer Research, Division of Neurogeriatrics, Department of Neurobiology, Care Sciences and Society, Bioclinicum, Karolinska Institutet, Solna, Sweden.
Unit for Hereditary Dementias, Theme Inflammation and Aging, Karolinska University Hospital, Solna, Sweden.

Chris R Butler (CR)

Nuffield Department of Clinical Neurosciences, Medical Sciences Division, University of Oxford, Oxford, UK.
Department of Brain Sciences, Imperial College London, London, UK.

Sandro Sorbi (S)

Department of Neurofarba, University of Florence, Florence, Italy.
IRCCS Fondazione Don Carlo Gnocchi, Florence, Italy.

Lize Jiskoot (L)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

Harro Seelaar (H)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

John C van Swieten (JC)

Department of Neurology, Erasmus Medical Centre, Rotterdam, Netherlands.

Elizabeth Finger (E)

Department of Clinical Neurological Sciences, University of Western Ontario, London, Ontario, Canada.

Maria Carmela Tartaglia (MC)

Tanz Centre for Research in Neurodegenerative Diseases, University of Toronto, Toronto, Canada.

Mario Masellis (M)

Sunnybrook Health Sciences Centre, Sunnybrook Research Institute, University of Toronto, Toronto, Canada.

Pietro Tiraboschi (P)

Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.

Daniela Galimberti (D)

Department of Biomedical, Surgical and Dental Sciences, University of Milan, Milan, Italy.
Neurodegenerative Diseases Unit, Fondazione IRCCS Ca' Granda, Ospedale Maggiore Policlinico, Milan, Italy.

Barbara Borroni (B)

Centre for Neurodegenerative Disorders, Department of Clinical and Experimental Sciences, University of Brescia, Brescia, Italy.

James B Rowe (JB)

Department of Clinical Neurosciences and Cambridge University Hospitals NHS Trust and Medical Research Council Cognition and Brain Sciences Unit, University of Cambridge, Cambridge, UK.

Martina Bocchetta (M)

Dementia Research Centre, Department of Neurodegenerative Disease, UCL Queen Square Institute of Neurology, University College London, London, UK.
Centre for Cognitive and Clinical Neuroscience, Division of Psychology, Department of Life Sciences, College of Health, Medicine and Life Sciences, Brunel University London, London, UK.

Jonathan D Rohrer (JD)

Munich Cluster of Systems Neurology, Munich, Germany.

Gabriel A Devenyi (GA)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Department of Biomedical Engineering, McGill University, Montreal, Quebec, Canada.

M Mallar Chakravarty (MM)

Computational Brain Anatomy (CoBrA) Laboratory, Cerebral Imaging Centre, Douglas Mental Health University Institute, Montreal, Quebec, Canada.
Douglas Mental Health University Institute, McGill University, Montreal, Quebec, Canada.
Integrated Program in Neuroscience, McGill University, Montreal, Canada.
Department of Biomedical Engineering, McGill University, Montreal, Quebec, Canada.
Department of Psychiatry, McGill University, Montreal, Quebec, Canada.

Simon Ducharme (S)

Integrated Program in Neuroscience, McGill University, Montreal, Canada.
Department of Psychiatry, McGill University, Montreal, Quebec, Canada.
McConnell Brain Imaging Centre, Montreal Neurological Institute, McGill University, Montreal, Quebec, Canada.

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